No abstract available
MeSH terms
-
Amino Acid Metabolism, Inborn Errors / blood
-
Carnitine / therapeutic use
-
Cell Line
-
Child, Preschool
-
Female
-
Hemiterpenes
-
Humans
-
Isovaleryl-CoA Dehydrogenase
-
Leucine / therapeutic use
-
Male
-
Oxidoreductases / metabolism*
-
Oxidoreductases Acting on CH-CH Group Donors*
-
Pentanoic Acids / blood
-
Pentanoic Acids / metabolism*
-
Prognosis
-
Valerates / metabolism*
Substances
-
Hemiterpenes
-
Pentanoic Acids
-
Valerates
-
isovaleric acid
-
Oxidoreductases
-
Oxidoreductases Acting on CH-CH Group Donors
-
Isovaleryl-CoA Dehydrogenase
-
Leucine
-
Carnitine