U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Abnormal vestibular function

MedGen UID:
334848
Concept ID:
C1843865
Finding
Synonym: Vestibular dysfunction
 
HPO: HP:0001751

Definition

An abnormality of the functioning of the vestibular apparatus. [from HPO]

Conditions with this feature

Pendred syndrome
MedGen UID:
82890
Concept ID:
C0271829
Disease or Syndrome
Pendred syndrome / nonsyndromic enlarged vestibular aqueduct (PDS/NSEVA) comprises a phenotypic spectrum of sensorineural hearing loss (SNHL) that is usually congenital and often severe to profound (although mild-to-moderate progressive hearing impairment also occurs), vestibular dysfunction, and temporal bone abnormalities (bilateral enlarged vestibular aqueduct with or without cochlear hypoplasia). PDS also includes development of euthyroid goiter in late childhood to early adulthood whereas NSEVA does not.
Diabetes-deafness syndrome maternally transmitted
MedGen UID:
90979
Concept ID:
C0342289
Disease or Syndrome
Maternally inherited diabetes-deafness syndrome (MIDD) is a mitochondrial disorder characterized by onset of sensorineural hearing loss and diabetes in adulthood. Some patients may have additional features observed in mitochondrial disorders, including pigmentary retinopathy, ptosis, cardiomyopathy, myopathy, renal problems, and neuropsychiatric symptoms (Ballinger et al., 1992; Reardon et al., 1992; Guillausseau et al., 2001). The association of diabetes and deafness is observed with Wolfram syndrome (see 222300), Rogers syndrome (249270), and Herrmann syndrome (172500), but all 3 of these disorders have other clinical manifestations.
Autosomal recessive nonsyndromic hearing loss 25
MedGen UID:
237587
Concept ID:
C1414017
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the GRXCR1 gene.
Usher syndrome type 2D
MedGen UID:
292821
Concept ID:
C1568249
Disease or Syndrome
Usher syndrome type II (USH2) is characterized by the following: Congenital, bilateral sensorineural hearing loss that is mild to moderate in the low frequencies and severe to profound in the higher frequencies. Intact or variable vestibular responses. Retinitis pigmentosa (RP); progressive, bilateral, symmetric retinal degeneration that begins with night blindness and constricted visual fields (tunnel vision) and eventually includes decreased central visual acuity; the rate and degree of vision loss vary within and among families.
Episodic ataxia type 2
MedGen UID:
314039
Concept ID:
C1720416
Disease or Syndrome
Episodic ataxia is a genetically heterogeneous neurologic condition characterized by spells of incoordination and imbalance, often associated with progressive ataxia. Episodic ataxia type 2 is the most common form of EA (Jen et al., 2007). For a discussion of genetic heterogeneity of episodic ataxia, see EA1 (160120).
Autosomal recessive nonsyndromic hearing loss 70
MedGen UID:
760477
Concept ID:
C1824925
Disease or Syndrome
Autosomal recessive deafness-70 (DFNB70) is a neurologic disorder with a variable disease course. All individuals present with isolated congenital sensorineural hearing loss in infancy that appears to be stable for the first decades of life. Affected members of 1 family with longer follow-up developed a neurodegenerative disease in their forties, including ataxia with loss of ambulation, optic atrophy, dystonia or spasticity, and cognitive decline with psychiatric features. The later onset of additional symptoms in this family suggests that others with DFNB70 may be at risk of developing multisystem disease in mid-to-late adulthood. These reports indicate that there is a phenotypic spectrum of PNPT1-related disease manifestations (Von Ameln et al., 2012; Eaton et al., 2018).
Autosomal recessive nonsyndromic hearing loss 12
MedGen UID:
330455
Concept ID:
C1832394
Disease or Syndrome
An autosomal recessive nonsyndromic deafness that is characterized by prelingual onset with severe to profound, stable hearing loss and has material basis in mutation in the CDH23 gene on chromosome 10q22.
Autosomal dominant nonsyndromic hearing loss 11
MedGen UID:
331297
Concept ID:
C1832475
Disease or Syndrome
Autosomal dominant deafness-11 is a nonsyndromic form of progressive neurosensory hearing loss with postlingual onset. Some affected individuals have mild vestibular symptoms (summary by Sun et al., 2011).
Usher syndrome type 1D
MedGen UID:
322051
Concept ID:
C1832845
Disease or Syndrome
