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Wilms tumor 3(WT3)

MedGen UID:
349770
Concept ID:
C1860265
Disease or Syndrome
Synonym: WT3
 
Monarch Initiative: MONDO:0008683
OMIM®: 194090

Authors:
Joyce T Turner  |  Jack Brzezinski  |  Jeffrey S Dome   view full author information

Clinical features

From HPO
Nephroblastoma
MedGen UID:
10221
Concept ID:
C0027708
Neoplastic Process
The presence of a nephroblastoma, which is a neoplasm of the kidney that primarily affects children.

Professional guidelines

PubMed

Pérez LM, Naidu SI, Joseph DB
J Urol 1998 Sep;160(3 Pt 2):1207-11; discussion 1216. doi: 10.1097/00005392-199809020-00070. PMID: 9719312

Recent clinical studies

Etiology

Gupta AC, Owens CA, Shrestha S, Lee C, Smith SA, Weathers RE, Netherton T, Balter PA, Kry SF, Followill DS, Griffin KT, Long JP, Armstrong GT, Howell RM
Biomed Phys Eng Express 2022 Feb 1;8(2) doi: 10.1088/2057-1976/ac3f4e. PMID: 34874300Free PMC Article
Sandberg JK, Chi YY, Smith EA, Servaes S, Hoffer FA, Mullen EA, Perlman EJ, Tornwall B, Ehrlich PF, Geller JI, Grundy PE, Fernandez CV, Dome JS, Khanna G
AJR Am J Roentgenol 2020 May;214(5):987-994. Epub 2020 Mar 11 doi: 10.2214/AJR.19.22301. PMID: 32160052Free PMC Article
Su WT, Rutigliano DN, Gholizadeh M, Jarnagin WR, Blumgart LH, La Quaglia MP
Cancer 2007 May 15;109(10):2089-92. doi: 10.1002/cncr.22650. PMID: 17410597
Yang CP, Hung IJ, Jaing TH, Shih LY, Chang WH
Pediatr Hematol Oncol 2005 Sep;22(6):463-81. doi: 10.1080/08880010591002233. PMID: 16169813
DeBaun MR, Brown M, Kessler L
Med Pediatr Oncol 1996 Nov;27(5):415-21. doi: 10.1002/(SICI)1096-911X(199611)27:5<415::AID-MPO5>3.0.CO;2-P. PMID: 8827068

Diagnosis

Sandberg JK, Chi YY, Smith EA, Servaes S, Hoffer FA, Mullen EA, Perlman EJ, Tornwall B, Ehrlich PF, Geller JI, Grundy PE, Fernandez CV, Dome JS, Khanna G
AJR Am J Roentgenol 2020 May;214(5):987-994. Epub 2020 Mar 11 doi: 10.2214/AJR.19.22301. PMID: 32160052Free PMC Article
Pappo AS, Armstrong GT, Liu W, Srivastava DK, McDonald A, Leisenring WM, Hammond S, Stovall M, Neglia JP, Robison LL
Pediatr Blood Cancer 2013 Mar;60(3):461-6. Epub 2012 Aug 8 doi: 10.1002/pbc.24266. PMID: 22887858Free PMC Article
Yang CP, Hung IJ, Jaing TH, Shih LY, Chang WH
Pediatr Hematol Oncol 2005 Sep;22(6):463-81. doi: 10.1080/08880010591002233. PMID: 16169813
Willman JH, White K, Coffin CM
Pediatr Dev Pathol 2001 Jan-Feb;4(1):46-52. doi: 10.1007/s100240010122. PMID: 11200490
Nakissa N, Constine LS, Rubin P, Strohl R
Oncology 1985;42(6):358-63. doi: 10.1159/000226064. PMID: 2999670

Therapy

Oosterom N, Gooskens SLM, Renfro LA, Perlman EJ, van den Heuvel-Eibrink MM, Hamilton TE, Green DM, Grundy PE, Daw NC, Geller JI, Dome JS, Fernandez CV, Mullen EA
J Clin Oncol 2023 Sep 10;41(26):4247-4256. Epub 2023 Jun 21 doi: 10.1200/JCO.22.02555. PMID: 37343199Free PMC Article
Su WT, Rutigliano DN, Gholizadeh M, Jarnagin WR, Blumgart LH, La Quaglia MP
Cancer 2007 May 15;109(10):2089-92. doi: 10.1002/cncr.22650. PMID: 17410597
DeBaun MR, Brown M, Kessler L
Med Pediatr Oncol 1996 Nov;27(5):415-21. doi: 10.1002/(SICI)1096-911X(199611)27:5<415::AID-MPO5>3.0.CO;2-P. PMID: 8827068
Alanko S, Salmi TT, Pelliniemi TT
Med Pediatr Oncol 1995 Jun;24(6):373-8. doi: 10.1002/mpo.2950240607. PMID: 7715543
Pochedly C
N Y State J Med 1971 Jun 15;71(12):1526-8. PMID: 4325181

Prognosis

Pappo AS, Armstrong GT, Liu W, Srivastava DK, McDonald A, Leisenring WM, Hammond S, Stovall M, Neglia JP, Robison LL
Pediatr Blood Cancer 2013 Mar;60(3):461-6. Epub 2012 Aug 8 doi: 10.1002/pbc.24266. PMID: 22887858Free PMC Article
Su WT, Rutigliano DN, Gholizadeh M, Jarnagin WR, Blumgart LH, La Quaglia MP
Cancer 2007 May 15;109(10):2089-92. doi: 10.1002/cncr.22650. PMID: 17410597
Yang CP, Hung IJ, Jaing TH, Shih LY, Chang WH
Pediatr Hematol Oncol 2005 Sep;22(6):463-81. doi: 10.1080/08880010591002233. PMID: 16169813
Pérez LM, Naidu SI, Joseph DB
J Urol 1998 Sep;160(3 Pt 2):1207-11; discussion 1216. doi: 10.1097/00005392-199809020-00070. PMID: 9719312
Alanko S, Salmi TT, Pelliniemi TT
Med Pediatr Oncol 1995 Jun;24(6):373-8. doi: 10.1002/mpo.2950240607. PMID: 7715543

Clinical prediction guides

Pérez LM, Naidu SI, Joseph DB
J Urol 1998 Sep;160(3 Pt 2):1207-11; discussion 1216. doi: 10.1097/00005392-199809020-00070. PMID: 9719312

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