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Childhood malignant mesenchymoma

MedGen UID:
124688
Concept ID:
C0279991
Neoplastic Process
Synonyms: Childhood Malignant Mesenchymoma; childhood malignant mesenchymoma; malignant mesenchymoma of childhood; paediatric malignant mesenchymoma; pediatric malignant mesenchymoma
 
Monarch Initiative: MONDO:0003691

Definition

A malignant mesenchymoma occurring in children. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChildhood malignant mesenchymoma

Recent clinical studies

Etiology

Shern JF, Selfe J, Izquierdo E, Patidar R, Chou HC, Song YK, Yohe ME, Sindiri S, Wei J, Wen X, Rudzinski ER, Barkauskas DA, Lo T, Hall D, Linardic CM, Hughes D, Jamal S, Jenney M, Chisholm J, Brown R, Jones K, Hicks B, Angelini P, George S, Chesler L, Hubank M, Kelsey A, Gatz SA, Skapek SX, Hawkins DS, Shipley JM, Khan J
J Clin Oncol 2021 Sep 10;39(26):2859-2871. Epub 2021 Jun 24 doi: 10.1200/JCO.20.03060. PMID: 34166060Free PMC Article
Vujanić GM, Kelsey A, Perlman EJ, Sandstedt B, Beckwith JB
Am J Surg Pathol 2007 Oct;31(10):1459-68. doi: 10.1097/PAS.0b013e31804d43a4. PMID: 17895746
Ekinci S, Karnak I, Tanyel FC, Senocak ME, Kutluk T, Büyükpamukçu M, Büyükpamukçu N
Pediatr Surg Int 2006 Mar;22(3):228-32. Epub 2006 Jan 3 doi: 10.1007/s00383-005-1608-1. PMID: 16395609
Terracini B, Pastore G, Zurlo MG, Masera G, Fossati-Bellani F, Castello M, Tamaro P, Massolo F, Rosati D, Biddau PF
Eur J Cancer Clin Oncol 1987 May;23(5):499-504. doi: 10.1016/0277-5379(87)90309-9. PMID: 3653174

Diagnosis

Shern JF, Selfe J, Izquierdo E, Patidar R, Chou HC, Song YK, Yohe ME, Sindiri S, Wei J, Wen X, Rudzinski ER, Barkauskas DA, Lo T, Hall D, Linardic CM, Hughes D, Jamal S, Jenney M, Chisholm J, Brown R, Jones K, Hicks B, Angelini P, George S, Chesler L, Hubank M, Kelsey A, Gatz SA, Skapek SX, Hawkins DS, Shipley JM, Khan J
J Clin Oncol 2021 Sep 10;39(26):2859-2871. Epub 2021 Jun 24 doi: 10.1200/JCO.20.03060. PMID: 34166060Free PMC Article
Hajji I, Jellab B, Benhaddou R, Baki S
Bull Soc Belge Ophtalmol 2012;(319):23-8. PMID: 22550774
Vujanić GM, Kelsey A, Perlman EJ, Sandstedt B, Beckwith JB
Am J Surg Pathol 2007 Oct;31(10):1459-68. doi: 10.1097/PAS.0b013e31804d43a4. PMID: 17895746
Ekinci S, Karnak I, Tanyel FC, Senocak ME, Kutluk T, Büyükpamukçu M, Büyükpamukçu N
Pediatr Surg Int 2006 Mar;22(3):228-32. Epub 2006 Jan 3 doi: 10.1007/s00383-005-1608-1. PMID: 16395609
Urban CE, Mache CJ, Schwinger W, Pakisch B, Ranner G, Riccabona M, Schimpl G, Brandesky G, Messner H, Pobegen W
Cancer 1993 Oct 15;72(8):2511-6. doi: 10.1002/1097-0142(19931015)72:8<2511::aid-cncr2820720833>3.0.co;2-m. PMID: 8402469

