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Complete Neonatal Hearing Loss

MedGen UID:
1768554
•Concept ID:
C4761243
•
Disease or Syndrome

Definition

Complete loss of the ability to detect or understand sounds present in an infant within its first month after birth. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVComplete Neonatal Hearing Loss

Professional guidelines

PubMed

New-born Hearing Screening Programmes in 2020: CODEPEH Recommendations.
Núñez-Batalla F, Jáudenes-Casaubón C, Sequí-Canet JM, Vivanco-Allende A, Zubicaray-Ugarteche J, Olleta Lascarro I
Acta Otorrinolaringol Esp (Engl Ed) 2021 Sep-Oct;72(5):312-323. doi: 10.1016/j.otoeng.2020.06.009. PMID: 34535222
Methodological quality of clinical guidelines for universal newborn hearing screening.
Kamenov K, Chadha S
Dev Med Child Neurol 2021 Jan;63(1):16-21. Epub 2020 Sep 27 doi: 10.1111/dmcn.14694. PMID: 32981050
Outcome and management of newborns with congenital cytomegalovirus infection.
Nicloux M, Peterman L, Parodi M, Magny JF
Arch Pediatr 2020 Apr;27(3):160-165. Epub 2020 Feb 29 doi: 10.1016/j.arcped.2020.01.006. PMID: 32127242

Recent clinical studies

Etiology

Associations of childhood hearing loss and adverse childhood experiences in deaf adults.
Hall WC, Dye TDV, Siddiqi S
PLoS One 2023;18(6):e0287024. Epub 2023 Jun 21 doi: 10.1371/journal.pone.0287024. PMID: 37343003Free PMC Article
Risk factors for hearing loss in neonates admitted to neonatal intensive care units.
Pan L, Fang X, Chen H, Zhai F, Chen J
J Laryngol Otol 2022 Dec;136(12):1196-1202. Epub 2021 Dec 20 doi: 10.1017/S002221512100414X. PMID: 36210183
Neurodevelopmental outcomes at age 5 among children born preterm: EPIPAGE-2 cohort study.
Pierrat V, Marchand-Martin L, Marret S, Arnaud C, Benhammou V, Cambonie G, Debillon T, Dufourg MN, Gire C, Goffinet F, Kaminski M, Lapillonne A, Morgan AS, Rozé JC, Twilhaar S, Charles MA, Ancel PY; EPIPAGE-2 writing group
BMJ 2021 Apr 28;373:n741. doi: 10.1136/bmj.n741. PMID: 33910920Free PMC Article
Outcome and management of newborns with congenital cytomegalovirus infection.
Nicloux M, Peterman L, Parodi M, Magny JF
Arch Pediatr 2020 Apr;27(3):160-165. Epub 2020 Feb 29 doi: 10.1016/j.arcped.2020.01.006. PMID: 32127242
Association Between Oxygen Saturation Targeting and Death or Disability in Extremely Preterm Infants in the Neonatal Oxygenation Prospective Meta-analysis Collaboration.
Askie LM, Darlow BA, Finer N, Schmidt B, Stenson B, Tarnow-Mordi W, Davis PG, Carlo WA, Brocklehurst P, Davies LC, Das A, Rich W, Gantz MG, Roberts RS, Whyte RK, Costantini L, Poets C, Asztalos E, Battin M, Halliday HL, Marlow N, Tin W, King A, Juszczak E, Morley CJ, Doyle LW, Gebski V, Hunter KE, Simes RJ; Neonatal Oxygenation Prospective Meta-analysis (NeOProM) Collaboration
JAMA 2018 Jun 5;319(21):2190-2201. doi: 10.1001/jama.2018.5725. PMID: 29872859Free PMC Article

Diagnosis

New-born Hearing Screening Programmes in 2020: CODEPEH Recommendations.
Núñez-Batalla F, Jáudenes-Casaubón C, Sequí-Canet JM, Vivanco-Allende A, Zubicaray-Ugarteche J, Olleta Lascarro I
Acta Otorrinolaringol Esp (Engl Ed) 2021 Sep-Oct;72(5):312-323. doi: 10.1016/j.otoeng.2020.06.009. PMID: 34535222
Neurodevelopmental outcomes at age 5 among children born preterm: EPIPAGE-2 cohort study.
Pierrat V, Marchand-Martin L, Marret S, Arnaud C, Benhammou V, Cambonie G, Debillon T, Dufourg MN, Gire C, Goffinet F, Kaminski M, Lapillonne A, Morgan AS, Rozé JC, Twilhaar S, Charles MA, Ancel PY; EPIPAGE-2 writing group
BMJ 2021 Apr 28;373:n741. doi: 10.1136/bmj.n741. PMID: 33910920Free PMC Article
Outcome and management of newborns with congenital cytomegalovirus infection.
Nicloux M, Peterman L, Parodi M, Magny JF
Arch Pediatr 2020 Apr;27(3):160-165. Epub 2020 Feb 29 doi: 10.1016/j.arcped.2020.01.006. PMID: 32127242
Association Between Oxygen Saturation Targeting and Death or Disability in Extremely Preterm Infants in the Neonatal Oxygenation Prospective Meta-analysis Collaboration.
Askie LM, Darlow BA, Finer N, Schmidt B, Stenson B, Tarnow-Mordi W, Davis PG, Carlo WA, Brocklehurst P, Davies LC, Das A, Rich W, Gantz MG, Roberts RS, Whyte RK, Costantini L, Poets C, Asztalos E, Battin M, Halliday HL, Marlow N, Tin W, King A, Juszczak E, Morley CJ, Doyle LW, Gebski V, Hunter KE, Simes RJ; Neonatal Oxygenation Prospective Meta-analysis (NeOProM) Collaboration
JAMA 2018 Jun 5;319(21):2190-2201. doi: 10.1001/jama.2018.5725. PMID: 29872859Free PMC Article
KBG syndrome.
Brancati F, Sarkozy A, Dallapiccola B
Orphanet J Rare Dis 2006 Dec 12;1:50. doi: 10.1186/1750-1172-1-50. PMID: 17163996Free PMC Article

