U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Descending aorta hypoplasia

MedGen UID:
1376270
Concept ID:
C4476811
Congenital Abnormality
Synonym: Hypoplastic aorta
 
HPO: HP:0025495

Definition

Significant luminal narrowing of a long segment of the descending aorta. [from HPO]

Term Hierarchy

Professional guidelines

PubMed

Tretter JT, Spicer DE, Franklin RCG, Béland MJ, Aiello VD, Cook AC, Crucean A, Loomba RS, Yoo SJ, Quintessenza JA, Tchervenkov CI, Jacobs JP, Najm HK, Anderson RH
Ann Thorac Surg 2023 Jul;116(1):6-16. Epub 2023 Jun 8 doi: 10.1016/j.athoracsur.2023.03.023. PMID: 37294261
Michelena HI, Della Corte A, Evangelista A, Maleszewski JJ, Edwards WD, Roman MJ, Devereux RB, Fernández B, Asch FM, Barker AJ, Sierra-Galan LM, De Kerchove L, Fernandes SM, Fedak PWM, Girdauskas E, Delgado V, Abbara S, Lansac E, Prakash SK, Bissell MM, Popescu BA, Hope MD, Sitges M, Thourani VH, Pibarot P, Chandrasekaran K, Lancellotti P, Borger MA, Forrest JK, Webb J, Milewicz DM, Makkar R, Leon MB, Sanders SP, Markl M, Ferrari VA, Roberts WC, Song JK, Blanke P, White CS, Siu S, Svensson LG, Braverman AC, Bavaria J, Sundt TM, El Khoury G, De Paulis R, Enriquez-Sarano M, Bax JJ, Otto CM, Schäfers HJ
J Thorac Cardiovasc Surg 2021 Sep;162(3):e383-e414. Epub 2021 Jul 22 doi: 10.1016/j.jtcvs.2021.06.019. PMID: 34304896
Riambau V, Böckler D, Brunkwall J, Cao P, Chiesa R, Coppi G, Czerny M, Fraedrich G, Haulon S, Jacobs MJ, Lachat ML, Moll FL, Setacci C, Taylor PR, Thompson M, Trimarchi S, Verhagen HJ, Verhoeven EL, Esvs Guidelines Committee, Kolh P, de Borst GJ, Chakfé N, Debus ES, Hinchliffe RJ, Kakkos S, Koncar I, Lindholt JS, Vega de Ceniga M, Vermassen F, Verzini F, Document Reviewers, Kolh P, Black JH 3rd, Busund R, Björck M, Dake M, Dick F, Eggebrecht H, Evangelista A, Grabenwöger M, Milner R, Naylor AR, Ricco JB, Rousseau H, Schmidli J
Eur J Vasc Endovasc Surg 2017 Jan;53(1):4-52. doi: 10.1016/j.ejvs.2016.06.005. PMID: 28081802

Recent clinical studies

Etiology

Haranal M, Srimurugan B, Sivalingam S
Asian Cardiovasc Thorac Ann 2022 Feb;30(2):217-225. Epub 2021 May 6 doi: 10.1177/02184923211015092. PMID: 33957784
Riley JYJ, Leong K, Mortensen KH, Ariff B, Gopalan D
Br J Radiol 2021 Jul 1;94(1123):20210211. Epub 2021 Jun 9 doi: 10.1259/bjr.20210211. PMID: 33989055Free PMC Article
Karangelis D, Loggos S, Tzifa A, Mitropoulos FA
Curr Opin Cardiol 2020 Nov;35(6):636-642. doi: 10.1097/HCO.0000000000000793. PMID: 32852349
Yoshimura N, Fukahara K, Yamashita A, Doi T, Yamashita S, Homma T, Yokoyama S, Aoki M, Higashida A, Shimada Y, Toritsuka D, Nagao K, Ikeno Y
Surg Today 2020 Oct;50(10):1151-1158. Epub 2019 Nov 1 doi: 10.1007/s00595-019-01907-5. PMID: 31676999
Friedman K
Semin Cardiothorac Vasc Anesth 2018 Sep;22(3):265-269. Epub 2018 Apr 12 doi: 10.1177/1089253218770198. PMID: 29649938

