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Classic Hodgkin lymphoma, lymphocyte-rich type

MedGen UID:
224769
Concept ID:
C1266194
Neoplastic Process
Synonym: Hodgkin's lymphoma, lymphocytic-histiocytic predominance
SNOMED CT: Hodgkin lymphoma, lymphocyte-rich (clinical) (118607005); Classical Hodgkin lymphoma, lymphocyte-rich (128799007); Hodgkin lymphoma, lymphocyte-rich (128799007); Hodgkin lymphoma, lymphocyte-rich (118607005); Lymphocyte-rich classical Hodgkin lymphoma (118607005)
 
Monarch Initiative: MONDO:0004604
Orphanet: ORPHA98845

Definition

A subtype of classic Hodgkin lymphoma with scattered Hodgkin and Reed-Sternberg cells and a nodular or less often diffuse cellular background consisting of small lymphocytes and with an absence of neutrophils and eosinophils. (WHO, 2008) [from NCI]

Term Hierarchy

Professional guidelines

PubMed

Aoki T, Jiang A, Xu A, Yin Y, Gamboa A, Milne K, Takata K, Miyata-Takata T, Chung S, Rai S, Wu S, Warren M, Strong C, Goodyear T, Morris K, Chong LC, Hav M, Colombo AR, Telenius A, Boyle M, Ben-Neriah S, Power M, Gerrie AS, Weng AP, Karsan A, Roth A, Farinha P, Scott DW, Savage KJ, Nelson BH, Merchant A, Steidl C
J Clin Oncol 2024 Mar 20;42(9):1077-1087. Epub 2023 Dec 19 doi: 10.1200/JCO.23.01115. PMID: 38113419Free PMC Article
Al-Juhaishi T, Ahmed S
Hematology Am Soc Hematol Educ Program 2023 Dec 8;2023(1):500-509. doi: 10.1182/hematology.2023000511. PMID: 38066938Free PMC Article
Miyazaki K
Jpn J Clin Oncol 2022 Jul 8;52(7):690-699. doi: 10.1093/jjco/hyac056. PMID: 35435235

Curated

NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®) Hodgkin Lymphoma, 2022

Recent clinical studies

Etiology

Aoki T, Jiang A, Xu A, Yin Y, Gamboa A, Milne K, Takata K, Miyata-Takata T, Chung S, Rai S, Wu S, Warren M, Strong C, Goodyear T, Morris K, Chong LC, Hav M, Colombo AR, Telenius A, Boyle M, Ben-Neriah S, Power M, Gerrie AS, Weng AP, Karsan A, Roth A, Farinha P, Scott DW, Savage KJ, Nelson BH, Merchant A, Steidl C
J Clin Oncol 2024 Mar 20;42(9):1077-1087. Epub 2023 Dec 19 doi: 10.1200/JCO.23.01115. PMID: 38113419Free PMC Article
Al-Juhaishi T, Ahmed S
Hematology Am Soc Hematol Educ Program 2023 Dec 8;2023(1):500-509. doi: 10.1182/hematology.2023000511. PMID: 38066938Free PMC Article
Nowakowski GS, Chiappella A, Gascoyne RD, Scott DW, Zhang Q, Jurczak W, Özcan M, Hong X, Zhu J, Jin J, Belada D, Bergua JM, Piazza F, Mócikova H, Molinari AL, Yoon DH, Cavallo F, Tani M, Yamamoto K, Izutsu K, Kato K, Czuczman M, Hersey S, Kilcoyne A, Russo J, Hudak K, Zhang J, Wade S, Witzig TE, Vitolo U
J Clin Oncol 2021 Apr 20;39(12):1317-1328. Epub 2021 Feb 23 doi: 10.1200/JCO.20.01366. PMID: 33621109Free PMC Article
Ferenczi K, Makkar HS
Clin Dermatol 2016 Nov-Dec;34(6):749-759. Epub 2016 Jul 10 doi: 10.1016/j.clindermatol.2016.07.010. PMID: 27968935
Ekstrand BC, Horning SJ
Curr Oncol Rep 2002 Sep;4(5):424-33. doi: 10.1007/s11912-002-0037-8. PMID: 12162918

