Neurosarcoidosis and Ocular Inflammation: A Case Series and Literature Review

J Neuroophthalmol. 2021 Jun 1;41(2):e259-e266. doi: 10.1097/WNO.0000000000001117.

Abstract

Objective: To describe the ocular findings of neurosarcoidosis (NS) through a case series and review the current literature on the ocular complications of NS.

Methods: Case series of 4 patients with a literature review.

Results: Ophthalmic involvement in NS includes scleritis, cranial nerve palsies, uveitis, optic nerve granulomas, and occlusive retinal vasculitis.

Conclusion: NS is an uncommon, but potentially life-threatening, manifestation of sarcoidosis with ocular involvement up to 25% of patients. Patients presenting with neuro-ophthalmic manifestations of sarcoidosis are more likely to have other sites of involvement requiring ophthalmologists to maintain a high index of suspicion for systemic disease.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Aged
  • Brain / pathology
  • Central Nervous System Diseases / complications*
  • Central Nervous System Diseases / diagnosis
  • Female
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Sarcoidosis / complications*
  • Sarcoidosis / diagnosis
  • Uveitis / complications*
  • Uveitis / diagnosis
  • Vision Disorders / diagnosis
  • Vision Disorders / etiology*
  • Young Adult

Supplementary concepts

  • Neurosarcoidosis