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Bilateral deafness

MedGen UID:
777106
•Concept ID:
C3665473
•
Finding
Synonyms: Bilateral Deafness; Bilateral, Deafness; Bilaterals, Deafness; Deafness Bilateral; Deafness Bilaterals; Deafness, Bilateral
SNOMED CT: Bilateral deafness (162344009)

Definition

Partial or total inability to hear sounds in both ears. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBilateral deafness

Professional guidelines

PubMed

Fetal anemia in monochorionic twins: a review on diagnosis, management, and outcome.
Tollenaar LSA, Slaghekke F, Middeldorp JM, Lopriore E
Expert Rev Hematol 2023 Jan;16(1):9-16. Epub 2023 Jan 19 doi: 10.1080/17474086.2023.2166921. PMID: 36609186
American Cochlear Implant Alliance Task Force Guidelines for Clinical Assessment and Management of Cochlear Implantation in Children With Single-Sided Deafness.
Park LR, Griffin AM, Sladen DP, Neumann S, Young NM
Ear Hear 2022 Mar/Apr;43(2):255-267. doi: 10.1097/AUD.0000000000001204. PMID: 35213890Free PMC Article
Rapidly progressive bilateral postmeningitic deafness in children: Diagnosis and management.
De Barros A, Roy T, Amstutz Montadert I, Marie JP, Marcolla A, Obstoy MF, Choussy O, Dehesdin D, Lerosey Y
Eur Ann Otorhinolaryngol Head Neck Dis 2014 Apr;131(2):107-12. Epub 2014 Feb 18 doi: 10.1016/j.anorl.2013.04.006. PMID: 24559741

Recent clinical studies

Etiology

Data Logging Evidence of Cochlear Implant Use in Single-Sided and Bilateral Deafness.
Rauch AK, Kagermann S, Wesarg T, Jakob TF, Aschendorff A, Ihorst G, Speck I, Arndt S
Audiol Neurootol 2019;24(4):206-216. Epub 2019 Sep 11 doi: 10.1159/000502051. PMID: 31509836
Middle Fossa Approach for Cochlear Implantation.
Gawęcki W, Karlik M, Borucki Ł, Wróbel M, Stieler OM, Szyfter W
Otol Neurotol 2018 Feb;39(2):e96-e102. doi: 10.1097/MAO.0000000000001680. PMID: 29315183
Rapidly progressive bilateral postmeningitic deafness in children: Diagnosis and management.
De Barros A, Roy T, Amstutz Montadert I, Marie JP, Marcolla A, Obstoy MF, Choussy O, Dehesdin D, Lerosey Y
Eur Ann Otorhinolaryngol Head Neck Dis 2014 Apr;131(2):107-12. Epub 2014 Feb 18 doi: 10.1016/j.anorl.2013.04.006. PMID: 24559741
Bilateral cochlear implantation in children and the impact of the inter-implant interval.
Lammers MJ, Venekamp RP, Grolman W, van der Heijden GJ
Laryngoscope 2014 Apr;124(4):993-9. Epub 2013 Oct 10 doi: 10.1002/lary.24395. PMID: 24122619
What is the optimal timing for bilateral cochlear implantation in children?
Gordon KA, Jiwani S, Papsin BC
Cochlear Implants Int 2011 Aug;12 Suppl 2:S8-14. doi: 10.1179/146701011X13074645127199. PMID: 21917210

