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Neoplasm of mature T-cells or NK-cells

MedGen UID:: 233675
•Concept ID:: C1334640
•: Neoplastic Process

Synonyms:	mature T and NK neoplasms; Mature T-Cell and NK-Cell Neoplasm; mature T-cell and NK-cell neoplasm; Mature T-Cell Neoplasm; mature T-cell neoplasm; neoplasm of mature T-cells or NK-cells

Monarch Initiative:	MONDO:0005169

Definition

A group of neoplasms composed of T-lymphocytes with a mature (peripheral/post-thymic) immunophenotypic profile and/or NK-cells. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVNeoplasm of mature T-cells or NK-cells

Disorder by Site
- Hematopoietic and Lymphoid System Disorder
  - Hematologic disorder
    - Hematopoietic and lymphoid cell neoplasm
      - Lymphoid neoplasm
        T-cell and NK-cell neoplasm
        Neoplasm of mature T-cells or NK-cells
        Aggressive NK-cell leukemia
        Recurrent Aggressive NK-Cell Leukemia
        Refractory Aggressive NK-Cell Leukemia
        Chronic lymphoproliferative disorder of NK-cells
        Cutaneous Mature T-Cell and NK-Cell Neoplasm
        Cutaneous Adult T-Cell Leukemia/Lymphoma
        Cutaneous Angioimmunoblastic T-Cell Lymphoma
        Cutaneous Nasal Type Extranodal NK/T-Cell Lymphoma
        Lymphomatoid papulosis
        Lymphomatoid Papulosis with DUSP22-IRF4 Gene Rearrangement
        Type A Lymphomatoid Papulosis
        Type B Lymphomatoid Papulosis
        Type C Lymphomatoid Papulosis
        Type D Lymphomatoid Papulosis
        Type E Lymphomatoid Papulosis
        Primary Cutaneous CD30-Positive T-Cell Lymphoproliferative Disorder
        Borderline Primary Cutaneous CD30-Positive T-Cell Lymphoproliferative Disorder
        Primary cutaneous anaplastic large cell lymphoma
        Primary Cutaneous CD4-Positive Small/Medium T-Cell Lymphoproliferative Disorder
        Primary cutaneous T-cell lymphoma
        Advanced Primary Cutaneous T-Cell Non-Hodgkin Lymphoma
        Early Primary Cutaneous T-Cell Non-Hodgkin Lymphoma
        Mycosis fungoides
        Mycosis fungoides variant
        Primary Cutaneous Peripheral T-Cell Lymphoma, Rare Subtype
        Recurrent Primary Cutaneous T-Cell Non-Hodgkin Lymphoma
        Refractory Primary Cutaneous T-Cell Non-Hodgkin Lymphoma
        Sezary syndrome
        Subcutaneous panniculitis-like T-cell lymphoma
        EBV-positive T-cell lymphoproliferative disorder of childhood
        Hydroa vacciniforme-like lymphoma
        Systemic EBV-Positive T-Cell Lymphoma of Childhood
        Mature T-cell and NK-cell non-Hodgkin lymphoma
        Anaplastic large cell lymphoma
        Adult anaplastic large cell lymphoma
        Advanced Anaplastic Large Cell Lymphoma
        ALK-negative anaplastic large cell lymphoma
        ALK-positive anaplastic large cell lymphoma
        Anaplastic Large Cell Lymphoma, Giant Cell Rich Subtype
        Anaplastic Large Cell Lymphoma, Sarcomatoid Subtype
        Anaplastic Large Cell Lymphoma, Signet Ring-Like Subtype
        Central nervous system anaplastic large cell lymphoma
        Childhood anaplastic large cell lymphoma
        Common Variant Anaplastic Large Cell Lymphoma
        Localized Anaplastic Large Cell Lymphoma
        Lymphohistiocytic Variant Anaplastic Large Cell Lymphoma
        Noncutaneous Anaplastic Large Cell Lymphoma by Ann Arbor Stage
        Recurrent Anaplastic Large Cell Lymphoma
        Refractory Anaplastic Large Cell Lymphoma
        Small cell variant anaplastic large cell lymphoma
        Systemic Anaplastic Large Cell Lymphoma
        Central Nervous System Mature T-Cell and NK-Cell Non-Hodgkin Lymphoma
        Childhood Mature T-Cell and NK-Cell Non-Hodgkin Lymphoma
        Childhood Nasal Type Extranodal NK/T-Cell Lymphoma
        Extranodal nasal NK/T cell lymphoma
        Adult Nasal Type Extranodal NK/T-Cell Lymphoma
        Nasal Type NK/T-Cell Lymphoma by Ann Arbor Stage
        Recurrent Nasal Type Extranodal NK/T-Cell Lymphoma
        Refractory Nasal Type Extranodal NK/T-Cell Lymphoma
        Sinonasal Extranodal NK/T-Cell Lymphoma
        Testicular Nasal Type Extranodal NK/T-Cell Lymphoma
        Hepatosplenic T-cell lymphoma
        Recurrent Hepatosplenic T-Cell Lymphoma
        Refractory Hepatosplenic T-Cell Lymphoma
        Indolent T-Cell Non-Hodgkin Lymphoma