Therapy

Two-year outcomes following a randomised platelet transfusion trial in preterm infants.
Moore CM, D'Amore A, Fustolo-Gunnink S, Hudson C, Newton A, Santamaria BL, Deary A, Hodge R, Hopkins V, Mora A, Llewelyn C, Venkatesh V, Khan R, Willoughby K, Onland W, Fijnvandraat K, New HV, Clarke P, Lopriore E, Watts T, Stanworth S, Curley A; PlaNeT2 MATISSE
Arch Dis Child Fetal Neonatal Ed 2023 Sep;108(5):452-457. Epub 2023 Feb 21 doi: 10.1136/archdischild-2022-324915. PMID: 36810309Free PMC Article
Cytomegalovirus-A Risk Factor for Childhood Hearing Loss: A Systematic Review.
Vos B, Noll D, Whittingham J, Pigeon M, Bagatto M, Fitzpatrick EM
Ear Hear 2021 Nov-Dec 01;42(6):1447-1461. doi: 10.1097/AUD.0000000000001055. PMID: 33928914
Clinical manifestations of congenital rubella syndrome: A review of our experience in Vietnam.
Toizumi M, Vo HM, Dang DA, Moriuchi H, Yoshida LM
Vaccine 2019 Jan 3;37(1):202-209. Epub 2018 Nov 30 doi: 10.1016/j.vaccine.2018.11.046. PMID: 30503658
Hearing impairment and hypoxia ischaemic encephalopathy: Incidence and associated factors.
Fitzgerald MP, Reynolds A, Garvey CM, Norman G, King MD, Hayes BC
Eur J Paediatr Neurol 2019 Jan;23(1):81-86. Epub 2018 Oct 10 doi: 10.1016/j.ejpn.2018.10.002. PMID: 30366758
Association Between Oxygen Saturation Targeting and Death or Disability in Extremely Preterm Infants in the Neonatal Oxygenation Prospective Meta-analysis Collaboration.
Askie LM, Darlow BA, Finer N, Schmidt B, Stenson B, Tarnow-Mordi W, Davis PG, Carlo WA, Brocklehurst P, Davies LC, Das A, Rich W, Gantz MG, Roberts RS, Whyte RK, Costantini L, Poets C, Asztalos E, Battin M, Halliday HL, Marlow N, Tin W, King A, Juszczak E, Morley CJ, Doyle LW, Gebski V, Hunter KE, Simes RJ; Neonatal Oxygenation Prospective Meta-analysis (NeOProM) Collaboration
JAMA 2018 Jun 5;319(21):2190-2201. doi: 10.1001/jama.2018.5725. PMID: 29872859Free PMC Article

Prognosis

Sudden Sensorineural Hearing Loss in Children-Management and Outcomes: A Meta-analysis.
Wood JW, Shaffer AD, Kitsko D, Chi DH
Laryngoscope 2021 Feb;131(2):425-434. Epub 2020 Jul 16 doi: 10.1002/lary.28829. PMID: 32673420
Outcome and management of newborns with congenital cytomegalovirus infection.
Nicloux M, Peterman L, Parodi M, Magny JF
Arch Pediatr 2020 Apr;27(3):160-165. Epub 2020 Feb 29 doi: 10.1016/j.arcped.2020.01.006. PMID: 32127242
Hearing impairment and hypoxia ischaemic encephalopathy: Incidence and associated factors.
Fitzgerald MP, Reynolds A, Garvey CM, Norman G, King MD, Hayes BC
Eur J Paediatr Neurol 2019 Jan;23(1):81-86. Epub 2018 Oct 10 doi: 10.1016/j.ejpn.2018.10.002. PMID: 30366758
Association Between Oxygen Saturation Targeting and Death or Disability in Extremely Preterm Infants in the Neonatal Oxygenation Prospective Meta-analysis Collaboration.
Askie LM, Darlow BA, Finer N, Schmidt B, Stenson B, Tarnow-Mordi W, Davis PG, Carlo WA, Brocklehurst P, Davies LC, Das A, Rich W, Gantz MG, Roberts RS, Whyte RK, Costantini L, Poets C, Asztalos E, Battin M, Halliday HL, Marlow N, Tin W, King A, Juszczak E, Morley CJ, Doyle LW, Gebski V, Hunter KE, Simes RJ; Neonatal Oxygenation Prospective Meta-analysis (NeOProM) Collaboration
JAMA 2018 Jun 5;319(21):2190-2201. doi: 10.1001/jama.2018.5725. PMID: 29872859Free PMC Article
Pediatric tinnitus: A clinical perspective.
Chan KH, Jensen EL, Gao D
Laryngoscope 2018 Mar;128(3):727-731. Epub 2017 Nov 6 doi: 10.1002/lary.26851. PMID: 29105770