Therapy

Stevens MC, Rey A, Bouvet N, Ellershaw C, Flamant F, Habrand JL, Marsden HB, Martelli H, Sanchez de Toledo J, Spicer RD, Spooner D, Terrier-Lacombe MJ, van Unnik A, Oberlin O
J Clin Oncol 2005 Apr 20;23(12):2618-28. Epub 2005 Feb 22 doi: 10.1200/JCO.2005.08.130. PMID: 15728225
Hill DA
Pediatr Dev Pathol 2005 Jan-Feb;8(1):77-84. Epub 2005 Feb 23 doi: 10.1007/s10024-004-6069-3. PMID: 15719205
Urban CE, Mache CJ, Schwinger W, Pakisch B, Ranner G, Riccabona M, Schimpl G, Brandesky G, Messner H, Pobegen W
Cancer 1993 Oct 15;72(8):2511-6. doi: 10.1002/1097-0142(19931015)72:8<2511::aid-cncr2820720833>3.0.co;2-m. PMID: 8402469

Prognosis

Shern JF, Selfe J, Izquierdo E, Patidar R, Chou HC, Song YK, Yohe ME, Sindiri S, Wei J, Wen X, Rudzinski ER, Barkauskas DA, Lo T, Hall D, Linardic CM, Hughes D, Jamal S, Jenney M, Chisholm J, Brown R, Jones K, Hicks B, Angelini P, George S, Chesler L, Hubank M, Kelsey A, Gatz SA, Skapek SX, Hawkins DS, Shipley JM, Khan J
J Clin Oncol 2021 Sep 10;39(26):2859-2871. Epub 2021 Jun 24 doi: 10.1200/JCO.20.03060. PMID: 34166060Free PMC Article
Ekinci S, Karnak I, Tanyel FC, Senocak ME, Kutluk T, Büyükpamukçu M, Büyükpamukçu N
Pediatr Surg Int 2006 Mar;22(3):228-32. Epub 2006 Jan 3 doi: 10.1007/s00383-005-1608-1. PMID: 16395609
Stevens MC, Rey A, Bouvet N, Ellershaw C, Flamant F, Habrand JL, Marsden HB, Martelli H, Sanchez de Toledo J, Spicer RD, Spooner D, Terrier-Lacombe MJ, van Unnik A, Oberlin O
J Clin Oncol 2005 Apr 20;23(12):2618-28. Epub 2005 Feb 22 doi: 10.1200/JCO.2005.08.130. PMID: 15728225
Leonard MP, Partin AW, Epstein JI, Jeffs RD, Gearhart JP
J Urol 1990 Nov;144(5):1222-6. doi: 10.1016/s0022-5347(17)39699-4. PMID: 2231901
Schmidt D, Harms D, Lang W
Virchows Arch A Pathol Anat Histopathol 1985;407(4):387-405. doi: 10.1007/BF00709986. PMID: 2413614

Clinical prediction guides

Shern JF, Selfe J, Izquierdo E, Patidar R, Chou HC, Song YK, Yohe ME, Sindiri S, Wei J, Wen X, Rudzinski ER, Barkauskas DA, Lo T, Hall D, Linardic CM, Hughes D, Jamal S, Jenney M, Chisholm J, Brown R, Jones K, Hicks B, Angelini P, George S, Chesler L, Hubank M, Kelsey A, Gatz SA, Skapek SX, Hawkins DS, Shipley JM, Khan J
J Clin Oncol 2021 Sep 10;39(26):2859-2871. Epub 2021 Jun 24 doi: 10.1200/JCO.20.03060. PMID: 34166060Free PMC Article
Ekinci S, Karnak I, Tanyel FC, Senocak ME, Kutluk T, Büyükpamukçu M, Büyükpamukçu N
Pediatr Surg Int 2006 Mar;22(3):228-32. Epub 2006 Jan 3 doi: 10.1007/s00383-005-1608-1. PMID: 16395609
Stevens MC, Rey A, Bouvet N, Ellershaw C, Flamant F, Habrand JL, Marsden HB, Martelli H, Sanchez de Toledo J, Spicer RD, Spooner D, Terrier-Lacombe MJ, van Unnik A, Oberlin O
J Clin Oncol 2005 Apr 20;23(12):2618-28. Epub 2005 Feb 22 doi: 10.1200/JCO.2005.08.130. PMID: 15728225

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