Diagnosis

Fetal anemia in monochorionic twins: a review on diagnosis, management, and outcome.
Tollenaar LSA, Slaghekke F, Middeldorp JM, Lopriore E
Expert Rev Hematol 2023 Jan;16(1):9-16. Epub 2023 Jan 19 doi: 10.1080/17474086.2023.2166921. PMID: 36609186
Deafness after COVID-19?
Gerstacker K, Speck I, Riemann S, Aschendorff A, Knopf A, Arndt S
HNO 2021 Aug;69(Suppl 2):92-95. Epub 2021 May 21 doi: 10.1007/s00106-021-01041-0. PMID: 34019138Free PMC Article
Hearing Impairment in Old Age.
Löhler J, Cebulla M, Shehata-Dieler W, Volkenstein S, Völter C, Walther LE
Dtsch Arztebl Int 2019 Apr 26;116(17):301-310. doi: 10.3238/arztebl.2019.0301. PMID: 31196393Free PMC Article
Rapidly progressive bilateral postmeningitic deafness in children: Diagnosis and management.
De Barros A, Roy T, Amstutz Montadert I, Marie JP, Marcolla A, Obstoy MF, Choussy O, Dehesdin D, Lerosey Y
Eur Ann Otorhinolaryngol Head Neck Dis 2014 Apr;131(2):107-12. Epub 2014 Feb 18 doi: 10.1016/j.anorl.2013.04.006. PMID: 24559741
Cogan syndrome.
Orsoni JG, Zavota L, Pellistri I, Piazza F, Cimino L
Cornea 2002 May;21(4):356-9. doi: 10.1097/00003226-200205000-00005. PMID: 11973382

Therapy

Chronic Myeloid Leukaemia with Sudden Bilateral Deafness and Leg Ulcer Associated with Hydroxyurea Therapy.
Ugwu NI, Okoye AE, Ugwu CN, Ibiam FA, Nnachi OA, Ugwu GC, Okoh NU
West Afr J Med 2021 May 29;38(5):502-506. PMID: 34051725
Perception and coding of interaural time differences with bilateral cochlear implants.
Laback B, Egger K, Majdak P
Hear Res 2015 Apr;322:138-50. Epub 2014 Oct 19 doi: 10.1016/j.heares.2014.10.004. PMID: 25456088
Bilateral cochlear implantation in children and the impact of the inter-implant interval.
Lammers MJ, Venekamp RP, Grolman W, van der Heijden GJ
Laryngoscope 2014 Apr;124(4):993-9. Epub 2013 Oct 10 doi: 10.1002/lary.24395. PMID: 24122619
What is the optimal timing for bilateral cochlear implantation in children?
Gordon KA, Jiwani S, Papsin BC
Cochlear Implants Int 2011 Aug;12 Suppl 2:S8-14. doi: 10.1179/146701011X13074645127199. PMID: 21917210
Cogan syndrome.
Orsoni JG, Zavota L, Pellistri I, Piazza F, Cimino L
Cornea 2002 May;21(4):356-9. doi: 10.1097/00003226-200205000-00005. PMID: 11973382

Prognosis

Neurodevelopmental outcome after antenatal therapy for fetal supraventricular tachyarrhythmia: 3-year follow-up of multicenter trial.
Miyoshi T, Maeno Y, Matsuda T, Ito Y, Inamura N, Kim KS, Shiraishi I, Kurosaki K, Ikeda T, Sago H; Collaborators; Japan Fetal Arrhythmia Group
Ultrasound Obstet Gynecol 2023 Jan;61(1):49-58. doi: 10.1002/uog.26113. PMID: 36350016
Acoustic Features of Cry of Deaf and Hard-of-Hearing Infants.
Zayed AM, Afsah O, Ismail EI, Baz H
J Deaf Stud Deaf Educ 2021 Sep 15;26(4):483-489. doi: 10.1093/deafed/enab016. PMID: 34121119
Chronic Myeloid Leukaemia with Sudden Bilateral Deafness and Leg Ulcer Associated with Hydroxyurea Therapy.
Ugwu NI, Okoye AE, Ugwu CN, Ibiam FA, Nnachi OA, Ugwu GC, Okoh NU
West Afr J Med 2021 May 29;38(5):502-506. PMID: 34051725
Long-term Implant Usage and Quality-of-Life in Sequential Bilateral Pediatric Cochlear Implantation.
Low D, Shipp D, Gordon K, Kuroiwa-Rivero M, Cushing S, Papsin B, Le T, Lin V, Chen J
Otol Neurotol 2020 Jan;41(1):39-44. doi: 10.1097/MAO.0000000000002439. PMID: 31498292
What is the optimal timing for bilateral cochlear implantation in children?
Gordon KA, Jiwani S, Papsin BC
Cochlear Implants Int 2011 Aug;12 Suppl 2:S8-14. doi: 10.1179/146701011X13074645127199. PMID: 21917210