Clinical prediction guides

Risk factors for hearing loss in neonates admitted to neonatal intensive care units.
Pan L, Fang X, Chen H, Zhai F, Chen J
J Laryngol Otol 2022 Dec;136(12):1196-1202. Epub 2021 Dec 20 doi: 10.1017/S002221512100414X. PMID: 36210183
Neurodevelopmental outcomes at age 5 among children born preterm: EPIPAGE-2 cohort study.
Pierrat V, Marchand-Martin L, Marret S, Arnaud C, Benhammou V, Cambonie G, Debillon T, Dufourg MN, Gire C, Goffinet F, Kaminski M, Lapillonne A, Morgan AS, Rozé JC, Twilhaar S, Charles MA, Ancel PY; EPIPAGE-2 writing group
BMJ 2021 Apr 28;373:n741. doi: 10.1136/bmj.n741. PMID: 33910920Free PMC Article
Outcome and management of newborns with congenital cytomegalovirus infection.
Nicloux M, Peterman L, Parodi M, Magny JF
Arch Pediatr 2020 Apr;27(3):160-165. Epub 2020 Feb 29 doi: 10.1016/j.arcped.2020.01.006. PMID: 32127242
Association Between Oxygen Saturation Targeting and Death or Disability in Extremely Preterm Infants in the Neonatal Oxygenation Prospective Meta-analysis Collaboration.
Askie LM, Darlow BA, Finer N, Schmidt B, Stenson B, Tarnow-Mordi W, Davis PG, Carlo WA, Brocklehurst P, Davies LC, Das A, Rich W, Gantz MG, Roberts RS, Whyte RK, Costantini L, Poets C, Asztalos E, Battin M, Halliday HL, Marlow N, Tin W, King A, Juszczak E, Morley CJ, Doyle LW, Gebski V, Hunter KE, Simes RJ; Neonatal Oxygenation Prospective Meta-analysis (NeOProM) Collaboration
JAMA 2018 Jun 5;319(21):2190-2201. doi: 10.1001/jama.2018.5725. PMID: 29872859Free PMC Article
KBG syndrome.
Brancati F, Sarkozy A, Dallapiccola B
Orphanet J Rare Dis 2006 Dec 12;1:50. doi: 10.1186/1750-1172-1-50. PMID: 17163996Free PMC Article

Recent systematic reviews

Barriers to and Facilitators of Early Hearing Detection and Intervention in the United States: A Systematic Review.
Findlen UM, Davenport CA, Cadieux J, Gehred A, Frush Holt R, Vaughn LM, Houston D, Hunter LL
Ear Hear 2023 May-Jun 01;44(3):448-459. Epub 2022 Dec 29 doi: 10.1097/AUD.0000000000001312. PMID: 36579673
Effectiveness of universal newborn hearing screening: A systematic review and meta-analysis.
Edmond K, Chadha S, Hunnicutt C, Strobel N, Manchaiah V, Yoshinga-Itano C; Universal Newborn Hearing Screening (UNHS) review group
J Glob Health 2022 Oct 19;12:12006. doi: 10.7189/jogh.12.12006. PMID: 36259421Free PMC Article
Cytomegalovirus-A Risk Factor for Childhood Hearing Loss: A Systematic Review.
Vos B, Noll D, Whittingham J, Pigeon M, Bagatto M, Fitzpatrick EM
Ear Hear 2021 Nov-Dec 01;42(6):1447-1461. doi: 10.1097/AUD.0000000000001055. PMID: 33928914
Sudden Sensorineural Hearing Loss in Children-Management and Outcomes: A Meta-analysis.
Wood JW, Shaffer AD, Kitsko D, Chi DH
Laryngoscope 2021 Feb;131(2):425-434. Epub 2020 Jul 16 doi: 10.1002/lary.28829. PMID: 32673420
Monitoring for postnatal hearing loss using risk factors: a systematic literature review.
Beswick R, Driscoll C, Kei J
Ear Hear 2012 Nov-Dec;33(6):745-56. doi: 10.1097/AUD.0b013e31825b1cd9. PMID: 22955247

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