Diagnosis

Xu J, Li S, Yin CC, Patel KP, Tang G, Wang W, Miranda RN, Garces S, Tang Z, Lin P, Medeiros LJ
Hum Pathol 2023 Apr;134:114-123. Epub 2022 Dec 28 doi: 10.1016/j.humpath.2022.12.014. PMID: 36584716
Huang Y, Hu S, Larson DP, Shi M, He R, Dave BJ, Greiner TC, Fu K, McPhail ED, Ketterling RP, Medeiros LJ, Yuan J
Am J Surg Pathol 2022 Jun 1;46(6):793-800. Epub 2022 Jan 24 doi: 10.1097/PAS.0000000000001828. PMID: 35067515
Wang W, Zhang Q, Medeiros LJ
Hum Pathol 2021 Nov;117:115-125. Epub 2021 May 28 doi: 10.1016/j.humpath.2021.05.008. PMID: 34058246
Ferenczi K, Makkar HS
Clin Dermatol 2016 Nov-Dec;34(6):749-759. Epub 2016 Jul 10 doi: 10.1016/j.clindermatol.2016.07.010. PMID: 27968935
Iyer VK
Indian J Pediatr 2013 Sep;80(9):756-63. Epub 2013 Aug 8 doi: 10.1007/s12098-013-1128-2. PMID: 23925793

Therapy

Al-Juhaishi T, Ahmed S
Hematology Am Soc Hematol Educ Program 2023 Dec 8;2023(1):500-509. doi: 10.1182/hematology.2023000511. PMID: 38066938Free PMC Article
Nowakowski GS, Chiappella A, Gascoyne RD, Scott DW, Zhang Q, Jurczak W, Özcan M, Hong X, Zhu J, Jin J, Belada D, Bergua JM, Piazza F, Mócikova H, Molinari AL, Yoon DH, Cavallo F, Tani M, Yamamoto K, Izutsu K, Kato K, Czuczman M, Hersey S, Kilcoyne A, Russo J, Hudak K, Zhang J, Wade S, Witzig TE, Vitolo U
J Clin Oncol 2021 Apr 20;39(12):1317-1328. Epub 2021 Feb 23 doi: 10.1200/JCO.20.01366. PMID: 33621109Free PMC Article
Cabrera TB, Wang W, Yedururi S, Slopis JM, Steiner RE, Rytting ME, Cuglievan B
J Pediatr Hematol Oncol 2021 May 1;43(4):e535-e538. doi: 10.1097/MPH.0000000000001811. PMID: 32366782
Xie W, Medeiros LJ, Li S, Yin CC, Khoury JD, Xu J
Curr Hematol Malig Rep 2020 Aug;15(4):372-381. doi: 10.1007/s11899-020-00589-y. PMID: 32394185
Dunleavy K, Grant C, Eberle FC, Pittaluga S, Jaffe ES, Wilson WH
Curr Hematol Malig Rep 2012 Sep;7(3):241-7. doi: 10.1007/s11899-012-0130-5. PMID: 22833351Free PMC Article

