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Urinary System Paraganglioma

MedGen UID:
234462
Concept ID:
C1336894
Neoplastic Process
Synonym: Urinary Tract Paraganglioma

Definition

An extra-adrenal paraganglioma that arises from the urinary system. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVUrinary System Paraganglioma

Professional guidelines

PubMed

Corssmit EP, Romijn JA
Eur J Endocrinol 2014 Dec;171(6):R231-43. Epub 2014 Jul 25 doi: 10.1530/EJE-14-0396. PMID: 25063320
Lenders JW, Duh QY, Eisenhofer G, Gimenez-Roqueplo AP, Grebe SK, Murad MH, Naruse M, Pacak K, Young WF Jr; Endocrine Society
J Clin Endocrinol Metab 2014 Jun;99(6):1915-42. doi: 10.1210/jc.2014-1498. PMID: 24893135
Ilias I, Pacak K
Horm Metab Res 2005 Dec;37(12):717-21. doi: 10.1055/s-2005-921091. PMID: 16372223

Recent clinical studies

Etiology

Petrák O, Krátká Z, Holaj R, Zítek M, Nguyen Nikrýnová T, Klímová J, Kološová B, Waldauf P, Michalský D, Novák K, Markvartová A, Zlatohlávek L, Grus T, Dušková J, Widimský J Jr, Zelinka T
Hypertension 2024 Mar;81(3):595-603. Epub 2023 Dec 28 doi: 10.1161/HYPERTENSIONAHA.123.21902. PMID: 38152977
Reel PS, Reel S, van Kralingen JC, Langton K, Lang K, Erlic Z, Larsen CK, Amar L, Pamporaki C, Mulatero P, Blanchard A, Kabat M, Robertson S, MacKenzie SM, Taylor AE, Peitzsch M, Ceccato F, Scaroni C, Reincke M, Kroiss M, Dennedy MC, Pecori A, Monticone S, Deinum J, Rossi GP, Lenzini L, McClure JD, Nind T, Riddell A, Stell A, Cole C, Sudano I, Prehn C, Adamski J, Gimenez-Roqueplo AP, Assié G, Arlt W, Beuschlein F, Eisenhofer G, Davies E, Zennaro MC, Jefferson E
EBioMedicine 2022 Oct;84:104276. Epub 2022 Sep 27 doi: 10.1016/j.ebiom.2022.104276. PMID: 36179553Free PMC Article
Corssmit EP, Romijn JA
Eur J Endocrinol 2014 Dec;171(6):R231-43. Epub 2014 Jul 25 doi: 10.1530/EJE-14-0396. PMID: 25063320
Lenders JW, Duh QY, Eisenhofer G, Gimenez-Roqueplo AP, Grebe SK, Murad MH, Naruse M, Pacak K, Young WF Jr; Endocrine Society
J Clin Endocrinol Metab 2014 Jun;99(6):1915-42. doi: 10.1210/jc.2014-1498. PMID: 24893135
Carney JA, Sizemore GW, Hayles AB
Pathobiol Annu 1978;8:105-53. PMID: 364372

Diagnosis

Reel PS, Reel S, van Kralingen JC, Langton K, Lang K, Erlic Z, Larsen CK, Amar L, Pamporaki C, Mulatero P, Blanchard A, Kabat M, Robertson S, MacKenzie SM, Taylor AE, Peitzsch M, Ceccato F, Scaroni C, Reincke M, Kroiss M, Dennedy MC, Pecori A, Monticone S, Deinum J, Rossi GP, Lenzini L, McClure JD, Nind T, Riddell A, Stell A, Cole C, Sudano I, Prehn C, Adamski J, Gimenez-Roqueplo AP, Assié G, Arlt W, Beuschlein F, Eisenhofer G, Davies E, Zennaro MC, Jefferson E
EBioMedicine 2022 Oct;84:104276. Epub 2022 Sep 27 doi: 10.1016/j.ebiom.2022.104276. PMID: 36179553Free PMC Article
Corssmit EP, Romijn JA
Eur J Endocrinol 2014 Dec;171(6):R231-43. Epub 2014 Jul 25 doi: 10.1530/EJE-14-0396. PMID: 25063320
Lenders JW, Duh QY, Eisenhofer G, Gimenez-Roqueplo AP, Grebe SK, Murad MH, Naruse M, Pacak K, Young WF Jr; Endocrine Society
J Clin Endocrinol Metab 2014 Jun;99(6):1915-42. doi: 10.1210/jc.2014-1498. PMID: 24893135
Whalen RK, Althausen AF, Daniels GH
J Urol 1992 Jan;147(1):1-10. doi: 10.1016/s0022-5347(17)37119-7. PMID: 1729490
Cryer PE
Clin Endocrinol Metab 1985 Feb;14(1):203-20. doi: 10.1016/s0300-595x(85)80070-0. PMID: 3893809

