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Anaplastic Medulloblastoma

MedGen UID:
457446
Concept ID:
C2985220
Neoplastic Process

Definition

A medulloblastoma characterized by marked nuclear pleomorphism, and high mitotic activity. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAnaplastic Medulloblastoma

Professional guidelines

PubMed

Klesse LJ, Bowers DC
CNS Drugs 2010 Apr;24(4):285-301. doi: 10.2165/11530140-000000000-00000. PMID: 20297854

Recent clinical studies

Etiology

Cassia GSE, Alves CAPF, Taranath A, López NS, Oztekin O, Gonçalves FG, Patay Z
Top Magn Reson Imaging 2018 Dec;27(6):479-502. doi: 10.1097/RMR.0000000000000184. PMID: 30516696
von Bueren AO, Kortmann RD, von Hoff K, Friedrich C, Mynarek M, Müller K, Goschzik T, Zur Mühlen A, Gerber N, Warmuth-Metz M, Soerensen N, Deinlein F, Benesch M, Zwiener I, Kwiecien R, Faldum A, Bode U, Fleischhack G, Hovestadt V, Kool M, Jones D, Northcott P, Kuehl J, Pfister S, Pietsch T, Rutkowski S
J Clin Oncol 2016 Dec;34(34):4151-4160. Epub 2016 Oct 31 doi: 10.1200/JCO.2016.67.2428. PMID: 27863192
Klesse LJ, Bowers DC
CNS Drugs 2010 Apr;24(4):285-301. doi: 10.2165/11530140-000000000-00000. PMID: 20297854
von Hoff K, Hartmann W, von Bueren AO, Gerber NU, Grotzer MA, Pietsch T, Rutkowski S
Pediatr Blood Cancer 2010 Mar;54(3):369-76. doi: 10.1002/pbc.22339. PMID: 19908297
Louis DN, Ohgaki H, Wiestler OD, Cavenee WK, Burger PC, Jouvet A, Scheithauer BW, Kleihues P
Acta Neuropathol 2007 Aug;114(2):97-109. Epub 2007 Jul 6 doi: 10.1007/s00401-007-0243-4. PMID: 17618441Free PMC Article

Diagnosis

Yilmaz H, Akcay E, Benek HB
Turk Neurosurg 2021;31(6):980-985. doi: 10.5137/1019-5149.JTN.32143-20.2. PMID: 34542903
Cassia GSE, Alves CAPF, Taranath A, López NS, Oztekin O, Gonçalves FG, Patay Z
Top Magn Reson Imaging 2018 Dec;27(6):479-502. doi: 10.1097/RMR.0000000000000184. PMID: 30516696
von Bueren AO, Kortmann RD, von Hoff K, Friedrich C, Mynarek M, Müller K, Goschzik T, Zur Mühlen A, Gerber N, Warmuth-Metz M, Soerensen N, Deinlein F, Benesch M, Zwiener I, Kwiecien R, Faldum A, Bode U, Fleischhack G, Hovestadt V, Kool M, Jones D, Northcott P, Kuehl J, Pfister S, Pietsch T, Rutkowski S
J Clin Oncol 2016 Dec;34(34):4151-4160. Epub 2016 Oct 31 doi: 10.1200/JCO.2016.67.2428. PMID: 27863192
Klesse LJ, Bowers DC
CNS Drugs 2010 Apr;24(4):285-301. doi: 10.2165/11530140-000000000-00000. PMID: 20297854
von Hoff K, Hartmann W, von Bueren AO, Gerber NU, Grotzer MA, Pietsch T, Rutkowski S
Pediatr Blood Cancer 2010 Mar;54(3):369-76. doi: 10.1002/pbc.22339. PMID: 19908297

