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Pericardial constriction

MedGen UID:
116108
Concept ID:
C0240709
Finding
Synonym: Pericardial Constriction
 
HPO: HP:0005132

Definition

Compression of the heart caused by rigid, thickened, or fused pericardial membranes. [from HPO]

Term Hierarchy

Conditions with this feature

Mulibrey nanism syndrome
MedGen UID:
99347
Concept ID:
C0524582
Disease or Syndrome
Mulibrey nanism (MUL) is a rare autosomal recessive growth disorder with prenatal onset, including occasional progressive cardiomyopathy, characteristic facial features, failure of sexual maturation, insulin resistance with type 2 diabetes, and an increased risk for Wilms tumor (summary by Hamalainen et al., 2006).

Professional guidelines

PubMed

Welch TD
Heart 2018 May;104(9):725-731. Epub 2017 Nov 25 doi: 10.1136/heartjnl-2017-311683. PMID: 29175978
Evans DJ
Respir Med 2008 Jun;102(6):793-800. Epub 2008 Apr 14 doi: 10.1016/j.rmed.2008.01.018. PMID: 18407484
Banerjee S, Swanton RH
Hosp Med 2002 Feb;63(2):72-9. doi: 10.12968/hosp.2002.63.2.2083. PMID: 11902092

Recent clinical studies

Etiology

Arrossi AV
Adv Anat Pathol 2023 Jul 1;30(4):253-258. Epub 2023 Apr 27 doi: 10.1097/PAP.0000000000000399. PMID: 37104724
Obokata M, Reddy YNV, Borlaug BA
JACC Cardiovasc Imaging 2020 Jan;13(1 Pt 2):245-257. Epub 2019 Jun 12 doi: 10.1016/j.jcmg.2018.12.034. PMID: 31202759Free PMC Article
Welch TD
Heart 2018 May;104(9):725-731. Epub 2017 Nov 25 doi: 10.1136/heartjnl-2017-311683. PMID: 29175978
Gujral DM, Lloyd G, Bhattacharyya S
Heart 2016 Feb 15;102(4):269-76. Epub 2015 Dec 9 doi: 10.1136/heartjnl-2015-308765. PMID: 26661320
Moores DW, Dziuban SW Jr
Chest Surg Clin N Am 1995 May;5(2):359-73. PMID: 7613970

Diagnosis

Arrossi AV
Adv Anat Pathol 2023 Jul 1;30(4):253-258. Epub 2023 Apr 27 doi: 10.1097/PAP.0000000000000399. PMID: 37104724
Huang YS, Zhang JX, Sun Y
J Int Med Res 2020 Nov;48(11):300060520973091. doi: 10.1177/0300060520973091. PMID: 33233991Free PMC Article
Obokata M, Reddy YNV, Borlaug BA
JACC Cardiovasc Imaging 2020 Jan;13(1 Pt 2):245-257. Epub 2019 Jun 12 doi: 10.1016/j.jcmg.2018.12.034. PMID: 31202759Free PMC Article
Welch TD
Heart 2018 May;104(9):725-731. Epub 2017 Nov 25 doi: 10.1136/heartjnl-2017-311683. PMID: 29175978
Mayosi BM, Burgess LJ, Doubell AF
Circulation 2005 Dec 6;112(23):3608-16. doi: 10.1161/CIRCULATIONAHA.105.543066. PMID: 16330703

Therapy

Baritussio A, Giordani AS, Iliceto S, Marcolongo R, Caforio ALP
Int J Cardiol 2023 Nov 1;390:131225. Epub 2023 Jul 29 doi: 10.1016/j.ijcard.2023.131225. PMID: 37524124
Depboylu BC, Mootoosamy P, Vistarini N, Testuz A, El-Hamamsy I, Cikirikcioglu M
Tex Heart Inst J 2017 Apr;44(2):101-106. Epub 2017 Apr 1 doi: 10.14503/THIJ-16-5772. PMID: 28461794Free PMC Article
Gujral DM, Lloyd G, Bhattacharyya S
Heart 2016 Feb 15;102(4):269-76. Epub 2015 Dec 9 doi: 10.1136/heartjnl-2015-308765. PMID: 26661320
Mayosi BM, Burgess LJ, Doubell AF
Circulation 2005 Dec 6;112(23):3608-16. doi: 10.1161/CIRCULATIONAHA.105.543066. PMID: 16330703
Moores DW, Dziuban SW Jr
Chest Surg Clin N Am 1995 May;5(2):359-73. PMID: 7613970

Prognosis

Baritussio A, Giordani AS, Iliceto S, Marcolongo R, Caforio ALP
Int J Cardiol 2023 Nov 1;390:131225. Epub 2023 Jul 29 doi: 10.1016/j.ijcard.2023.131225. PMID: 37524124
Arrossi AV
Adv Anat Pathol 2023 Jul 1;30(4):253-258. Epub 2023 Apr 27 doi: 10.1097/PAP.0000000000000399. PMID: 37104724
Obokata M, Reddy YNV, Borlaug BA
JACC Cardiovasc Imaging 2020 Jan;13(1 Pt 2):245-257. Epub 2019 Jun 12 doi: 10.1016/j.jcmg.2018.12.034. PMID: 31202759Free PMC Article
Depboylu BC, Mootoosamy P, Vistarini N, Testuz A, El-Hamamsy I, Cikirikcioglu M
Tex Heart Inst J 2017 Apr;44(2):101-106. Epub 2017 Apr 1 doi: 10.14503/THIJ-16-5772. PMID: 28461794Free PMC Article
Gujral DM, Lloyd G, Bhattacharyya S
Heart 2016 Feb 15;102(4):269-76. Epub 2015 Dec 9 doi: 10.1136/heartjnl-2015-308765. PMID: 26661320

Clinical prediction guides

Baritussio A, Giordani AS, Iliceto S, Marcolongo R, Caforio ALP
Int J Cardiol 2023 Nov 1;390:131225. Epub 2023 Jul 29 doi: 10.1016/j.ijcard.2023.131225. PMID: 37524124
Fadl SA, Nasrullah A, Harris A, Edwards R, Kicska G
Int J Cardiovasc Imaging 2020 May;36(5):947-969. Epub 2020 Feb 11 doi: 10.1007/s10554-020-01784-x. PMID: 32048125
Obokata M, Reddy YNV, Borlaug BA
JACC Cardiovasc Imaging 2020 Jan;13(1 Pt 2):245-257. Epub 2019 Jun 12 doi: 10.1016/j.jcmg.2018.12.034. PMID: 31202759Free PMC Article
Depboylu BC, Mootoosamy P, Vistarini N, Testuz A, El-Hamamsy I, Cikirikcioglu M
Tex Heart Inst J 2017 Apr;44(2):101-106. Epub 2017 Apr 1 doi: 10.14503/THIJ-16-5772. PMID: 28461794Free PMC Article
Gujral DM, Lloyd G, Bhattacharyya S
Heart 2016 Feb 15;102(4):269-76. Epub 2015 Dec 9 doi: 10.1136/heartjnl-2015-308765. PMID: 26661320

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