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Intracranial primitive neuroectodermal tumor

MedGen UID:
272770
•Concept ID:
C1334246
•
Neoplastic Process
Synonyms: brain primitive neuroectodermal tumor; brain primitive neuroectodermal tumour; Intracranial Embryonal Tumor, NOS; Intracranial Embryonal Tumor, Not Otherwise Specified; intracranial PNET; intracranial primitive neuroectodermal neoplasm; intracranial primitive neuroectodermal tumor; primitive neuroectodermal tumor of brain; primitive neuroectodermal tumour of brain
 
Monarch Initiative: MONDO:0003142

Definition

A central nervous system embryonal tumor, not otherwise specified arising from the brain. [from NCI]

Professional guidelines

PubMed

Guidelines for imaging retinoblastoma: imaging principles and MRI standardization.
de Graaf P, Göricke S, Rodjan F, Galluzzi P, Maeder P, Castelijns JA, Brisse HJ; European Retinoblastoma Imaging Collaboration (ERIC)
Pediatr Radiol 2012 Jan;42(1):2-14. Epub 2011 Aug 18 doi: 10.1007/s00247-011-2201-5. PMID: 21850471Free PMC Article

Recent clinical studies

Etiology

Trilateral retinoblastoma: neuroimaging characteristics and value of routine brain screening on admission.
Rodjan F, de Graaf P, Brisse HJ, Göricke S, Maeder P, Galluzzi P, Aerts I, Alapetite C, Desjardins L, Wieland R, Popovic MB, Diezi M, Munier FL, Hadjistilianou T, Knol DL, Moll AC, Castelijns JA
J Neurooncol 2012 Sep;109(3):535-44. Epub 2012 Jul 18 doi: 10.1007/s11060-012-0922-4. PMID: 22802019Free PMC Article
Trilateral retinoblastoma: is the location of the intracranial tumor important?
Paulino AC
Cancer 1999 Jul 1;86(1):135-41. PMID: 10391573

Diagnosis

A rare case of pediatric primary central nervous system differentiating neuroblastoma: an unusual and rare intracranial primitive neuroectodermal tumor (a case report).
Borni M, Znazen M, Mdhaffar N, Boudawara MZ
Pan Afr Med J 2021;40:33. Epub 2021 Sep 13 doi: 10.11604/pamj.2021.40.33.30587. PMID: 34795814Free PMC Article
Trilateral retinoblastoma: neuroimaging characteristics and value of routine brain screening on admission.
Rodjan F, de Graaf P, Brisse HJ, Göricke S, Maeder P, Galluzzi P, Aerts I, Alapetite C, Desjardins L, Wieland R, Popovic MB, Diezi M, Munier FL, Hadjistilianou T, Knol DL, Moll AC, Castelijns JA
J Neurooncol 2012 Sep;109(3):535-44. Epub 2012 Jul 18 doi: 10.1007/s11060-012-0922-4. PMID: 22802019Free PMC Article
Trilateral retinoblastoma: is the location of the intracranial tumor important?
Paulino AC
Cancer 1999 Jul 1;86(1):135-41. PMID: 10391573
Leptomeningeal fibrosis and the delayed diagnosis of a central nervous system neoplasm (primitive neuroectodermal tumor).
Robertson PL, Muraszko KM, Blaivas M, Brunberg JA
Pediatr Neurol 1997 Jan;16(1):74-8. doi: 10.1016/s0887-8994(96)00261-5. PMID: 9044409
Association of a suprasellar mass and intraocular retinoblastoma: a variant of pineal trilateral retinoblastoma?
Bejjani GK, Donahue DJ, Selby D, Cogen PH, Packer R
Pediatr Neurosurg 1996 Nov;25(5):269-75. doi: 10.1159/000121138. PMID: 9309793

Therapy

Refractory LCH With Secondary Intracranial PNET: A Case Report and Review of Literature.
Chayapathi V, Mahajan A, Kalra M
J Pediatr Hematol Oncol 2018 Mar;40(2):e117-e120. doi: 10.1097/MPH.0000000000000927. PMID: 28859038

Prognosis

A rare case of pediatric primary central nervous system differentiating neuroblastoma: an unusual and rare intracranial primitive neuroectodermal tumor (a case report).
Borni M, Znazen M, Mdhaffar N, Boudawara MZ
Pan Afr Med J 2021;40:33. Epub 2021 Sep 13 doi: 10.11604/pamj.2021.40.33.30587. PMID: 34795814Free PMC Article
Effects of Proton Center Closure on Pediatric Case Volume and Resident Education at an Academic Cancer Center.
Galle JO, Long DE, Lautenschlaeger T, Zellars RC, Watson GA, Ellsworth SG
Int J Radiat Oncol Biol Phys 2018 Mar 1;100(3):710-718. Epub 2017 Nov 8 doi: 10.1016/j.ijrobp.2017.10.055. PMID: 29413283
Refractory LCH With Secondary Intracranial PNET: A Case Report and Review of Literature.
Chayapathi V, Mahajan A, Kalra M
J Pediatr Hematol Oncol 2018 Mar;40(2):e117-e120. doi: 10.1097/MPH.0000000000000927. PMID: 28859038
Trilateral retinoblastoma: neuroimaging characteristics and value of routine brain screening on admission.
Rodjan F, de Graaf P, Brisse HJ, Göricke S, Maeder P, Galluzzi P, Aerts I, Alapetite C, Desjardins L, Wieland R, Popovic MB, Diezi M, Munier FL, Hadjistilianou T, Knol DL, Moll AC, Castelijns JA
J Neurooncol 2012 Sep;109(3):535-44. Epub 2012 Jul 18 doi: 10.1007/s11060-012-0922-4. PMID: 22802019Free PMC Article
Trilateral retinoblastoma: is the location of the intracranial tumor important?
Paulino AC
Cancer 1999 Jul 1;86(1):135-41. PMID: 10391573

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