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Anomalous origin of right pulmonary artery from ascending aorta

MedGen UID:
576705
Concept ID:
C0345037
Congenital Abnormality
Synonyms: Hemitruncus to right; Origin of right pulmonary artery from ascending aorta; Right hemitruncus
SNOMED CT: Anomalous origin of right pulmonary artery from ascending aorta (253634009); Origin of right pulmonary artery from ascending aorta (253634009); Right hemitruncus (253634009); Hemitruncus to right (253634009)
 
HPO: HP:0005143

Definition

The right pulmonary artery originates from the ascending aorta in the presence of a pulmonary valve and main pulmonary artery. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAnomalous origin of right pulmonary artery from ascending aorta

Conditions with this feature

Right pulmonary artery, anomalous origin of, familial
MedGen UID:
322780
Concept ID:
C1835910
Disease or Syndrome

Professional guidelines

PubMed

Gupta A, VanLoozen D, Polimenakos AC, Murdison KA
Pediatr Cardiol 2018 Apr;39(4):848-851. Epub 2018 Mar 2 doi: 10.1007/s00246-018-1849-0. PMID: 29500505
Li X, Mu Z, Li X, Weng Z
Prenat Diagn 2018 Apr;38(5):310-317. Epub 2018 Mar 23 doi: 10.1002/pd.5235. PMID: 29451683
Manuel V, Sousa-Uva M, Morais H, Magalhães MP, Pedro A, Miguel G, Nunes MA, Gamboa S, Júnior AP
World J Pediatr Congenit Heart Surg 2015 Oct;6(4):521-5. doi: 10.1177/2150135115601832. PMID: 26467865

Recent clinical studies

Etiology

Arcieri L, Colaneri M, Bianco F, Merlino E, Santoro G, Silvano R, Baldinelli A, Pozzi M
J Card Surg 2022 Nov;37(11):3536-3542. Epub 2022 Aug 21 doi: 10.1111/jocs.16876. PMID: 35989538
Verma M, Pandey NN, Ramakrishnan S, Jagia P
J Card Surg 2022 Mar;37(3):483-491. Epub 2022 Jan 11 doi: 10.1111/jocs.16229. PMID: 35018673
Li X, Mu Z, Li X, Weng Z
Prenat Diagn 2018 Apr;38(5):310-317. Epub 2018 Mar 23 doi: 10.1002/pd.5235. PMID: 29451683
Guzeltas A, Ozturk E, Tanidir IC, Kasar T, Haydin S
Braz J Cardiovasc Surg 2017 Jan-Feb;32(1):29-37. doi: 10.21470/1678-9741-2016-0082. PMID: 28423127Free PMC Article
Prifti E, Bonacchi M, Murzi B, Crucean A, Leacche M, Bernabei M, Bartolozzi F, Nathan NS, Vanini V
J Card Surg 2004 Mar-Apr;19(2):103-12. doi: 10.1111/j.0886-0440.2004.04023.x. PMID: 15016045

Diagnosis

Arcieri L, Colaneri M, Bianco F, Merlino E, Santoro G, Silvano R, Baldinelli A, Pozzi M
J Card Surg 2022 Nov;37(11):3536-3542. Epub 2022 Aug 21 doi: 10.1111/jocs.16876. PMID: 35989538
Verma M, Pandey NN, Ramakrishnan S, Jagia P
J Card Surg 2022 Mar;37(3):483-491. Epub 2022 Jan 11 doi: 10.1111/jocs.16229. PMID: 35018673
Li X, Mu Z, Li X, Weng Z
Prenat Diagn 2018 Apr;38(5):310-317. Epub 2018 Mar 23 doi: 10.1002/pd.5235. PMID: 29451683
Prifti E, Bonacchi M, Murzi B, Crucean A, Leacche M, Bernabei M, Bartolozzi F, Nathan NS, Vanini V
J Card Surg 2004 Mar-Apr;19(2):103-12. doi: 10.1111/j.0886-0440.2004.04023.x. PMID: 15016045
O'Mara CS, Baker RR, Jeyasingham K
Surg Gynecol Obstet 1978 Oct;147(4):609-16. PMID: 360452

