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Anaplastic Brain Stem Glioma

MedGen UID:
231067
Concept ID:
C1332280
Neoplastic Process
Synonyms: Anaplastic Brainstem Glioma; Anaplastic Glioma of Brain Stem; Anaplastic Glioma of Brainstem; Anaplastic Glioma of the Brain Stem; Anaplastic Glioma of the Brainstem; Brain Stem Glioma, Grade III; Brainstem Glioma, Grade III; Grade 3 Brain Stem Glioma; Grade 3 Brainstem Glioma; Grade 3 Glioma of Brain Stem; Grade 3 Glioma of Brainstem; Grade 3 Glioma of the Brain Stem; Grade 3 Glioma of the Brainstem; Grade III Brain Stem Glioma; Grade III Brainstem Glioma; Grade III Glioma of Brain Stem; Grade III Glioma of Brainstem; Grade III Glioma of the Brain Stem; Grade III Glioma of the Brainstem; Undifferentiated Brain Stem Glioma; Undifferentiated Brainstem Glioma; Undifferentiated Glioma of Brain Stem; Undifferentiated Glioma of Brainstem; Undifferentiated Glioma of the Brain Stem; Undifferentiated Glioma of the Brainstem

Definition

An anaplastic glioma that arises from the brain stem. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAnaplastic Brain Stem Glioma

Professional guidelines

PubMed

Mohme M, Fritzsche FS, Mende KC, Matschke J, Löbel U, Kammler G, Westphal M, Emami P, Martens T
Neurosurg Focus 2018 Jun;44(6):E15. doi: 10.3171/2018.3.FOCUS1850. PMID: 29852760
Duffau H, Taillandier L
Neuro Oncol 2015 Mar;17(3):332-42. Epub 2014 Aug 2 doi: 10.1093/neuonc/nou153. PMID: 25087230Free PMC Article
Driever PH, Knüpfer MM, Cinatl J, Wolff JE
Klin Padiatr 1999 Jul-Aug;211(4):323-8. doi: 10.1055/s-2008-1043809. PMID: 10472571

Recent clinical studies

Etiology

Tumturk A, Gorkem SB, Ozmansur EN, Peduk Y, Arslan U, Gok V, Dogan H, Cetin BS, Sahin A, Gumus H, Guney A, Unal E, Kurtsoy A, Per H
Turk Neurosurg 2021;31(3):389-398. doi: 10.5137/1019-5149.JTN.31359-20.2. PMID: 33759163
Guerreiro Stucklin AS, Ryall S, Fukuoka K, Zapotocky M, Lassaletta A, Li C, Bridge T, Kim B, Arnoldo A, Kowalski PE, Zhong Y, Johnson M, Li C, Ramani AK, Siddaway R, Nobre LF, de Antonellis P, Dunham C, Cheng S, Boué DR, Finlay JL, Coven SL, de Prada I, Perez-Somarriba M, Faria CC, Grotzer MA, Rushing E, Sumerauer D, Zamecnik J, Krskova L, Garcia Ariza M, Cruz O, Morales La Madrid A, Solano P, Terashima K, Nakano Y, Ichimura K, Nagane M, Sakamoto H, Gil-da-Costa MJ, Silva R, Johnston DL, Michaud J, Wilson B, van Landeghem FKH, Oviedo A, McNeely PD, Crooks B, Fried I, Zhukova N, Hansford JR, Nageswararao A, Garzia L, Shago M, Brudno M, Irwin MS, Bartels U, Ramaswamy V, Bouffet E, Taylor MD, Tabori U, Hawkins C
Nat Commun 2019 Sep 25;10(1):4343. doi: 10.1038/s41467-019-12187-5. PMID: 31554817Free PMC Article
Cassia GSE, Alves CAPF, Taranath A, López NS, Oztekin O, Gonçalves FG, Patay Z
Top Magn Reson Imaging 2018 Dec;27(6):479-502. doi: 10.1097/RMR.0000000000000184. PMID: 30516696
Venkatesh HS, Tam LT, Woo PJ, Lennon J, Nagaraja S, Gillespie SM, Ni J, Duveau DY, Morris PJ, Zhao JJ, Thomas CJ, Monje M
Nature 2017 Sep 28;549(7673):533-537. Epub 2017 Sep 20 doi: 10.1038/nature24014. PMID: 28959975Free PMC Article
Eberhart CG
Brain Pathol 2011 Jan;21(1):96-104. doi: 10.1111/j.1750-3639.2010.00455.x. PMID: 21129063Free PMC Article

