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Neuronal/glioneuronal neoplasm of the central nervous system

MedGen UID:
105377
Concept ID:
C0474844
Neoplastic Process
Synonyms: Glioneuronal and Neuronal Tumors; Glioneuronal tumor; Glioneuronal tumour; mixed neuronal-glial tumor; Mixed neuronal-glial tumor; Neuronal and Glio-Neuronal Neoplasm; neuronal and Glio-neuronal neoplasm; Neuronal and Glio-Neuronal Tumor; neuronal and Glio-neuronal tumor; neuronal and Glio-neuronal tumour; Neuronal and Mixed Neuronal-Glial Tumor; Neuronal and mixed neuronal-glial tumor; neuronal and mixed neuronal-glial tumor; Neuronal and Mixed Neuronal-Glial Tumors; neuronal and mixed neuronal-glial tumors; Neuronal and mixed neuronal-glial tumour; neuronal and mixed neuronal-glial tumour; neuronal and mixed neuronal-glial tumours; Neuronal/glioneuronal neoplasm of the CNS
SNOMED CT: Neuronal and mixed neuronal-glial tumor (302831000)
 
HPO: HP:0025170
Monarch Initiative: MONDO:0016729
Orphanet: ORPHA251934

Definition

A central nervous system neoplasm with neuronal and, less consistently, glial differentiation. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNeuronal/glioneuronal neoplasm of the central nervous system

Recent clinical studies

Etiology

Ho CY, Bornhorst M, Almira-Suarez MI, Donev K, Grafe M, Gordish-Dressman H, Rodriguez FJ
J Neuropathol Exp Neurol 2020 Jan 1;79(1):67-73. doi: 10.1093/jnen/nlz115. PMID: 31793986Free PMC Article
Chandrashekhar TN, Mahadevan A, Vani S, Yasha TC, Sampath S, Chandramouli BA, Devi BI, Arvinda HR, Shankar SK
Neuropathology 2012 Feb;32(1):1-12. Epub 2011 Mar 17 doi: 10.1111/j.1440-1789.2011.01206.x. PMID: 21410777

Diagnosis

Wang KY, Chen MM, Malayil Lincoln CM
Neuroimaging Clin N Am 2021 Feb;31(1):121-138. doi: 10.1016/j.nic.2020.09.011. PMID: 33220825
Ho CY, Bornhorst M, Almira-Suarez MI, Donev K, Grafe M, Gordish-Dressman H, Rodriguez FJ
J Neuropathol Exp Neurol 2020 Jan 1;79(1):67-73. doi: 10.1093/jnen/nlz115. PMID: 31793986Free PMC Article
Wang KY, Chen MM, Malayil Lincoln CM
Radiol Clin North Am 2019 Nov;57(6):1147-1162. Epub 2019 Aug 16 doi: 10.1016/j.rcl.2019.07.004. PMID: 31582041
Chandrashekhar TN, Mahadevan A, Vani S, Yasha TC, Sampath S, Chandramouli BA, Devi BI, Arvinda HR, Shankar SK
Neuropathology 2012 Feb;32(1):1-12. Epub 2011 Mar 17 doi: 10.1111/j.1440-1789.2011.01206.x. PMID: 21410777

Prognosis

Ho CY, Bornhorst M, Almira-Suarez MI, Donev K, Grafe M, Gordish-Dressman H, Rodriguez FJ
J Neuropathol Exp Neurol 2020 Jan 1;79(1):67-73. doi: 10.1093/jnen/nlz115. PMID: 31793986Free PMC Article
Chandrashekhar TN, Mahadevan A, Vani S, Yasha TC, Sampath S, Chandramouli BA, Devi BI, Arvinda HR, Shankar SK
Neuropathology 2012 Feb;32(1):1-12. Epub 2011 Mar 17 doi: 10.1111/j.1440-1789.2011.01206.x. PMID: 21410777

Clinical prediction guides

Wang KY, Chen MM, Malayil Lincoln CM
Neuroimaging Clin N Am 2021 Feb;31(1):121-138. doi: 10.1016/j.nic.2020.09.011. PMID: 33220825
Ho CY, Bornhorst M, Almira-Suarez MI, Donev K, Grafe M, Gordish-Dressman H, Rodriguez FJ
J Neuropathol Exp Neurol 2020 Jan 1;79(1):67-73. doi: 10.1093/jnen/nlz115. PMID: 31793986Free PMC Article
Wang KY, Chen MM, Malayil Lincoln CM
Radiol Clin North Am 2019 Nov;57(6):1147-1162. Epub 2019 Aug 16 doi: 10.1016/j.rcl.2019.07.004. PMID: 31582041
Chandrashekhar TN, Mahadevan A, Vani S, Yasha TC, Sampath S, Chandramouli BA, Devi BI, Arvinda HR, Shankar SK
Neuropathology 2012 Feb;32(1):1-12. Epub 2011 Mar 17 doi: 10.1111/j.1440-1789.2011.01206.x. PMID: 21410777

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