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Intravenous leiomyomatosis

MedGen UID:
83417
Concept ID:
C0346200
Neoplastic Process
Synonyms: Intravascular Leiomyomatosis of the Uterus; Intravascular Leiomyomatosis of Uterus; Intravenous Leiomyomatosis; intravenous leiomyomatosis; Intravenous Leiomyomatosis of the Uterus; Intravenous Leiomyomatosis of Uterus; Uterine Corpus Intravenous Leiomyomatosis
SNOMED CT: Intravenous leiomyomatosis (254883003); Intravenous leiomyomatosis (1157175007)
 
Monarch Initiative: MONDO:0003614

Definition

A rare benign neoplasm characterized by the presence of smooth muscle cells growing within the veins of the uterine corpus. The intravascular neoplasm growth occurs outside the confines of an adjacent leiomyoma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVIntravenous leiomyomatosis
  • Intravenous leiomyomatosis
    • Intravenous leiomyomatosis
      • Intravenous leiomyomatosis
        • Intravenous leiomyomatosis
          • Intravenous leiomyomatosis
            • Intravenous leiomyomatosis
              • Intravenous leiomyomatosis

Professional guidelines

PubMed

Ma GT, Miao Q, Liu XR, Zhang CJ, Zheng YH, Shao J, Cheng NH, DU SD, Liu JZ, Jiang C
Zhongguo Yi Xue Ke Xue Yuan Xue Bao 2016 Aug;38(4):438-43. doi: 10.3881/j.issn.1000-503X.2016.04.013. PMID: 27594158
Li Y, Yang N, Lu L, Ma F, Yao J
Heart Surg Forum 2016 May 9;19(3):E094-6. doi: 10.1532/hsf.1362. PMID: 27355139
Wang J, Yang J, Huang H, Li Y, Miao Q, Lu X, Li Y, Yang N, Huang Y, Chen J, Cao D, Wu M, Pan L, Lang J, Shen K
Obstet Gynecol 2012 Dec;120(6):1400-6. doi: 10.1097/aog.0b013e31826ebb90. PMID: 23168766

Recent clinical studies

Etiology

Gao Y, Qu P
Int J Gynaecol Obstet 2023 Dec;163(3):825-833. Epub 2023 Jun 19 doi: 10.1002/ijgo.14932. PMID: 37334980
Yu X, Fu J, Cao T, Huang L, Qie M, Ouyang Y
Medicine (Baltimore) 2021 Jan 8;100(1):e24228. doi: 10.1097/MD.0000000000024228. PMID: 33429819Free PMC Article
Ordulu Z, Chai H, Peng G, McDonald AG, De Nictolis M, Garcia-Fernandez E, Hardisson D, Prat J, Li P, Hui P, Oliva E, Buza N
Mod Pathol 2020 Sep;33(9):1844-1860. Epub 2020 Apr 27 doi: 10.1038/s41379-020-0546-8. PMID: 32341498Free PMC Article
Low HY, Zhao Y, Huang KS, Shen HP, Wu PJ, Tseng CJ
Taiwan J Obstet Gynecol 2017 Jun;56(3):362-365. doi: 10.1016/j.tjog.2017.04.017. PMID: 28600049
Li R, Shen Y, Sun Y, Zhang C, Yang Y, Yang J, Su R, Jiang B
Tex Heart Inst J 2014 Oct;41(5):502-6. Epub 2014 Oct 1 doi: 10.14503/THIJ-13-3533. PMID: 25425982Free PMC Article