Usher syndrome type I (USH1) is characterized by congenital, bilateral, profound sensorineural hearing loss, vestibular areflexia, and adolescent-onset retinitis pigmentosa (RP). Unless fitted with a cochlear implant, individuals do not typically develop speech. RP, a progressive, bilateral, symmetric degeneration of rod and cone functions of the retina, develops in adolescence, resulting in progressively constricted visual fields and impaired visual acuity.
Autosomal recessive nonsyndromic hearing loss 7
MedGen UID:
322084
Concept ID:
C1832978
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the TMC1 gene.
Autosomal recessive nonsyndromic hearing loss 48
MedGen UID:
332149
Concept ID:
C1836199
Disease or Syndrome
DFNB48 is an autosomal recessive form of deafness. Affected individuals have prelingual onset of severe to profound sensorineural hearing loss affecting all frequencies (summary by Riazuddin et al., 2012).
Autosomal recessive nonsyndromic hearing loss 2
MedGen UID:
325485
Concept ID:
C1838701
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the MYO7A gene.
Hyperostosis cranialis interna
MedGen UID:
327093
Concept ID:
C1840404
Disease or Syndrome
Hyperostosis cranialis interna is a bone disorder characterized by endosteal hyperostosis and osteosclerosis of the calvaria and the skull base. The progressive bone overgrowth causes entrapment and dysfunction of cranial nerves I, II, V, VII, and VIII (Waterval et al., 2010).
Autosomal recessive nonsyndromic hearing loss 37
MedGen UID:
375076
Concept ID:
C1843028
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the MYO6 gene.
Sensory ataxic neuropathy, dysarthria, and ophthalmoparesis
MedGen UID:
375302
Concept ID:
C1843851
Disease or Syndrome
POLG-related disorders comprise a continuum of overlapping phenotypes that were clinically defined long before their molecular basis was known. Most affected individuals have some, but not all, of the features of a given phenotype; nonetheless, the following nomenclature can assist the clinician in diagnosis and management. Onset of the POLG-related disorders ranges from infancy to late adulthood. Alpers-Huttenlocher syndrome (AHS), one of the most severe phenotypes, is characterized by childhood-onset progressive and ultimately severe encephalopathy with intractable epilepsy and hepatic failure. Childhood myocerebrohepatopathy spectrum (MCHS) presents between the first few months of life and about age three years with developmental delay or dementia, lactic acidosis, and a myopathy with failure to thrive. Other findings can include liver failure, renal tubular acidosis, pancreatitis, cyclic vomiting, and hearing loss. Myoclonic epilepsy myopathy sensory ataxia (MEMSA) now describes the spectrum of disorders with epilepsy, myopathy, and ataxia without ophthalmoplegia. MEMSA now includes the disorders previously described as spinocerebellar ataxia with epilepsy (SCAE). The ataxia neuropathy spectrum (ANS) includes the phenotypes previously referred to as mitochondrial recessive ataxia syndrome (MIRAS) and sensory ataxia neuropathy dysarthria and ophthalmoplegia (SANDO). About 90% of persons in the ANS have ataxia and neuropathy as core features. Approximately two thirds develop seizures and almost one half develop ophthalmoplegia; clinical myopathy is rare. Autosomal recessive progressive external ophthalmoplegia (arPEO) is characterized by progressive weakness of the extraocular eye muscles resulting in ptosis and ophthalmoparesis (or paresis of the extraocular muscles) without associated systemic involvement; however, caution is advised because many individuals with apparently isolated arPEO at the onset develop other manifestations of POLG-related disorders over years or decades. Of note, in the ANS spectrum the neuropathy commonly precedes the onset of PEO by years to decades. Autosomal dominant progressive external ophthalmoplegia (adPEO) typically includes a generalized myopathy and often variable degrees of sensorineural hearing loss, axonal neuropathy, ataxia, depression, parkinsonism, hypogonadism, and cataracts (in what has been called "chronic progressive external ophthalmoplegia plus," or "CPEO+").
Autosomal dominant nonsyndromic hearing loss 44
MedGen UID:
334525
Concept ID:
C1843895
Disease or Syndrome
Any autosomal dominant nonsyndromic deafness in which the cause of the disease is a mutation in the CCDC50 gene.
Usher syndrome type 1G
MedGen UID:
339683
Concept ID:
C1847089
Disease or Syndrome