Diagnosis

Friedman K
Semin Cardiothorac Vasc Anesth 2018 Sep;22(3):265-269. Epub 2018 Apr 12 doi: 10.1177/1089253218770198. PMID: 29649938
Riambau V, Böckler D, Brunkwall J, Cao P, Chiesa R, Coppi G, Czerny M, Fraedrich G, Haulon S, Jacobs MJ, Lachat ML, Moll FL, Setacci C, Taylor PR, Thompson M, Trimarchi S, Verhagen HJ, Verhoeven EL, Esvs Guidelines Committee, Kolh P, de Borst GJ, Chakfé N, Debus ES, Hinchliffe RJ, Kakkos S, Koncar I, Lindholt JS, Vega de Ceniga M, Vermassen F, Verzini F, Document Reviewers, Kolh P, Black JH 3rd, Busund R, Björck M, Dake M, Dick F, Eggebrecht H, Evangelista A, Grabenwöger M, Milner R, Naylor AR, Ricco JB, Rousseau H, Schmidli J
Eur J Vasc Endovasc Surg 2017 Jan;53(1):4-52. doi: 10.1016/j.ejvs.2016.06.005. PMID: 28081802
Cubero A, Ayala J, Hamzeh G, Cortes A, Udaondo J, Aramendi JI
World J Pediatr Congenit Heart Surg 2017 Mar;8(2):231-234. Epub 2016 Jun 23 doi: 10.1177/2150135116629396. PMID: 27095117
Tan KH, Ko SY, Chou SL
Am J Emerg Med 2012 Jul;30(6):1011.e5-6. Epub 2011 Jun 8 doi: 10.1016/j.ajem.2011.03.023. PMID: 21641746
Weinberg PM
J Cardiovasc Magn Reson 2006;8(4):633-43. doi: 10.1080/10976640600713756. PMID: 16869315

Therapy

Karangelis D, Loggos S, Tzifa A, Mitropoulos FA
Curr Opin Cardiol 2020 Nov;35(6):636-642. doi: 10.1097/HCO.0000000000000793. PMID: 32852349
Riambau V, Böckler D, Brunkwall J, Cao P, Chiesa R, Coppi G, Czerny M, Fraedrich G, Haulon S, Jacobs MJ, Lachat ML, Moll FL, Setacci C, Taylor PR, Thompson M, Trimarchi S, Verhagen HJ, Verhoeven EL, Esvs Guidelines Committee, Kolh P, de Borst GJ, Chakfé N, Debus ES, Hinchliffe RJ, Kakkos S, Koncar I, Lindholt JS, Vega de Ceniga M, Vermassen F, Verzini F, Document Reviewers, Kolh P, Black JH 3rd, Busund R, Björck M, Dake M, Dick F, Eggebrecht H, Evangelista A, Grabenwöger M, Milner R, Naylor AR, Ricco JB, Rousseau H, Schmidli J
Eur J Vasc Endovasc Surg 2017 Jan;53(1):4-52. doi: 10.1016/j.ejvs.2016.06.005. PMID: 28081802
Schneider H, Uebing A, Shore DF
J Cardiovasc Surg (Torino) 2016 Aug;57(4):557-68. Epub 2016 May 31 PMID: 27243624
Castellano JM, Kovacic JC, Sanz J, Fuster V
Ann N Y Acad Sci 2012 Apr;1254:164-174. doi: 10.1111/j.1749-6632.2012.06493.x. PMID: 22548582
Israel G, Krinsky G, Lee V
Clin Imaging 2002 Mar-Apr;26(2):116-21. doi: 10.1016/s0899-7071(01)00368-0. PMID: 11852219

