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Abnormal atrial arrangement

MedGen UID:
488996
•Concept ID:
C2959688
•
Congenital Abnormality
Synonym: Abnormal location of heart atrium
SNOMED CT: Abnormal atrial arrangement (445898001)
 
HPO: HP:0011535

Definition

Abnormality of the spatial relationship of the atria to other components of the heart. [from HPO]

Professional guidelines

PubMed

Human Laterality Disorders: Pathogenesis, Clinical Manifestations, Diagnosis, and Management.
Soofi M, Alpert MA, Barbadora J, Mukerji B, Mukerji V
Am J Med Sci 2021 Sep;362(3):233-242. Epub 2021 May 28 doi: 10.1016/j.amjms.2021.05.020. PMID: 34052215
National Heart Foundation of Australia and Cardiac Society of Australia and New Zealand: Australian clinical guidelines for the management of heart failure 2018.
Atherton JJ, Sindone A, De Pasquale CG, Driscoll A, MacDonald PS, Hopper I, Kistler P, Briffa TG, Wong J, Abhayaratna WP, Thomas L, Audehm R, Newton PJ, O'Loughlin J, Connell C, Branagan M
Med J Aust 2018 Oct 15;209(8):363-369. Epub 2018 Aug 2 doi: 10.5694/mja18.00647. PMID: 30067937
Prenatal diagnosis of criss-cross heart: sonographical and pathological features of five cases.
Li S, Luo G, Norwitz ER, Wang C, Ouyang S, Yao Y, Wen H, Chen C, Fu Q, Xia X, Bi J, Zhu J
J Perinatol 2013 Feb;33(2):98-102. Epub 2012 May 3 doi: 10.1038/jp.2012.56. PMID: 22555779

Recent clinical studies

Etiology

Imaging characteristics and associations of left atrioventricular valve atresia and patent aortic root with isometric atrial appendages on multidetector CT.
Verma M, Ojha V, Mukherjee A, Kumar S, Ramakrishnan S, Jagia P
J Card Surg 2022 Jul;37(7):1928-1936. Epub 2022 Apr 8 doi: 10.1111/jocs.16468. PMID: 35396763
The surgical anatomy of hearts with isomeric atrial appendages-implications for surgical management.
Spicer DE, Chowdhury UK, Anderson RH, Pandey NN, Sankhyan LK, George N, Goja S, Malik V
Eur J Cardiothorac Surg 2022 Jun 15;62(1) doi: 10.1093/ejcts/ezac139. PMID: 35234855
Human Laterality Disorders: Pathogenesis, Clinical Manifestations, Diagnosis, and Management.
Soofi M, Alpert MA, Barbadora J, Mukerji B, Mukerji V
Am J Med Sci 2021 Sep;362(3):233-242. Epub 2021 May 28 doi: 10.1016/j.amjms.2021.05.020. PMID: 34052215
Atrial septal defects, supravalvular aortic stenosis and syndromes predisposing to aneurysm of large vessels.
Baglivo M, Dassati S, Krasi G, Fanelli F, Kurti D, Bonelli A, Arabia G, Fabbicatore D, Muneretto C, Bertelli M
Acta Biomed 2019 Sep 30;90(10-S):53-57. doi: 10.23750/abm.v90i10-S.8760. PMID: 31577255Free PMC Article
Disharmonious Patterns of Heterotaxy and Isomerism: How Often Are the Classic Patterns Breached?
Yim D, Nagata H, Lam CZ, Grosse-Wortmann L, Seed M, Jaeggi E, Yoo SJ
Circ Cardiovasc Imaging 2018 Feb;11(2):e006917. doi: 10.1161/CIRCIMAGING.117.006917. PMID: 29444810

