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Locally Advanced Paraganglioma

MedGen UID:
1613911
•Concept ID:
C4524842
•
Neoplastic Process
Synonym: Locally Advanced Malignant Paraganglioma

Definition

A paraganglioma that has spread from its original site of growth to nearby tissues or lymph nodes. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLocally Advanced Paraganglioma

Professional guidelines

PubMed

Clinical consensus guideline on the management of phaeochromocytoma and paraganglioma in patients harbouring germline SDHD pathogenic variants.
Taïeb D, Wanna GB, Ahmad M, Lussey-Lepoutre C, Perrier ND, Nölting S, Amar L, Timmers HJLM, Schwam ZG, Estrera AL, Lim M, Pollom EL, Vitzthum L, Bourdeau I, Casey RT, Castinetti F, Clifton-Bligh R, Corssmit EPM, de Krijger RR, Del Rivero J, Eisenhofer G, Ghayee HK, Gimenez-Roqueplo AP, Grossman A, Imperiale A, Jansen JC, Jha A, Kerstens MN, Kunst HPM, Liu JK, Maher ER, Marchioni D, Mercado-Asis LB, Mete O, Naruse M, Nilubol N, Pandit-Taskar N, Sebag F, Tanabe A, Widimsky J, Meuter L, Lenders JWM, Pacak K
Lancet Diabetes Endocrinol 2023 May;11(5):345-361. Epub 2023 Mar 31 doi: 10.1016/S2213-8587(23)00038-4. PMID: 37011647Free PMC Article
Multidisciplinary practice guidelines for the diagnosis, genetic counseling and treatment of pheochromocytomas and paragangliomas.
Garcia-Carbonero R, Matute Teresa F, Mercader-Cidoncha E, Mitjavila-Casanovas M, Robledo M, Tena I, Alvarez-Escola C, Arístegui M, Bella-Cueto MR, Ferrer-Albiach C, Hanzu FA
Clin Transl Oncol 2021 Oct;23(10):1995-2019. Epub 2021 May 6 doi: 10.1007/s12094-021-02622-9. PMID: 33959901Free PMC Article
Metastatic pheochromocytoma and paraganglioma: recent advances in prognosis and management.
Hamidi O
Curr Opin Endocrinol Diabetes Obes 2019 Jun;26(3):146-154. doi: 10.1097/MED.0000000000000476. PMID: 30893083

Recent clinical studies

Diagnosis

Malignant phenotype and two SDHD mutations in a family with paraganglioma syndrome type 1.
Leidenz FB, Bastos-Rodrigues L, Oliveira M, Mamede M, Sarquis M, Friedman E, de Marco L
Genet Res (Camb) 2015 Mar 30;97:e3. doi: 10.1017/S0016672315000063. PMID: 25819804Free PMC Article
Locally advanced paraganglioma of the urinary bladder: a case report.
Beilan J, Lawton A, Hajdenberg J, Rosser CJ
BMC Res Notes 2013 Apr 18;6:156. doi: 10.1186/1756-0500-6-156. PMID: 23594404Free PMC Article

Prognosis

Malignant phenotype and two SDHD mutations in a family with paraganglioma syndrome type 1.
Leidenz FB, Bastos-Rodrigues L, Oliveira M, Mamede M, Sarquis M, Friedman E, de Marco L
Genet Res (Camb) 2015 Mar 30;97:e3. doi: 10.1017/S0016672315000063. PMID: 25819804Free PMC Article
Locally advanced paraganglioma of the urinary bladder: a case report.
Beilan J, Lawton A, Hajdenberg J, Rosser CJ
BMC Res Notes 2013 Apr 18;6:156. doi: 10.1186/1756-0500-6-156. PMID: 23594404Free PMC Article

Supplemental Content

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    Practice guidelines

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      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

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