Prognosis

Aoki T, Jiang A, Xu A, Yin Y, Gamboa A, Milne K, Takata K, Miyata-Takata T, Chung S, Rai S, Wu S, Warren M, Strong C, Goodyear T, Morris K, Chong LC, Hav M, Colombo AR, Telenius A, Boyle M, Ben-Neriah S, Power M, Gerrie AS, Weng AP, Karsan A, Roth A, Farinha P, Scott DW, Savage KJ, Nelson BH, Merchant A, Steidl C
J Clin Oncol 2024 Mar 20;42(9):1077-1087. Epub 2023 Dec 19 doi: 10.1200/JCO.23.01115. PMID: 38113419Free PMC Article
Al-Juhaishi T, Ahmed S
Hematology Am Soc Hematol Educ Program 2023 Dec 8;2023(1):500-509. doi: 10.1182/hematology.2023000511. PMID: 38066938Free PMC Article
Nowakowski GS, Chiappella A, Gascoyne RD, Scott DW, Zhang Q, Jurczak W, Özcan M, Hong X, Zhu J, Jin J, Belada D, Bergua JM, Piazza F, Mócikova H, Molinari AL, Yoon DH, Cavallo F, Tani M, Yamamoto K, Izutsu K, Kato K, Czuczman M, Hersey S, Kilcoyne A, Russo J, Hudak K, Zhang J, Wade S, Witzig TE, Vitolo U
J Clin Oncol 2021 Apr 20;39(12):1317-1328. Epub 2021 Feb 23 doi: 10.1200/JCO.20.01366. PMID: 33621109Free PMC Article
Ferenczi K, Makkar HS
Clin Dermatol 2016 Nov-Dec;34(6):749-759. Epub 2016 Jul 10 doi: 10.1016/j.clindermatol.2016.07.010. PMID: 27968935
Ekstrand BC, Horning SJ
Curr Oncol Rep 2002 Sep;4(5):424-33. doi: 10.1007/s11912-002-0037-8. PMID: 12162918

Clinical prediction guides

Aoki T, Jiang A, Xu A, Yin Y, Gamboa A, Milne K, Takata K, Miyata-Takata T, Chung S, Rai S, Wu S, Warren M, Strong C, Goodyear T, Morris K, Chong LC, Hav M, Colombo AR, Telenius A, Boyle M, Ben-Neriah S, Power M, Gerrie AS, Weng AP, Karsan A, Roth A, Farinha P, Scott DW, Savage KJ, Nelson BH, Merchant A, Steidl C
J Clin Oncol 2024 Mar 20;42(9):1077-1087. Epub 2023 Dec 19 doi: 10.1200/JCO.23.01115. PMID: 38113419Free PMC Article
AbdullGaffar B, Raman L
Diagn Cytopathol 2022 Sep;50(9):E255-E263. Epub 2022 May 17 doi: 10.1002/dc.24976. PMID: 35581946
Nowakowski GS, Chiappella A, Gascoyne RD, Scott DW, Zhang Q, Jurczak W, Özcan M, Hong X, Zhu J, Jin J, Belada D, Bergua JM, Piazza F, Mócikova H, Molinari AL, Yoon DH, Cavallo F, Tani M, Yamamoto K, Izutsu K, Kato K, Czuczman M, Hersey S, Kilcoyne A, Russo J, Hudak K, Zhang J, Wade S, Witzig TE, Vitolo U
J Clin Oncol 2021 Apr 20;39(12):1317-1328. Epub 2021 Feb 23 doi: 10.1200/JCO.20.01366. PMID: 33621109Free PMC Article
Arlt A, von Bonin F, Rehberg T, Perez-Rubio P, Engelmann JC, Limm K, Reinke S, Dullin C, Sun X, Specht R, Maulhardt M, Linke F, Bunt G, Klapper W, Vockerodt M, Wilting J, Pukrop T, Dettmer K, Gronwald W, Oefner PJ, Spang R, Kube D
Mol Oncol 2020 Mar;14(3):571-589. Epub 2020 Jan 28 doi: 10.1002/1878-0261.12616. PMID: 31825135Free PMC Article
Carbone A, Spina M, Gloghini A, Tirelli U
Am J Hematol 2011 Feb;86(2):170-9. doi: 10.1002/ajh.21910. PMID: 21264899

Supplemental Content

Table of contents

    Clinical resources

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    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Curated

    • NCCN, 2022
      NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®) Hodgkin Lymphoma, 2022

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