Diagnosis

The surgical anatomy of hearts with isomeric atrial appendages-implications for surgical management.
Spicer DE, Chowdhury UK, Anderson RH, Pandey NN, Sankhyan LK, George N, Goja S, Malik V
Eur J Cardiothorac Surg 2022 Jun 15;62(1) doi: 10.1093/ejcts/ezac139. PMID: 35234855
Human Laterality Disorders: Pathogenesis, Clinical Manifestations, Diagnosis, and Management.
Soofi M, Alpert MA, Barbadora J, Mukerji B, Mukerji V
Am J Med Sci 2021 Sep;362(3):233-242. Epub 2021 May 28 doi: 10.1016/j.amjms.2021.05.020. PMID: 34052215
Atrial septal defects, supravalvular aortic stenosis and syndromes predisposing to aneurysm of large vessels.
Baglivo M, Dassati S, Krasi G, Fanelli F, Kurti D, Bonelli A, Arabia G, Fabbicatore D, Muneretto C, Bertelli M
Acta Biomed 2019 Sep 30;90(10-S):53-57. doi: 10.23750/abm.v90i10-S.8760. PMID: 31577255Free PMC Article
Ivemark Syndrome.
Masiwal P, Chenthil KS, Priyadarsini B, Gnanaprakasam J, Srihari I
J Assoc Physicians India 2016 May;64(5):73-75. PMID: 27735157
Echocardiographic characteristics of the criss-cross heart.
Yang YL, Wang XF, Cheng TO, Xie MX, Lü Q, He L, Lu XF, Wang J, Li L, Anderson RH
Int J Cardiol 2010 Apr 15;140(2):133-7. Epub 2009 Sep 16 doi: 10.1016/j.ijcard.2009.08.039. PMID: 19762095

Therapy

Conduction velocity is reduced in the posterior wall of hypertrophic cardiomyopathy patients with normal bipolar voltage undergoing ablation for paroxysmal atrial fibrillation.
Zahid S, Malik T, Peterson C, Tarabanis C, Dai M, Katz M, Bernstein SA, Barbhaiya C, Park DS, Knotts RJ, Holmes DS, Kushnir A, Aizer A, Chinitz LA, Jankelson L
J Interv Card Electrophysiol 2024 Jan;67(1):203-210. Epub 2023 Mar 23 doi: 10.1007/s10840-023-01533-9. PMID: 36952090
Impact of bilateral bidirectional Glenn anastomosis on staged Fontan strategy and Fontan circulation.
Imai K, Hoashi T, Okuda N, Ohuchi H, Kurosaki K, Ichikawa H
Eur J Cardiothorac Surg 2021 Oct 22;60(4):930-938. doi: 10.1093/ejcts/ezab162. PMID: 33895850
Unusual long survival in a case of heterotaxy and polysplenia.
Doello K, Conde V, Perez MC, Mendoza I, Mesas C, Prados J
Surg Radiol Anat 2021 Apr;43(4):607-611. Epub 2020 Sep 29 doi: 10.1007/s00276-020-02586-5. PMID: 32995936
Double-decker repair of partial anomalous pulmonary venous return into the superior vena cava.
Hongu H, Yamagishi M, Maeda Y, Itatani K, Asada S, Fujita S, Yaku H
J Thorac Cardiovasc Surg 2019 May;157(5):1970-1977. Epub 2019 Jan 26 doi: 10.1016/j.jtcvs.2019.01.057. PMID: 30824350
Cardiovascular anatomy in children with bidirectional Glenn anastomosis, regarding the transcatheter Fontan completion.
Sizarov A, Raimondi F, Bonnet D, Boudjemline Y
Arch Cardiovasc Dis 2018 Apr;111(4):257-269. Epub 2017 Nov 13 doi: 10.1016/j.acvd.2017.08.003. PMID: 29146107

