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Ossifying Renal Tumor of Infancy

MedGen UID:
362189
Concept ID:
C1882198
Neoplastic Process

Definition

A benign neoplasm of the kidney occurring in infants. It develops as an intracalyceal mass and is characterized by the presence of osteoid formation, osteoblast-like cells, and spindle cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVOssifying Renal Tumor of Infancy

Recent clinical studies

Etiology

Fang YW, Song HC, Sun N, Zhang WP
BMC Urol 2022 Jun 22;22(1):89. doi: 10.1186/s12894-022-01042-3. PMID: 35733141Free PMC Article
El-Husseini TK, Egail SA, Al-Orf AM, Mostert C
Saudi Med J 2005 Dec;26(12):1978-9. PMID: 16380785
Glick RD, Hicks MJ, Nuchtern JG, Wesson DE, Olutoye OO, Cass DL
J Pediatr Surg 2004 Apr;39(4):522-5. doi: 10.1016/j.jpedsurg.2003.12.007. PMID: 15065020
Ito J, Shinohara N, Koyanagi T, Hanioka K
Pathol Int 1998 Feb;48(2):151-9. doi: 10.1111/j.1440-1827.1998.tb03885.x. PMID: 9589480

Diagnosis

Vaillancourt B, Oligny L, Déry J, Franc-Guimond J, Soglio DB
Pediatr Dev Pathol 2017 Nov-Dec;20(6):511-516. Epub 2017 Feb 13 doi: 10.1177/1093526617693105. PMID: 29187024
Guan W, Yan Y, He W, Qiao M, Liu Y, Wang Y, Jiang B, Yu W, Wang R, Wang L
Pathol Res Pract 2016 Nov;212(11):1004-1009. Epub 2016 Sep 2 doi: 10.1016/j.prp.2016.08.008. PMID: 27633911
Lee SH, Choi YH, Kim WS, Cheon JE, Moon KC
Pediatr Radiol 2014 May;44(5):625-8. Epub 2014 Jan 10 doi: 10.1007/s00247-013-2855-2. PMID: 24407230
Hu J, Wu Y, Qi J, Zhang C, Lv F
J Pediatr Surg 2013 Feb;48(2):e37-40. doi: 10.1016/j.jpedsurg.2012.12.020. PMID: 23414900
Lowe LH, Isuani BH, Heller RM, Stein SM, Johnson JE, Navarro OM, Hernanz-Schulman M
Radiographics 2000 Nov-Dec;20(6):1585-603. doi: 10.1148/radiographics.20.6.g00nv051585. PMID: 11112813

Prognosis

Fang YW, Song HC, Sun N, Zhang WP
BMC Urol 2022 Jun 22;22(1):89. doi: 10.1186/s12894-022-01042-3. PMID: 35733141Free PMC Article
El-Husseini TK, Egail SA, Al-Orf AM, Mostert C
Saudi Med J 2005 Dec;26(12):1978-9. PMID: 16380785
Glick RD, Hicks MJ, Nuchtern JG, Wesson DE, Olutoye OO, Cass DL
J Pediatr Surg 2004 Apr;39(4):522-5. doi: 10.1016/j.jpedsurg.2003.12.007. PMID: 15065020
Ito J, Shinohara N, Koyanagi T, Hanioka K
Pathol Int 1998 Feb;48(2):151-9. doi: 10.1111/j.1440-1827.1998.tb03885.x. PMID: 9589480

Clinical prediction guides

Fang YW, Song HC, Sun N, Zhang WP
BMC Urol 2022 Jun 22;22(1):89. doi: 10.1186/s12894-022-01042-3. PMID: 35733141Free PMC Article

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