Therapy

Gupta A, VanLoozen D, Polimenakos AC, Murdison KA
Pediatr Cardiol 2018 Apr;39(4):848-851. Epub 2018 Mar 2 doi: 10.1007/s00246-018-1849-0. PMID: 29500505
Cho S, Kim WH, Choi ES, Lee JR, Kim YJ
Pediatr Cardiol 2015 Oct;36(7):1532-8. Epub 2015 May 27 doi: 10.1007/s00246-015-1197-2. PMID: 26008763
Martinez PD, Déry J, Vobecky S, Bigras JL, Lapierre C
Pediatr Radiol 2012 Dec;42(12):1514-6. Epub 2012 Jun 15 doi: 10.1007/s00247-012-2448-5. PMID: 22699374
Garg P, Talwar S, Kothari SS, Saxena A, Juneja R, Choudhary SK, Airan B
Interact Cardiovasc Thorac Surg 2012 Jul;15(1):86-92. Epub 2012 Mar 30 doi: 10.1093/icvts/ivs110. PMID: 22467006Free PMC Article
Kajihara N, Imoto Y, Sakamoto M, Ochiai Y, Kan-o M, Joo K, Watanabe M, Yuge T, Asou T, Takeda Y, Sese A
Ann Thorac Surg 2008 Apr;85(4):1407-11. doi: 10.1016/j.athoracsur.2007.11.081. PMID: 18355536

Prognosis

Cicek M, Onalan MA, Ilker Y, Ozkok S, Ozdemir F, Yurdakok O, Aydemir NA, Sasmazel A
Cardiol Young 2023 Sep;33(9):1700-1705. Epub 2023 Apr 13 doi: 10.1017/S1047951123000860. PMID: 37045608
Arcieri L, Colaneri M, Bianco F, Merlino E, Santoro G, Silvano R, Baldinelli A, Pozzi M
J Card Surg 2022 Nov;37(11):3536-3542. Epub 2022 Aug 21 doi: 10.1111/jocs.16876. PMID: 35989538
Beyaz MO, Coban S, Ulukan MO, Dogan MS, Erol C, Saritas T, Erdem A, Akdeniz C, Ugurlucan M, Akcevin A, Turkoglu H
Heart Surg Forum 2021 Jan 20;24(1):E065-E071. doi: 10.1532/hsf.3421. PMID: 33635248
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Prifti E, Bonacchi M, Murzi B, Crucean A, Leacche M, Bernabei M, Bartolozzi F, Nathan NS, Vanini V
J Card Surg 2004 Mar-Apr;19(2):103-12. doi: 10.1111/j.0886-0440.2004.04023.x. PMID: 15016045

Clinical prediction guides

Patel H, Malhotra P, Patel K, Patel M, Gajjar T, Mishra A, Sheth M
World J Pediatr Congenit Heart Surg 2024 May;15(3):365-370. Epub 2024 Jan 23 doi: 10.1177/21501351231221467. PMID: 38263672
Cicek M, Onalan MA, Ilker Y, Ozkok S, Ozdemir F, Yurdakok O, Aydemir NA, Sasmazel A
Cardiol Young 2023 Sep;33(9):1700-1705. Epub 2023 Apr 13 doi: 10.1017/S1047951123000860. PMID: 37045608
Arcieri L, Colaneri M, Bianco F, Merlino E, Santoro G, Silvano R, Baldinelli A, Pozzi M
J Card Surg 2022 Nov;37(11):3536-3542. Epub 2022 Aug 21 doi: 10.1111/jocs.16876. PMID: 35989538
Verma M, Pandey NN, Ramakrishnan S, Jagia P
J Card Surg 2022 Mar;37(3):483-491. Epub 2022 Jan 11 doi: 10.1111/jocs.16229. PMID: 35018673
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879

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