Prognosis

Human Laterality Disorders: Pathogenesis, Clinical Manifestations, Diagnosis, and Management.
Soofi M, Alpert MA, Barbadora J, Mukerji B, Mukerji V
Am J Med Sci 2021 Sep;362(3):233-242. Epub 2021 May 28 doi: 10.1016/j.amjms.2021.05.020. PMID: 34052215
Atrial septal defects, supravalvular aortic stenosis and syndromes predisposing to aneurysm of large vessels.
Baglivo M, Dassati S, Krasi G, Fanelli F, Kurti D, Bonelli A, Arabia G, Fabbicatore D, Muneretto C, Bertelli M
Acta Biomed 2019 Sep 30;90(10-S):53-57. doi: 10.23750/abm.v90i10-S.8760. PMID: 31577255Free PMC Article
Long-term survival and phenotypic spectrum in heterotaxy syndrome: A 25-year follow-up experience.
Baban A, Cantarutti N, Adorisio R, Lombardi R, Calcagni G, Piano Mortari E, Dallapiccola B, Marino B, Iorio FS, Carsetti R, Digilio MC, Giannico S, Drago F, Carotti A
Int J Cardiol 2018 Oct 1;268:100-105. doi: 10.1016/j.ijcard.2018.02.050. PMID: 30041775
Abnormalities of Fetal Situs: An Overview and Literature Review.
Lambert TE, Kuller J, Small M, Rhee E, Barker P
Obstet Gynecol Surv 2016 Jan;71(1):33-8. doi: 10.1097/OGX.0000000000000262. PMID: 26819133
Right heart and pulmonary vessels structure and function.
D'Alto M, Scognamiglio G, Dimopoulos K, Bossone E, Vizza D, Romeo E, Vonk-Noordergraaf A, Gaine S, Peacock A, Naeije R
Echocardiography 2015 Jan;32 Suppl 1:S3-10. Epub 2014 Sep 19 doi: 10.1111/echo.12227. PMID: 25244348

Clinical prediction guides

The surgical anatomy of hearts with isomeric atrial appendages-implications for surgical management.
Spicer DE, Chowdhury UK, Anderson RH, Pandey NN, Sankhyan LK, George N, Goja S, Malik V
Eur J Cardiothorac Surg 2022 Jun 15;62(1) doi: 10.1093/ejcts/ezac139. PMID: 35234855
Long-term survival and phenotypic spectrum in heterotaxy syndrome: A 25-year follow-up experience.
Baban A, Cantarutti N, Adorisio R, Lombardi R, Calcagni G, Piano Mortari E, Dallapiccola B, Marino B, Iorio FS, Carsetti R, Digilio MC, Giannico S, Drago F, Carotti A
Int J Cardiol 2018 Oct 1;268:100-105. doi: 10.1016/j.ijcard.2018.02.050. PMID: 30041775
Determining bronchial morphology for the purposes of segregating so-called heterotaxy.
Loomba RS, Pelech AN, Shah PH, Anderson RH
Cardiol Young 2016 Apr;26(4):725-37. Epub 2015 Jul 10 doi: 10.1017/S1047951115001195. PMID: 26159655
Right heart and pulmonary vessels structure and function.
D'Alto M, Scognamiglio G, Dimopoulos K, Bossone E, Vizza D, Romeo E, Vonk-Noordergraaf A, Gaine S, Peacock A, Naeije R
Echocardiography 2015 Jan;32 Suppl 1:S3-10. Epub 2014 Sep 19 doi: 10.1111/echo.12227. PMID: 25244348
Echocardiographic characteristics of the criss-cross heart.
Yang YL, Wang XF, Cheng TO, Xie MX, Lü Q, He L, Lu XF, Wang J, Li L, Anderson RH
Int J Cardiol 2010 Apr 15;140(2):133-7. Epub 2009 Sep 16 doi: 10.1016/j.ijcard.2009.08.039. PMID: 19762095

Recent systematic reviews

Lead-I ECG for detecting atrial fibrillation in patients with an irregular pulse using single time point testing: a systematic review and economic evaluation.
Duarte R, Stainthorpe A, Greenhalgh J, Richardson M, Nevitt S, Mahon J, Kotas E, Boland A, Thom H, Marshall T, Hall M, Takwoingi Y
Health Technol Assess 2020 Jan;24(3):1-164. doi: 10.3310/hta24030. PMID: 31933471Free PMC Article

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