Usher syndrome type I (USH1) is characterized by congenital, bilateral, profound sensorineural hearing loss, vestibular areflexia, and adolescent-onset retinitis pigmentosa (RP). Unless fitted with a cochlear implant, individuals do not typically develop speech. RP, a progressive, bilateral, symmetric degeneration of rod and cone functions of the retina, develops in adolescence, resulting in progressively constricted visual fields and impaired visual acuity.
Autosomal recessive nonsyndromic hearing loss 67
MedGen UID:
343997
Concept ID:
C1853223
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the LHFPL5 gene.
Autosomal dominant nonsyndromic hearing loss 25
MedGen UID:
344221
Concept ID:
C1854158
Disease or Syndrome
Any autosomal dominant nonsyndromic deafness in which the cause of the disease is a mutation in the SLC17A8 gene.
Autosomal dominant nonsyndromic hearing loss 53
MedGen UID:
355336
Concept ID:
C1864957
Disease or Syndrome
An autosomal dominant nonsyndromic deafness that has material basis in variation in the chromosome region 14q11.2-q12.
Autosomal recessive nonsyndromic hearing loss 55
MedGen UID:
355338
Concept ID:
C1864962
Disease or Syndrome
An autosomal recessive nonsyndromic deafness that has material basis in variation in the chromosome region 4q12-q13.2.
Autosomal recessive nonsyndromic hearing loss 47
MedGen UID:
355339
Concept ID:
C1864964
Disease or Syndrome
An autosomal recessive nonsyndromic deafness that has material basis in variation in the chromosome region 2p25.1-p24.3.
Usher syndrome type 1F
MedGen UID:
356393
Concept ID:
C1865885
Disease or Syndrome
Usher syndrome type I (USH1) is characterized by congenital, bilateral, profound sensorineural hearing loss, vestibular areflexia, and adolescent-onset retinitis pigmentosa (RP). Unless fitted with a cochlear implant, individuals do not typically develop speech. RP, a progressive, bilateral, symmetric degeneration of rod and cone functions of the retina, develops in adolescence, resulting in progressively constricted visual fields and impaired visual acuity.
Deafness, congenital heart defects, and posterior embryotoxon
MedGen UID:
355614
Concept ID:
C1866053
Disease or Syndrome
Autosomal recessive nonsyndromic hearing loss 15
MedGen UID:
355626
Concept ID:
C1866094
Disease or Syndrome
This form of autosomal recessive deafness is sensorineural and nonsyndromic, and shows prelingual onset (summary by Charizopoulou et al., 2011).
Autosomal recessive nonsyndromic hearing loss 63
MedGen UID:
409872
Concept ID:
C1969621
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the LRTOMT gene.
Deafness-infertility syndrome
MedGen UID:
370197
Concept ID:
C1970187
Disease or Syndrome
CATSPER-related male infertility results from abnormalities in sperm and can be either CATSPER-related nonsyndromic male infertility (NSMI) or the deafness-infertility syndrome (DIS) when associated with non-progressive prelingual sensorineural hearing loss. Males with NSMI have infertility while females have no symptoms. Males with DIS have both infertility and hearing loss, while females have only hearing loss. Routine semen analysis typically identifies abnormalities in sperm number, morphology, and motility. Otologic examination and audiologic assessment can identify hearing loss.
Autosomal recessive nonsyndromic hearing loss 1A
MedGen UID:
388720
Concept ID:
C2673759
Disease or Syndrome
Nonsyndromic hearing loss and deafness (DFNB1) is characterized by congenital non-progressive mild-to-profound sensorineural hearing impairment. No other associated medical findings are present.
Autosomal recessive nonsyndromic hearing loss 1B
MedGen UID:
436381
Concept ID:
C2675235
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the GJB6 gene.
Autosomal recessive nonsyndromic hearing loss 77
MedGen UID:
412541
Concept ID:
C2746083
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the LOXHD1 gene.
Autosomal recessive nonsyndromic hearing loss 84A
MedGen UID:
462004
Concept ID:
C3150654
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the PTPRQ gene.
Autosomal dominant nonsyndromic hearing loss 4B
MedGen UID:
482927
Concept ID:
C3281297
Disease or Syndrome
Autosomal dominant deafness-4B is a form of nonsyndromic progressive sensorineural hearing loss with postlingual onset (summary by Wang et al., 2015)
Usher syndrome type 1K
MedGen UID:
761332
Concept ID:
C3539124
Disease or Syndrome
