Abstract
Pilomatrix carcinoma, a malignant counterpart of pilomatrixoma, is a rare skin neoplasm composed of basaloid and shadow cells that characterize differentiation toward the hair matrix. The authors present a case of pilomatrix carcinoma of the clitoris, a very unusual location not previously reported. Diagnostic criteria and differential diagnoses are discussed. Pilomatrix carcinoma should be differentiated from benign pilomatrixoma and other carcinomas with shadow cells, including basal cell carcinoma with matrical differentiation and metastases of visceral carcinomas with shadow cells.
MeSH terms
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Biomarkers, Tumor / metabolism
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Carcinoma, Basal Cell / diagnosis
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Cell Nucleus / metabolism
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Cell Nucleus / pathology
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Clitoris / pathology*
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Cyclin D1 / metabolism
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Diagnosis, Differential
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Fatal Outcome
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Female
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Hair Diseases / diagnosis*
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Hair Diseases / metabolism
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Hair Diseases / surgery
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Humans
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Pilomatrixoma / diagnosis*
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Pilomatrixoma / metabolism
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Pilomatrixoma / surgery
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Skin Neoplasms / diagnosis*
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Skin Neoplasms / metabolism
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Skin Neoplasms / surgery
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Vulvar Neoplasms / diagnosis*
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Vulvar Neoplasms / metabolism
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Vulvar Neoplasms / surgery
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beta Catenin / metabolism
Substances
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Biomarkers, Tumor
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CCND1 protein, human
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CTNNB1 protein, human
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beta Catenin
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Cyclin D1