Clinical prediction guides

Acoustic Features of Cry of Deaf and Hard-of-Hearing Infants.
Zayed AM, Afsah O, Ismail EI, Baz H
J Deaf Stud Deaf Educ 2021 Sep 15;26(4):483-489. doi: 10.1093/deafed/enab016. PMID: 34121119
Downward cross-modal plasticity in single-sided deafness.
Qiao Y, Li X, Shen H, Zhang X, Sun Y, Hao W, Guo B, Ni D, Gao Z, Guo H, Shang Y
Neuroimage 2019 Aug 15;197:608-617. Epub 2019 May 12 doi: 10.1016/j.neuroimage.2019.05.031. PMID: 31091475
Middle Fossa Approach for Cochlear Implantation.
Gawęcki W, Karlik M, Borucki Ł, Wróbel M, Stieler OM, Szyfter W
Otol Neurotol 2018 Feb;39(2):e96-e102. doi: 10.1097/MAO.0000000000001680. PMID: 29315183
Rapidly progressive bilateral postmeningitic deafness in children: Diagnosis and management.
De Barros A, Roy T, Amstutz Montadert I, Marie JP, Marcolla A, Obstoy MF, Choussy O, Dehesdin D, Lerosey Y
Eur Ann Otorhinolaryngol Head Neck Dis 2014 Apr;131(2):107-12. Epub 2014 Feb 18 doi: 10.1016/j.anorl.2013.04.006. PMID: 24559741
Bilateral cochlear implantation in children and the impact of the inter-implant interval.
Lammers MJ, Venekamp RP, Grolman W, van der Heijden GJ
Laryngoscope 2014 Apr;124(4):993-9. Epub 2013 Oct 10 doi: 10.1002/lary.24395. PMID: 24122619

Recent systematic reviews

Implantable Devices for Single-Sided Deafness and Conductive or Mixed Hearing Loss: A Health Technology Assessment.
Ontario Health (Quality)
Ont Health Technol Assess Ser 2020;20(1):1-165. Epub 2020 Mar 6 PMID: 32194878Free PMC Article
Endocrine disorders in Woodhouse-Sakati syndrome: a systematic review of the literature.
Agopiantz M, Corbonnois P, Sorlin A, Bonnet C, Klein M, Hubert N, Pascal-Vigneron V, Jonveaux P, Cuny T, Leheup B, Weryha G
J Endocrinol Invest 2014 Jan;37(1):1-7. Epub 2014 Jan 8 doi: 10.1007/s40618-013-0001-5. PMID: 24464444
Cochlear implantation versus auditory brainstem implantation in bilateral total deafness after head trauma: personal experience and review of the literature.
Medina M, Di Lella F, Di Trapani G, Prasad SC, Bacciu A, Aristegui M, Russo A, Sanna M
Otol Neurotol 2014 Feb;35(2):260-70. doi: 10.1097/MAO.0000000000000235. PMID: 24448286
Bilateral cochlear implantation in children and the impact of the inter-implant interval.
Lammers MJ, Venekamp RP, Grolman W, van der Heijden GJ
Laryngoscope 2014 Apr;124(4):993-9. Epub 2013 Oct 10 doi: 10.1002/lary.24395. PMID: 24122619
Effectiveness of multi-channel unilateral cochlear implants for profoundly deaf children: a systematic review.
Bond M, Elston J, Mealing S, Anderson R, Weiner G, Taylor RS, Liu Z, Stein K
Clin Otolaryngol 2009 Jun;34(3):199-211. doi: 10.1111/j.1749-4486.2009.01916.x. PMID: 19531168

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