Usher syndrome type I (USH1) is characterized by congenital, bilateral, profound sensorineural hearing loss, vestibular areflexia, and adolescent-onset retinitis pigmentosa (RP). Unless fitted with a cochlear implant, individuals do not typically develop speech. RP, a progressive, bilateral, symmetric degeneration of rod and cone functions of the retina, develops in adolescence, resulting in progressively constricted visual fields and impaired visual acuity.
Usher syndrome type 1J
MedGen UID:
766858
Concept ID:
C3553944
Disease or Syndrome
Usher syndrome type I (USH1) is characterized by congenital, bilateral, profound sensorineural hearing loss, vestibular areflexia, and adolescent-onset retinitis pigmentosa (RP). Unless fitted with a cochlear implant, individuals do not typically develop speech. RP, a progressive, bilateral, symmetric degeneration of rod and cone functions of the retina, develops in adolescence, resulting in progressively constricted visual fields and impaired visual acuity.
Autosomal dominant nonsyndromic hearing loss 56
MedGen UID:
816500
Concept ID:
C3810170
Disease or Syndrome
Autosomal dominant deafness-56 is a form of nonsyndromic sensorineural hearing loss. Hearing impairment shows postlingual onset and is progressive (summary by Zhao et al., 2013).
Autosomal recessive nonsyndromic hearing loss 45
MedGen UID:
854732
Concept ID:
C3888030
Disease or Syndrome
An autosomal recessive nonsyndromic deafness that has material basis in variation in the chromosome region 1q43-q44.
Autosomal dominant nonsyndromic hearing loss 65
MedGen UID:
856147
Concept ID:
C3892048
Disease or Syndrome
TBC1D24-related disorders comprise a continuum of features that were originally described as distinct, recognized phenotypes: DOORS syndrome (deafness, onychodystrophy, osteodystrophy, mental retardation, and seizures). Profound sensorineural hearing loss, onychodystrophy, osteodystrophy, intellectual disability / developmental delay, and seizures. Familial infantile myoclonic epilepsy (FIME). Early-onset myoclonic seizures, focal epilepsy, dysarthria, and mild-to-moderate intellectual disability. Progressive myoclonus epilepsy (PME). Action myoclonus, tonic-clonic seizures, progressive neurologic decline, and ataxia. Early-infantile epileptic encephalopathy 16 (EIEE16). Epileptiform EEG abnormalities which themselves are believed to contribute to progressive disturbance in cerebral function. Autosomal recessive nonsyndromic hearing loss, DFNB86. Profound prelingual deafness. Autosomal dominant nonsyndromic hearing loss, DFNA65. Slowly progressive deafness with onset in the third decade, initially affecting the high frequencies.
Autosomal recessive nonsyndromic hearing loss 101
MedGen UID:
856148
Concept ID:
C3892049
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the GRXCR2 gene.
Autosomal recessive nonsyndromic hearing loss 103
MedGen UID:
863487
Concept ID:
C4015050
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the CLIC5 gene.
Autosomal dominant nonsyndromic hearing loss 40
MedGen UID:
896665
Concept ID:
C4084708
Disease or Syndrome
Any autosomal dominant nonsyndromic deafness in which the cause of the disease is a mutation in the CRYM gene.
Autosomal recessive nonsyndromic hearing loss 104
MedGen UID:
899775
Concept ID:
C4225298
Disease or Syndrome
Any autosomal recessive nonsyndromic deafness in which the cause of the disease is a mutation in the RIPOR2 gene.
Autosomal dominant nonsyndromic hearing loss 66
MedGen UID:
924418
Concept ID:
C4283893
Disease or Syndrome
Autosomal dominant deafness-66 is a form of nonsyndromic sensorineural hearing impairment with widely variable age at onset (Nyegaard et al., 2015).
Autosomal dominant nonsyndromic hearing loss 70
MedGen UID:
934742
Concept ID:
C4310775
Disease or Syndrome
Autosomal dominant deafness-70 is a form of nonsyndromic sensorineural hearing loss. Hearing impairment shows postlingual onset and is slowly progressive (Gao et al., 2015).
Hearing loss, autosomal dominant 71
MedGen UID:
1621646
Concept ID:
C4539881
Disease or Syndrome
Hearing loss, autosomal recessive 57
MedGen UID:
1631180
Concept ID:
C4693893
Disease or Syndrome
Autosomal recessive deafness-57 (DFNB57) is characterized by symmetric bilateral moderate to severe hearing loss, represented by gently downward-sloping audiograms. The hearing loss may be mildly progressive (Guan et al., 2018).
Hearing loss, autosomal recessive 110
MedGen UID:
1648377
Concept ID:
C4748162
Disease or Syndrome
