Control of pyruvate and beta-hydroxybutyrate utilization in rat brain mitochondria and its relevance to phenylketonuria and maple syrup urine disease

J Neurochem. 1976 Apr;26(4):823-30. doi: 10.1111/j.1471-4159.1976.tb04458.x.
No abstract available

MeSH terms

  • Age Factors
  • Animals
  • Brain / metabolism*
  • Humans
  • Hydroxybutyrates / metabolism*
  • Male
  • Maple Syrup Urine Disease / metabolism*
  • Mitochondria / metabolism*
  • Phenylalanine / metabolism
  • Phenylketonurias / metabolism*
  • Phenylpyruvic Acids / metabolism
  • Pyruvates / metabolism*
  • Rats

Substances

  • Hydroxybutyrates
  • Phenylpyruvic Acids
  • Pyruvates
  • Phenylalanine