Prognosis

Vinnakota A, Idrees JJ, Rosinski BF, Tucker NJ, Roselli EE, Pettersson GB, Vekstein AM, Stewart RD, Raja S, Svensson LG
Ann Thorac Surg 2019 Dec;108(6):1745-1750. Epub 2019 Jun 27 doi: 10.1016/j.athoracsur.2019.04.122. PMID: 31254511
Hanneman K, Newman B, Chan F
Radiographics 2017 Jan-Feb;37(1):32-51. Epub 2016 Nov 18 doi: 10.1148/rg.2017160033. PMID: 27860551
Raimondi F, Bonnet D
Diagn Interv Imaging 2016 May;97(5):561-9. Epub 2016 Apr 26 doi: 10.1016/j.diii.2016.03.009. PMID: 27132711
Mavroudis C, Mavroudis CD, Jacobs JP
Cardiol Young 2015 Dec;25(8):1546-60. doi: 10.1017/S1047951115002048. PMID: 26675603
Langley SM, Sunstrom RE, Reed RD, Rekito AJ, Gerrah R
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2013;16(1):43-51. doi: 10.1053/j.pcsu.2013.01.008. PMID: 23561817

Clinical prediction guides

Rylski B, Schofer F, Beyersdorf F, Kondov S, Kreibich M, Schlett CL, Czerny M
Semin Thorac Cardiovasc Surg 2022 Spring;34(1):19-26. Epub 2021 Mar 11 doi: 10.1053/j.semtcvs.2021.03.001. PMID: 33713827
Vinnakota A, Idrees JJ, Rosinski BF, Tucker NJ, Roselli EE, Pettersson GB, Vekstein AM, Stewart RD, Raja S, Svensson LG
Ann Thorac Surg 2019 Dec;108(6):1745-1750. Epub 2019 Jun 27 doi: 10.1016/j.athoracsur.2019.04.122. PMID: 31254511
Maredia AK, Greenway SC, Verma S, Fedak PWM
Curr Opin Cardiol 2018 Mar;33(2):134-139. doi: 10.1097/HCO.0000000000000481. PMID: 29095713
Serra R, Butrico L, Fugetto F, Chibireva MD, Malva A, De Caridi G, Massara M, Barbetta A, Cannistrà M, de Franciscis S
Ann Vasc Surg 2016 Aug;35:210-25. Epub 2016 May 27 doi: 10.1016/j.avsg.2016.02.011. PMID: 27238990
Yuan SM
Braz J Cardiovasc Surg 2016 Feb;31(1):52-9. doi: 10.5935/1678-9741.20150071. PMID: 27074275Free PMC Article

Recent systematic reviews

Loschi D, Santoro A, Rinaldi E, Bilman V, Chiesa R, Melissano G
J Vasc Surg 2023 Feb;77(2):642-649.e4. Epub 2022 Jul 15 doi: 10.1016/j.jvs.2022.07.010. PMID: 35850164
Konstantinou N, Antonopoulos CN, Tzanis K, Kölbel T, Peterß S, Pichlmaier M, Stana J, Tsilimparis N
Eur J Vasc Endovasc Surg 2022 May;63(5):759-767. Epub 2022 Feb 25 doi: 10.1016/j.ejvs.2022.02.027. PMID: 35459610
Mills B, Gest T
Clin Anat 2017 May;30(4):517-524. Epub 2017 Mar 25 doi: 10.1002/ca.22844. PMID: 28192856
Barr JG, Sepehripour AH, Jarral OA, Tsipas P, Kokotsakis J, Kourliouros A, Athanasiou T
Interact Cardiovasc Thorac Surg 2016 Jul;23(1):156-62. Epub 2016 Mar 21 doi: 10.1093/icvts/ivw058. PMID: 27001673Free PMC Article
Singh S, Hakim FA, Sharma A, Roy RR, Panse PM, Chandrasekaran K, Alegria JR, Mookadam F
Heart Lung Circ 2015 Feb;24(2):110-8. Epub 2014 Aug 23 doi: 10.1016/j.hlc.2014.08.006. PMID: 25442062

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...