Hearing loss, autosomal dominant 74
MedGen UID:
1648467
Concept ID:
C4748334
Disease or Syndrome
Autosomal dominant deafness-74 (DFNA74) is characterized by nonsyndromic postlingual progressive hearing loss, with onset in the third decade of life in most affected individuals (Wang et al., 2018).
Usher syndrome, type 4
MedGen UID:
1648315
Concept ID:
C4748364
Disease or Syndrome
An atypical form of Usher syndrome, here designated type IV (USH4), is an autosomal recessive disorder characterized by late onset of retinitis pigmentosa and usually late-onset of progressive sensorineural hearing loss without vestibular involvement (summary by Khateb et al., 2018). For a discussion of genetic heterogeneity of Usher syndrome, see 276900.
Hearing loss, autosomal recessive 99
MedGen UID:
1678930
Concept ID:
C4760579
Disease or Syndrome
DFNB99 is characterized by prelingual, severe to profound sensorineural hearing loss without vestibular dysfunction (Cheng et al., 2003).
Hearing loss, autosomal recessive 113
MedGen UID:
1674289
Concept ID:
C5193079
Disease or Syndrome
DFNB113 is characterized by postlingual progressive hearing impairment (Booth et al., 2018).
Hearing loss, autosomal recessive 100
MedGen UID:
1682525
Concept ID:
C5193087
Disease or Syndrome
DFNB100 is characterized by prelingual onset of profound sensorineural deafness without vestibular involvement (Yousaf et al., 2018).
Hearing loss, autosomal recessive 94
MedGen UID:
1679077
Concept ID:
C5193096
Disease or Syndrome
DFNB94 is characterized by prelingual profound sensorineural hearing loss (Simon et al., 2015).
Usher syndrome, type 1M
MedGen UID:
1684669
Concept ID:
C5231434
Disease or Syndrome
Usher syndrome type 1M (USH1M) is characterized by prelingual sensorineural hearing loss, vestibular dysfunction, and retinitis pigmentosa (Ahmed et al., 2018). For a general phenotypic description and discussion of genetic heterogeneity of Usher syndrome, see USH1 (276900).
Hearing loss, autosomal dominant 76
MedGen UID:
1710038
Concept ID:
C5394080
Disease or Syndrome
Autosomal dominant deafness-76 (DFNA76) is characterized by progressive or nonprogressive hearing loss with variable age at onset. Hearing loss is more severe at higher frequencies in most patients (Schrauwen et al., 2019; Morgan et al., 2019; Diaz-Horta et al., 2019).
Tolchin-Le Caignec syndrome
MedGen UID:
1724999
Concept ID:
C5436509
Disease or Syndrome
Tolchin-Le Caignec syndrome (TOLCAS) is a developmental disorder characterized by mildly to moderately impaired intellectual development and behavioral problems, such as autism, ADHD, labile mood, and aggressive episodes. Many patients have bony abnormalities, including osteochondroma, craniosynostosis, dysmorphic facies, arachnodactyly, and large head circumference. Rarely, additional congenital anomalies may also be observed. These additional features and the bony defects are highly variable (summary by Tolchin et al., 2020).
Hearing loss, autosomal dominant 79
MedGen UID:
1735338
Concept ID:
C5436772
Disease or Syndrome
Autosomal dominant deafness-79 (DFNA79) is a nonsyndromic form of progressive sensorineural hearing loss with age of onset ranging from 20 years to 65 years. Affected females appear to have milder hearing loss than males (Lu et al., 2020).
Hearing loss, autosomal recessive 117
MedGen UID:
1747842
Concept ID:
C5436937
Disease or Syndrome
Autosomal recessive deafness-117 (DFNB117) is characterized by nonsyndromic bilateral moderate-to-profound sensorineural deafness, with onset in early childhood (Vona et al., 2021).
Hearing loss, autosomal dominant 81
MedGen UID:
1794182
Concept ID:
C5561972
Disease or Syndrome
DFNA81 is characterized by postlingual onset of slowly progressive sensorineural hearing loss (Li et al., 2018).
Hearing loss, autosomal recessive 118, with cochlear aplasia
MedGen UID:
1794206
Concept ID:
C5561996
Disease or Syndrome
DFNB118 is characterized by congenital profound sensorineural hearing loss and cochlear aplasia (Bademci et al., 2020).
Usher syndrome type 3A
MedGen UID:
1830415
Concept ID:
C5779850
Disease or Syndrome
Any Usher syndrome in which the cause of the disease is a mutation in the CLRN1 gene.
Hearing loss, autosomal dominant 86
MedGen UID:
1840976
Concept ID:
C5830340
Disease or Syndrome
Autosomal dominant deafness-86 (DFNA86) is characterized by late-onset progressive hearing loss through p53 (TP53; 191170)-mediated hair cell apoptosis (Zhang et al., 2020).