        Intestinal T-Cell Lymphoma
        Enteropathy-associated T-cell lymphoma
        Intestinal T-Cell Lymphoma, Not Otherwise Specified
        Monomorphic epitheliotropic intestinal T-cell lymphoma
        Leukemia-Lymphoma, Adult T-Cell
        Acute Adult T-Cell Leukemia/Lymphoma
        Adult T-Cell Leukemia/Lymphoma by Ann Arbor Stage
        Chronic Adult T-Cell Leukemia/Lymphoma
        Hodgkin-Like Adult T-Cell Leukemia/Lymphoma
        Lymphomatous Adult T-Cell Leukemia/Lymphoma
        Recurrent Adult T-Cell Leukemia/Lymphoma
        Refractory Adult T-Cell Leukemia/Lymphoma
        Smoldering Adult T-Cell Leukemia/Lymphoma
        Mature T- and NK-Cell Lymphoma by Ann Arbor Stage
        Angioimmunoblastic T-Cell Lymphoma by Ann Arbor Stage
        Ann Arbor Stage I Mature T- and NK-Cell Lymphoma
        Ann Arbor Stage II Mature T- and NK-Cell Lymphoma
        Ann Arbor Stage III Mature T- and NK-Cell Lymphoma
        Ann Arbor Stage IV Mature T- and NK-Cell Lymphoma
        Enteropathy-Associated T-Cell Lymphoma by Ann Arbor Stage
        Methotrexate-Associated Peripheral T-Cell Lymphoma
        Mycosis Fungoides and Sezary Syndrome
        Mycosis Fungoides and Sezary Syndrome by AJCC v7 Stage
        Mycosis Fungoides and Sezary Syndrome by AJCC v8 Stage
        Recurrent Mycosis Fungoides and Sezary Syndrome
        Refractory Mycosis Fungoides and Sezary Syndrome
        NK-Cell Lymphoma, Unclassifiable
        Recurrent NK-Cell Lymphoma, Unclassifiable
        Refractory NK-Cell Lymphoma, Unclassifiable
        Nodal Peripheral T-Cell Lymphoma of T Follicular Helper Cell Origin
        Angioimmunoblastic T-cell lymphoma
        Follicular T-Cell Lymphoma
        Nodal Peripheral T-Cell Lymphoma with TFH Phenotype
        Peripheral T-cell lymphoma
        Lymphoepithelioid Variant Peripheral T-Cell Lymphoma
        Primary EBV-Positive Nodal T-Cell or NK-Cell Lymphoma
        Recurrent Peripheral T-Cell Lymphoma, Not Otherwise Specified
        Refractory Peripheral T-Cell Lymphoma, Not Otherwise Specified
        Peripheral T-Cell Lymphoma, Unclassifiable
        Recurrent Mature T-Cell and NK-Cell Non-Hodgkin Lymphoma
        Recurrent Angioimmunoblastic T-Cell Lymphoma
        Recurrent Enteropathy-Associated T-Cell Lymphoma
        Recurrent Follicular T-Cell Lymphoma
        Recurrent Monomorphic Epitheliotropic Intestinal T-cell Lymphoma
        Recurrent Nodal Peripheral T-Cell Lymphoma with TFH Phenotype
        Recurrent Transformed T-cell Non-Hodgkin Lymphoma
        Refractory Mature T-Cell and NK-Cell Non-Hodgkin Lymphoma
        Refractory Angioimmunoblastic T-Cell Lymphoma
        Refractory Enteropathy-Associated T-Cell Lymphoma
        Refractory Follicular T-Cell Lymphoma
        Refractory Monomorphic Epitheliotropic Intestinal T-cell Lymphoma
        Refractory Nodal Peripheral T-Cell Lymphoma with TFH Phenotype
        Refractory Transformed T-cell Non-Hodgkin Lymphoma
        Recurrent Mature T-Cell and NK-Cell Neoplasm
        Recurrent T-Cell Large Granular Lymphocyte Leukemia
        Recurrent T-Cell Prolymphocytic Leukemia
        Refractory Mature T-Cell and NK-Cell Neoplasm
        Refractory T-Cell Large Granular Lymphocyte Leukemia
        Refractory T-Cell Prolymphocytic Leukemia
        T-cell large granular lymphocyte leukemia
        Splenic Manifestation of T-Cell Large Granular Lymphocyte Leukemia
        T-Cell Large Granular Lymphocyte Leukemia Expressing the T-Cell Receptor Gamma-Delta
        T-Cell Large Granular Lymphocyte Leukemia, Common Variant
        T-Cell Proliferation of Uncertain Malignant Potential
        Indolent T-Cell Lymphoproliferative Disorder of the Gastrointestinal Tract
        T-cell prolymphocytic leukemia
        Splenic Manifestation of T-Cell Prolymphocytic Leukemia
        T-Cell Prolymphocytic Leukemia, Cerebriform Cell Variant
        T-Cell Prolymphocytic Leukemia, Small Cell Variant

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Neoplasm of mature T-cells or NK-cells

Definition

Term Hierarchy

Professional guidelines

PubMed

Recent clinical studies

Etiology

Diagnosis

Therapy

Prognosis

Clinical prediction guides

Recent systematic reviews

Supplemental Content

Table of contents

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