The gamma-glutamyl cycle. Diseases associated with specific enzyme deficiencies

Ann Intern Med. 1974 Aug;81(2):247-53. doi: 10.7326/0003-4819-81-2-247.
No abstract available

Publication types

  • Review

MeSH terms

  • Acyltransferases / metabolism
  • Adult
  • Amidohydrolases / metabolism
  • Amino Acid Metabolism, Inborn Errors / enzymology*
  • Amino Acids / metabolism
  • Anemia, Hemolytic / enzymology
  • Cell Membrane Permeability
  • Child, Preschool
  • Cysteine / metabolism
  • Erythrocytes / enzymology
  • Female
  • Glutamates / metabolism
  • Glutathione / biosynthesis
  • Glutathione / metabolism*
  • Glycine / metabolism
  • Humans
  • Infant
  • Infant, Newborn
  • Kidney / enzymology
  • Kidney / metabolism
  • Male
  • Peptide Synthases / metabolism
  • Proline / metabolism
  • Pyrrolidonecarboxylic Acid / metabolism
  • Pyrrolidonecarboxylic Acid / urine
  • gamma-Glutamyltransferase / metabolism

Substances

  • Amino Acids
  • Glutamates
  • Proline
  • Acyltransferases
  • gamma-Glutamyltransferase
  • Amidohydrolases
  • Peptide Synthases
  • Glutathione
  • Cysteine
  • Pyrrolidonecarboxylic Acid
  • Glycine