Professional guidelines

PubMed

Rosenfeld RM, Tunkel DE, Schwartz SR, Anne S, Bishop CE, Chelius DC, Hackell J, Hunter LL, Keppel KL, Kim AH, Kim TW, Levine JM, Maksimoski MT, Moore DJ, Preciado DA, Raol NP, Vaughan WK, Walker EA, Monjur TM
Otolaryngol Head Neck Surg 2022 Feb;166(1_suppl):S1-S55. doi: 10.1177/01945998211065662. PMID: 35138954
Adam MP, Banka S, Bjornsson HT, Bodamer O, Chudley AE, Harris J, Kawame H, Lanpher BC, Lindsley AW, Merla G, Miyake N, Okamoto N, Stumpel CT, Niikawa N; Kabuki Syndrome Medical Advisory Board
J Med Genet 2019 Feb;56(2):89-95. Epub 2018 Dec 4 doi: 10.1136/jmedgenet-2018-105625. PMID: 30514738
Strupp M, Kim JS, Murofushi T, Straumann D, Jen JC, Rosengren SM, Della Santina CC, Kingma H
J Vestib Res 2017;27(4):177-189. doi: 10.3233/VES-170619. PMID: 29081426Free PMC Article

Recent clinical studies

Etiology

Kwon H, Kwon E, Kim HJ, Choi JY, Kim JS
Ann Clin Transl Neurol 2022 Oct;9(10):1616-1625. Epub 2022 Sep 2 doi: 10.1002/acn3.51661. PMID: 36056529Free PMC Article
Fu W, Wang Y, He F, Wei D, Bai Y, Han J, Wang X
Am J Otolaryngol 2021 Nov-Dec;42(6):103152. Epub 2021 Jun 29 doi: 10.1016/j.amjoto.2021.103152. PMID: 34218215
Adams ME, Telian SA, Kane RL, Butler M
Otolaryngol Head Neck Surg 2016 Jun;154(6):982-96. Epub 2016 Mar 1 doi: 10.1177/0194599816630963. PMID: 26932962
Thierry B, Blanchard M, Leboulanger N, Parodi M, Wiener-Vacher SR, Garabedian EN, Loundon N
Int J Pediatr Otorhinolaryngol 2015 Feb;79(2):101-4. Epub 2014 Nov 22 doi: 10.1016/j.ijporl.2014.11.002. PMID: 25500550
Maes L, De Kegel A, Van Waelvelde H, Dhooge I
Otol Neurotol 2014 Dec;35(10):e343-7. doi: 10.1097/MAO.0000000000000597. PMID: 25275872

Diagnosis

Akin FW, Swan AA, Kalvesmaki A, Hall CD, Riska KM, Stressman KD, Nguyen H, Amuan M, Pugh MJ
Am J Audiol 2023 Nov;32(3S):706-720. Epub 2023 Apr 11 doi: 10.1044/2023_AJA-22-00150. PMID: 37040302
Cohen HS, Sangi-Haghpeykar H, Watts M, Sweeney AD, Peng AS
Laryngoscope 2021 Jun;131(6):1382-1385. Epub 2021 Feb 26 doi: 10.1002/lary.29487. PMID: 33635545Free PMC Article
Tang H, Chen Y, Cen Z, Ouyang Z, Lou D, Tan Y, Luo W
Int J Neurosci 2021 Jun;131(6):521-526. Epub 2020 Sep 24 doi: 10.1080/00207454.2020.1825419. PMID: 32942935
da Costa Monsanto R, Kasemodel ALP, Tomaz A, de Oliveira Penido N
Otolaryngol Head Neck Surg 2020 Nov;163(5):1018-1024. Epub 2020 Jun 23 doi: 10.1177/0194599820931491. PMID: 32571144
Adams ME, Telian SA, Kane RL, Butler M
Otolaryngol Head Neck Surg 2016 Jun;154(6):982-96. Epub 2016 Mar 1 doi: 10.1177/0194599816630963. PMID: 26932962