Therapy

Takenaka J, Watanabe S, Abe T, Hirata K, Uchiyama Y, Kimura R, Shinohara N, Kudo K
Ann Nucl Med 2023 Jan;37(1):10-17. Epub 2022 Oct 27 doi: 10.1007/s12149-022-01798-6. PMID: 36301465
Aksakallı T, Kozubaev B, Yapanoğlu T, Utlu A, Alper F, Bilen A, Bulut N
J Med Case Rep 2022 Dec 25;16(1):479. doi: 10.1186/s13256-022-03715-x. PMID: 36566235Free PMC Article
Reel PS, Reel S, van Kralingen JC, Langton K, Lang K, Erlic Z, Larsen CK, Amar L, Pamporaki C, Mulatero P, Blanchard A, Kabat M, Robertson S, MacKenzie SM, Taylor AE, Peitzsch M, Ceccato F, Scaroni C, Reincke M, Kroiss M, Dennedy MC, Pecori A, Monticone S, Deinum J, Rossi GP, Lenzini L, McClure JD, Nind T, Riddell A, Stell A, Cole C, Sudano I, Prehn C, Adamski J, Gimenez-Roqueplo AP, Assié G, Arlt W, Beuschlein F, Eisenhofer G, Davies E, Zennaro MC, Jefferson E
EBioMedicine 2022 Oct;84:104276. Epub 2022 Sep 27 doi: 10.1016/j.ebiom.2022.104276. PMID: 36179553Free PMC Article
Johnson JT, Cherian KE, Kapoor N, Paul TV
BMJ Case Rep 2020 Mar 12;13(3) doi: 10.1136/bcr-2019-233556. PMID: 32169989Free PMC Article
Itskovitz HD
J Cardiovasc Pharmacol 1980;2 Suppl 1:S47-60. doi: 10.1097/00005344-198000021-00006. PMID: 6154836

Prognosis

Takenaka J, Watanabe S, Abe T, Hirata K, Uchiyama Y, Kimura R, Shinohara N, Kudo K
Ann Nucl Med 2023 Jan;37(1):10-17. Epub 2022 Oct 27 doi: 10.1007/s12149-022-01798-6. PMID: 36301465
So JS, Epstein JI
Mod Pathol 2013 Oct;26(10):1365-70. Epub 2013 Apr 19 doi: 10.1038/modpathol.2013.76. PMID: 23599157
Siatelis A, Konstantinidis C, Volanis D, Leontara V, Thoma-Tsagli E, Delakas D
Minerva Urol Nefrol 2008 Jun;60(2):137-40. PMID: 18500228
Ilias I, Pacak K
Horm Metab Res 2005 Dec;37(12):717-21. doi: 10.1055/s-2005-921091. PMID: 16372223
Whalen RK, Althausen AF, Daniels GH
J Urol 1992 Jan;147(1):1-10. doi: 10.1016/s0022-5347(17)37119-7. PMID: 1729490

Clinical prediction guides

Reel PS, Reel S, van Kralingen JC, Langton K, Lang K, Erlic Z, Larsen CK, Amar L, Pamporaki C, Mulatero P, Blanchard A, Kabat M, Robertson S, MacKenzie SM, Taylor AE, Peitzsch M, Ceccato F, Scaroni C, Reincke M, Kroiss M, Dennedy MC, Pecori A, Monticone S, Deinum J, Rossi GP, Lenzini L, McClure JD, Nind T, Riddell A, Stell A, Cole C, Sudano I, Prehn C, Adamski J, Gimenez-Roqueplo AP, Assié G, Arlt W, Beuschlein F, Eisenhofer G, Davies E, Zennaro MC, Jefferson E
EBioMedicine 2022 Oct;84:104276. Epub 2022 Sep 27 doi: 10.1016/j.ebiom.2022.104276. PMID: 36179553Free PMC Article
De Leo A, Vara G, Paccapelo A, Balacchi C, Vicennati V, Tucci L, Pagotto U, Selva S, Ricci C, Alberici L, Minni F, Nanni C, Ambrosi F, Santini D, Golfieri R, Di Dalmazi G, Mosconi C
J Endocrinol Invest 2022 Oct;45(10):1935-1944. Epub 2022 Jun 10 doi: 10.1007/s40618-022-01826-2. PMID: 35680695Free PMC Article
Tu X, Zhang N, Zhuang X, Chen S, Luo X
BMC Urol 2021 Jul 8;21(1):98. doi: 10.1186/s12894-021-00863-y. PMID: 34238271Free PMC Article
Konosu-Fukaya S, Omata K, Tezuka Y, Ono Y, Aoyama Y, Satoh F, Fujishima F, Sasano H, Nakamura Y
Endocr Pathol 2018 Dec;29(4):302-309. doi: 10.1007/s12022-018-9544-5. PMID: 30155766
Terzolo M, Osella G, Alì A, Reimondo G, Borretta G, Magro GP, Luceri S, Paccotti P, Angeli A
Minerva Endocrinol 1995 Mar;20(1):69-78. PMID: 7651285

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