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Neuroectodermal neoplasm

MedGen UID:
60072
Concept ID:
C0206093
Neoplastic Process
Synonyms: Neuroectodermal Tumor; Neuroectodermal Tumors; Tumor, Neuroectodermal; Tumors, Neuroectodermal
SNOMED CT: Neuroectodermal tumor (73676002); Neuroectodermal tumor (253096008)
 
HPO: HP:0030061

Definition

A neoplasm arising in the neuroectoderm, the portion of the ectoderm of the early embryo that gives rise to the central and peripheral nervous systems, including some glial cells. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNeuroectodermal neoplasm

Recent clinical studies

Etiology

Capper D, Engel NW, Stichel D, Lechner M, Glöss S, Schmid S, Koelsche C, Schrimpf D, Niesen J, Wefers AK, Jones DTW, Sill M, Weigert O, Ligon KL, Olar A, Koch A, Forster M, Moran S, Tirado OM, Sáinz-Jaspeado M, Mora J, Esteller M, Alonso J, Del Muro XG, Paulus W, Felsberg J, Reifenberger G, Glatzel M, Frank S, Monoranu CM, Lund VJ, von Deimling A, Pfister S, Buslei R, Ribbat-Idel J, Perner S, Gudziol V, Meinhardt M, Schüller U
Acta Neuropathol 2018 Aug;136(2):255-271. Epub 2018 May 5 doi: 10.1007/s00401-018-1854-7. PMID: 29730775
Uccella S, Ottini G, Facco C, Maragliano R, Asioli S, Sessa F, La Rosa S
Pathologica 2017 Mar;109(1):14-30. PMID: 28635990
Longmuir SQ, Syed NA, Boldt HC
Ophthalmology 2010 Oct;117(10):2034-8. Epub 2010 Jul 21 doi: 10.1016/j.ophtha.2010.02.010. PMID: 20663567
Jennings MT, Slatkin N, D'Angelo M, Ketonen L, Johnson MD, Rosenblum M, Creasy J, Tulipan N, Walker R
J Child Neurol 1993 Oct;8(4):306-12. doi: 10.1177/088307389300800403. PMID: 8228025

Diagnosis

Hung B, Pennington Z, Sciubba DM
World Neurosurg 2021 Jul;151:2-4. Epub 2021 Apr 2 doi: 10.1016/j.wneu.2021.03.137. PMID: 33819706
Ito J, Nakano Y, Shima H, Miwa T, Kogure Y, Isshiki K, Yamazaki F, Oishi Y, Morimoto Y, Kataoka K, Okita H, Hirato J, Ichimura K, Shimada H
Brain Tumor Pathol 2020 Jul;37(3):105-110. Epub 2020 Jun 18 doi: 10.1007/s10014-020-00371-1. PMID: 32556925
Pacino GA, Salvatore C, Antonino M, Cristina DMM, Piero P, Giacomo S
Childs Nerv Syst 2020 Mar;36(3):485-489. Epub 2020 Jan 27 doi: 10.1007/s00381-020-04514-9. PMID: 31989207
Capper D, Engel NW, Stichel D, Lechner M, Glöss S, Schmid S, Koelsche C, Schrimpf D, Niesen J, Wefers AK, Jones DTW, Sill M, Weigert O, Ligon KL, Olar A, Koch A, Forster M, Moran S, Tirado OM, Sáinz-Jaspeado M, Mora J, Esteller M, Alonso J, Del Muro XG, Paulus W, Felsberg J, Reifenberger G, Glatzel M, Frank S, Monoranu CM, Lund VJ, von Deimling A, Pfister S, Buslei R, Ribbat-Idel J, Perner S, Gudziol V, Meinhardt M, Schüller U
Acta Neuropathol 2018 Aug;136(2):255-271. Epub 2018 May 5 doi: 10.1007/s00401-018-1854-7. PMID: 29730775
Uccella S, Ottini G, Facco C, Maragliano R, Asioli S, Sessa F, La Rosa S
Pathologica 2017 Mar;109(1):14-30. PMID: 28635990

Therapy

Longmuir SQ, Syed NA, Boldt HC
Ophthalmology 2010 Oct;117(10):2034-8. Epub 2010 Jul 21 doi: 10.1016/j.ophtha.2010.02.010. PMID: 20663567
Csatary LK, Gosztonyi G, Szeberenyi J, Fabian Z, Liszka V, Bodey B, Csatary CM
J Neurooncol 2004 Mar-Apr;67(1-2):83-93. doi: 10.1023/b:neon.0000021735.85511.05. PMID: 15072452

Prognosis

Pacino GA, Salvatore C, Antonino M, Cristina DMM, Piero P, Giacomo S
Childs Nerv Syst 2020 Mar;36(3):485-489. Epub 2020 Jan 27 doi: 10.1007/s00381-020-04514-9. PMID: 31989207
Smolle E, Al-Qubati S, Stefanits H, Haberler C, Kleinert R, Haybaeck J
Anticancer Res 2012 Nov;32(11):4939-44. PMID: 23155263
Csatary LK, Gosztonyi G, Szeberenyi J, Fabian Z, Liszka V, Bodey B, Csatary CM
J Neurooncol 2004 Mar-Apr;67(1-2):83-93. doi: 10.1023/b:neon.0000021735.85511.05. PMID: 15072452
Anselmo AP, Cartoni C, Pacchiarotti A, Pescarmona E, Cafolla A, Rendina E, Mandelli F
Ann Hematol 1994 Jun;68(6):311-3. doi: 10.1007/BF01695039. PMID: 8038238

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