Therapy

Janky KL, Patterson JN, Shepard NT, Thomas MLA, Honaker JA
J Am Acad Audiol 2017 Oct;28(9):778-785. doi: 10.3766/jaaa.16138. PMID: 28972467Free PMC Article
Handelsman JA, Nasr SZ, Pitts C, King WM
Pediatr Pulmonol 2017 Sep;52(9):1157-1162. Epub 2017 Jul 24 doi: 10.1002/ppul.23763. PMID: 28737283
Adams ME, Telian SA, Kane RL, Butler M
Otolaryngol Head Neck Surg 2016 Jun;154(6):982-96. Epub 2016 Mar 1 doi: 10.1177/0194599816630963. PMID: 26932962
Peterka RJ
J Vestib Res 2005;15(5-6):291-311. PMID: 16614475

Prognosis

Akin FW, Swan AA, Kalvesmaki A, Hall CD, Riska KM, Stressman KD, Nguyen H, Amuan M, Pugh MJ
Am J Audiol 2023 Nov;32(3S):706-720. Epub 2023 Apr 11 doi: 10.1044/2023_AJA-22-00150. PMID: 37040302
Kwon H, Kwon E, Kim HJ, Choi JY, Kim JS
Ann Clin Transl Neurol 2022 Oct;9(10):1616-1625. Epub 2022 Sep 2 doi: 10.1002/acn3.51661. PMID: 36056529Free PMC Article
Fu W, Wang Y, He F, Wei D, Bai Y, Han J, Wang X
Am J Otolaryngol 2021 Nov-Dec;42(6):103152. Epub 2021 Jun 29 doi: 10.1016/j.amjoto.2021.103152. PMID: 34218215
Cohen HS, Sangi-Haghpeykar H, Watts M, Sweeney AD, Peng AS
Laryngoscope 2021 Jun;131(6):1382-1385. Epub 2021 Feb 26 doi: 10.1002/lary.29487. PMID: 33635545Free PMC Article
Adams ME, Telian SA, Kane RL, Butler M
Otolaryngol Head Neck Surg 2016 Jun;154(6):982-96. Epub 2016 Mar 1 doi: 10.1177/0194599816630963. PMID: 26932962

Clinical prediction guides

Akin FW, Swan AA, Kalvesmaki A, Hall CD, Riska KM, Stressman KD, Nguyen H, Amuan M, Pugh MJ
Am J Audiol 2023 Nov;32(3S):706-720. Epub 2023 Apr 11 doi: 10.1044/2023_AJA-22-00150. PMID: 37040302
Kwon H, Kwon E, Kim HJ, Choi JY, Kim JS
Ann Clin Transl Neurol 2022 Oct;9(10):1616-1625. Epub 2022 Sep 2 doi: 10.1002/acn3.51661. PMID: 36056529Free PMC Article
Fu W, Wang Y, He F, Wei D, Bai Y, Han J, Wang X
Am J Otolaryngol 2021 Nov-Dec;42(6):103152. Epub 2021 Jun 29 doi: 10.1016/j.amjoto.2021.103152. PMID: 34218215
da Costa Monsanto R, Kasemodel ALP, Tomaz A, de Oliveira Penido N
Otolaryngol Head Neck Surg 2020 Nov;163(5):1018-1024. Epub 2020 Jun 23 doi: 10.1177/0194599820931491. PMID: 32571144
Adams ME, Telian SA, Kane RL, Butler M
Otolaryngol Head Neck Surg 2016 Jun;154(6):982-96. Epub 2016 Mar 1 doi: 10.1177/0194599816630963. PMID: 26932962

Recent systematic reviews

Adams ME, Telian SA, Kane RL, Butler M
Otolaryngol Head Neck Surg 2016 Jun;154(6):982-96. Epub 2016 Mar 1 doi: 10.1177/0194599816630963. PMID: 26932962

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...