Therapy

Mynarek M, von Hoff K, Pietsch T, Ottensmeier H, Warmuth-Metz M, Bison B, Pfister S, Korshunov A, Sharma T, Jaeger N, Ryzhova M, Zheludkova O, Golanov A, Rushing EJ, Hasselblatt M, Koch A, Schüller U, von Deimling A, Sahm F, Sill M, Riemenschneider MJ, Dohmen H, Monoranu CM, Sommer C, Staszewski O, Mawrin C, Schittenhelm J, Brück W, Filipski K, Hartmann C, Meinhardt M, Pietschmann K, Haberler C, Slavc I, Gerber NU, Grotzer M, Benesch M, Schlegel PG, Deinlein F, von Bueren AO, Friedrich C, Juhnke BO, Obrecht D, Fleischhack G, Kwiecien R, Faldum A, Kortmann RD, Kool M, Rutkowski S
J Clin Oncol 2020 Jun 20;38(18):2028-2040. Epub 2020 Apr 24 doi: 10.1200/JCO.19.03057. PMID: 32330099
Indini A, Schiavello E, Biassoni V, Bergamaschi L, Magni MC, Puma N, Chiaravalli S, Pallotti F, Seregni E, Diletto B, Pecori E, Gandola L, Poggi G, Massimino M
J Neurooncol 2017 Jan;131(2):349-357. Epub 2016 Oct 21 doi: 10.1007/s11060-016-2306-7. PMID: 27770281
von Bueren AO, Kortmann RD, von Hoff K, Friedrich C, Mynarek M, Müller K, Goschzik T, Zur Mühlen A, Gerber N, Warmuth-Metz M, Soerensen N, Deinlein F, Benesch M, Zwiener I, Kwiecien R, Faldum A, Bode U, Fleischhack G, Hovestadt V, Kool M, Jones D, Northcott P, Kuehl J, Pfister S, Pietsch T, Rutkowski S
J Clin Oncol 2016 Dec;34(34):4151-4160. Epub 2016 Oct 31 doi: 10.1200/JCO.2016.67.2428. PMID: 27863192
von Bueren AO, Friedrich C, von Hoff K, Kwiecien R, Müller K, Pietsch T, Warmuth-Metz M, Hau P, Benesch M, Kuehl J, Kortmann RD, Rutkowski S
Eur J Cancer 2015 Nov;51(16):2434-43. Epub 2015 Aug 5 doi: 10.1016/j.ejca.2015.06.124. PMID: 26254812
Klesse LJ, Bowers DC
CNS Drugs 2010 Apr;24(4):285-301. doi: 10.2165/11530140-000000000-00000. PMID: 20297854

Prognosis

Yilmaz H, Akcay E, Benek HB
Turk Neurosurg 2021;31(6):980-985. doi: 10.5137/1019-5149.JTN.32143-20.2. PMID: 34542903
Huang PI, Lin SC, Lee YY, Ho DM, Guo WY, Chang KP, Chang FC, Liang ML, Chen HH, Liu YM, Yen SH, Wong TT, Chen YW
Childs Nerv Syst 2017 Aug;33(8):1285-1294. Epub 2017 May 9 doi: 10.1007/s00381-017-3435-9. PMID: 28488086
von Bueren AO, Kortmann RD, von Hoff K, Friedrich C, Mynarek M, Müller K, Goschzik T, Zur Mühlen A, Gerber N, Warmuth-Metz M, Soerensen N, Deinlein F, Benesch M, Zwiener I, Kwiecien R, Faldum A, Bode U, Fleischhack G, Hovestadt V, Kool M, Jones D, Northcott P, Kuehl J, Pfister S, Pietsch T, Rutkowski S
J Clin Oncol 2016 Dec;34(34):4151-4160. Epub 2016 Oct 31 doi: 10.1200/JCO.2016.67.2428. PMID: 27863192
Klesse LJ, Bowers DC
CNS Drugs 2010 Apr;24(4):285-301. doi: 10.2165/11530140-000000000-00000. PMID: 20297854
von Hoff K, Hartmann W, von Bueren AO, Gerber NU, Grotzer MA, Pietsch T, Rutkowski S
Pediatr Blood Cancer 2010 Mar;54(3):369-76. doi: 10.1002/pbc.22339. PMID: 19908297

Clinical prediction guides

von Bueren AO, Friedrich C, von Hoff K, Kwiecien R, Müller K, Pietsch T, Warmuth-Metz M, Hau P, Benesch M, Kuehl J, Kortmann RD, Rutkowski S
Eur J Cancer 2015 Nov;51(16):2434-43. Epub 2015 Aug 5 doi: 10.1016/j.ejca.2015.06.124. PMID: 26254812
Yeom KW, Mobley BC, Lober RM, Andre JB, Partap S, Vogel H, Barnes PD
AJR Am J Roentgenol 2013 Apr;200(4):895-903. doi: 10.2214/AJR.12.9249. PMID: 23521467
Li Y, Guessous F, Johnson EB, Eberhart CG, Li XN, Shu Q, Fan S, Lal B, Laterra J, Schiff D, Abounader R
Lab Invest 2008 Feb;88(2):98-111. Epub 2007 Dec 3 doi: 10.1038/labinvest.3700702. PMID: 18059365
Raso A, Negri F, Gregorio A, Nozza P, Mascelli S, De Marco P, Merello E, Milanaccio C, Ravegnani M, Cama A, Garrè ML, Capra V
Neuropathol Appl Neurobiol 2008 Jun;34(3):306-15. Epub 2007 Nov 9 doi: 10.1111/j.1365-2990.2007.00896.x. PMID: 17995922
Stearns D, Chaudhry A, Abel TW, Burger PC, Dang CV, Eberhart CG
Cancer Res 2006 Jan 15;66(2):673-81. doi: 10.1158/0008-5472.CAN-05-1580. PMID: 16423996

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