Diagnosis

Schaff LR, Mellinghoff IK
JAMA 2023 Feb 21;329(7):574-587. doi: 10.1001/jama.2023.0023. PMID: 36809318
Fares J, Ahmed AU, Ulasov IV, Sonabend AM, Miska J, Lee-Chang C, Balyasnikova IV, Chandler JP, Portnow J, Tate MC, Kumthekar P, Lukas RV, Grimm SA, Adams AK, Hébert CD, Strong TV, Amidei C, Arrieta VA, Zannikou M, Horbinski C, Zhang H, Burdett KB, Curiel DT, Sachdev S, Aboody KS, Stupp R, Lesniak MS
Lancet Oncol 2021 Aug;22(8):1103-1114. Epub 2021 Jun 29 doi: 10.1016/S1470-2045(21)00245-X. PMID: 34214495Free PMC Article
Tumturk A, Gorkem SB, Ozmansur EN, Peduk Y, Arslan U, Gok V, Dogan H, Cetin BS, Sahin A, Gumus H, Guney A, Unal E, Kurtsoy A, Per H
Turk Neurosurg 2021;31(3):389-398. doi: 10.5137/1019-5149.JTN.31359-20.2. PMID: 33759163
Cassia GSE, Alves CAPF, Taranath A, López NS, Oztekin O, Gonçalves FG, Patay Z
Top Magn Reson Imaging 2018 Dec;27(6):479-502. doi: 10.1097/RMR.0000000000000184. PMID: 30516696
Eberhart CG
Brain Pathol 2011 Jan;21(1):96-104. doi: 10.1111/j.1750-3639.2010.00455.x. PMID: 21129063Free PMC Article

Therapy

Schaff LR, Mellinghoff IK
JAMA 2023 Feb 21;329(7):574-587. doi: 10.1001/jama.2023.0023. PMID: 36809318
Fares J, Ahmed AU, Ulasov IV, Sonabend AM, Miska J, Lee-Chang C, Balyasnikova IV, Chandler JP, Portnow J, Tate MC, Kumthekar P, Lukas RV, Grimm SA, Adams AK, Hébert CD, Strong TV, Amidei C, Arrieta VA, Zannikou M, Horbinski C, Zhang H, Burdett KB, Curiel DT, Sachdev S, Aboody KS, Stupp R, Lesniak MS
Lancet Oncol 2021 Aug;22(8):1103-1114. Epub 2021 Jun 29 doi: 10.1016/S1470-2045(21)00245-X. PMID: 34214495Free PMC Article
Junca A, Villalva C, Tachon G, Rivet P, Cortes U, Guilloteau K, Balbous A, Godet J, Wager M, Karayan-Tapon L
Cancer Med 2017 Nov;6(11):2625-2634. Epub 2017 Sep 27 doi: 10.1002/cam4.1167. PMID: 28960893Free PMC Article
Soffietti R
Expert Opin Pharmacother 2004 Feb;5(2):295-306. doi: 10.1517/14656566.5.2.295. PMID: 14996626
Pech IV, Peterson K, Cairncross JG
Oncology (Williston Park) 1998 Apr;12(4):537-43, 547; discussion 547-8, 553. PMID: 9575527

Prognosis

Rehfeld M, Matschke J, Hagel C, Willenborg K, Glatzel M, Bernreuther C
J Cancer Res Clin Oncol 2021 Oct;147(10):2969-2982. Epub 2021 Jun 25 doi: 10.1007/s00432-021-03704-5. PMID: 34170383Free PMC Article
Cambruzzi E
Childs Nerv Syst 2018 May;34(5):809-815. Epub 2018 Mar 26 doi: 10.1007/s00381-018-3765-2. PMID: 29582169
Yazici G, Zorlu F, Cengiz M, Ozyigit G, Eren G, Yüce D, Varan A, Akyuz C, Akalan N, Gurkaynak M
Childs Nerv Syst 2016 Feb;32(2):291-7. Epub 2015 Dec 17 doi: 10.1007/s00381-015-2980-3. PMID: 26679932
Soffietti R
Expert Opin Pharmacother 2004 Feb;5(2):295-306. doi: 10.1517/14656566.5.2.295. PMID: 14996626
McComb RD, Burger PC
Neurol Clin 1985 Nov;3(4):711-28. PMID: 3001488

Clinical prediction guides

Trkova K, Sumerauer D, Krskova L, Vicha A, Koblizek M, Votava T, Priban V, Zapotocky M
Childs Nerv Syst 2023 Sep;39(9):2509-2513. Epub 2023 May 11 doi: 10.1007/s00381-023-05976-3. PMID: 37165121Free PMC Article
Schaff LR, Mellinghoff IK
JAMA 2023 Feb 21;329(7):574-587. doi: 10.1001/jama.2023.0023. PMID: 36809318
Andromidas F, Atashpanjeh S, Myers AJ, MacKinnon BE, Shaffer MM, Koob AO
Curr Neuropharmacol 2021;19(11):1952-1965. doi: 10.2174/1570159X19666210420095118. PMID: 33881971Free PMC Article
Annovazzi L, Mellai M, Caldera V, Valente G, Schiffer D
Cancer Genomics Proteomics 2011 May-Jun;8(3):139-47. PMID: 21518820
Soffietti R
Expert Opin Pharmacother 2004 Feb;5(2):295-306. doi: 10.1517/14656566.5.2.295. PMID: 14996626

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