Diagnosis

Wang Q, Li Y, Gu X, Zhang N, Xie J, Niu B, Xing Y, He Y
Clin Radiol 2023 Sep;78(9):655-660. Epub 2023 Apr 17 doi: 10.1016/j.crad.2023.03.017. PMID: 37365113
Gao Y, Qu P
Int J Gynaecol Obstet 2023 Dec;163(3):825-833. Epub 2023 Jun 19 doi: 10.1002/ijgo.14932. PMID: 37334980
Yu X, Fu J, Cao T, Huang L, Qie M, Ouyang Y
Medicine (Baltimore) 2021 Jan 8;100(1):e24228. doi: 10.1097/MD.0000000000024228. PMID: 33429819Free PMC Article
Low HY, Zhao Y, Huang KS, Shen HP, Wu PJ, Tseng CJ
Taiwan J Obstet Gynecol 2017 Jun;56(3):362-365. doi: 10.1016/j.tjog.2017.04.017. PMID: 28600049
Li R, Shen Y, Sun Y, Zhang C, Yang Y, Yang J, Su R, Jiang B
Tex Heart Inst J 2014 Oct;41(5):502-6. Epub 2014 Oct 1 doi: 10.14503/THIJ-13-3533. PMID: 25425982Free PMC Article

Therapy

Xu X, Ma G, Miao Q, Liu X, Zhang C, Liu J, Shao J, Cheng N, Cao D
J Vasc Surg Venous Lymphat Disord 2022 Mar;10(2):409-416. Epub 2021 Jul 9 doi: 10.1016/j.jvsv.2021.06.016. PMID: 34252578
Liang J, Lei R, Xie M, Lin S, Xu J, Ling X, Xie Q
Orphanet J Rare Dis 2021 Oct 29;16(1):453. doi: 10.1186/s13023-021-02087-7. PMID: 34715881Free PMC Article
Mata RP, Urzal C, Belo AI, Guerreiro F
BMJ Case Rep 2020 Mar 18;13(3) doi: 10.1136/bcr-2020-234864. PMID: 32193185Free PMC Article
Low HY, Zhao Y, Huang KS, Shen HP, Wu PJ, Tseng CJ
Taiwan J Obstet Gynecol 2017 Jun;56(3):362-365. doi: 10.1016/j.tjog.2017.04.017. PMID: 28600049
Wang J, Yang J, Huang H, Li Y, Miao Q, Lu X, Li Y, Yang N, Huang Y, Chen J, Cao D, Wu M, Pan L, Lang J, Shen K
Obstet Gynecol 2012 Dec;120(6):1400-6. doi: 10.1097/aog.0b013e31826ebb90. PMID: 23168766

Prognosis

Fitzpatrick MB, Hammer PM, Yang EJ, Howitt BE
Hum Pathol 2022 Feb;120:18-25. Epub 2021 Nov 29 doi: 10.1016/j.humpath.2021.11.009. PMID: 34856302
Luo G, Pan H, Bi J, Luo Y, Zhu J, Feng Z, Fan H, Zhang Y, Dai X
J Int Med Res 2019 Jul;47(7):3465-3474. Epub 2019 Jul 7 doi: 10.1177/0300060519858021. PMID: 31280644Free PMC Article
Low HY, Zhao Y, Huang KS, Shen HP, Wu PJ, Tseng CJ
Taiwan J Obstet Gynecol 2017 Jun;56(3):362-365. doi: 10.1016/j.tjog.2017.04.017. PMID: 28600049
Wang J, Yang J, Huang H, Li Y, Miao Q, Lu X, Li Y, Yang N, Huang Y, Chen J, Cao D, Wu M, Pan L, Lang J, Shen K
Obstet Gynecol 2012 Dec;120(6):1400-6. doi: 10.1097/aog.0b013e31826ebb90. PMID: 23168766
Konrad P, Mellblom L
Acta Obstet Gynecol Scand 1989;68(4):371-6. doi: 10.3109/00016348909028675. PMID: 2618625

Clinical prediction guides

Chen L, Yang Y, Zhao C
BMC Womens Health 2023 Sep 11;23(1):483. doi: 10.1186/s12905-023-02618-3. PMID: 37697329Free PMC Article
Barnaś E, Skręt-Magierło JE, Paszek S, Kaznowska E, Potocka N, Skręt A, Sakowicz A, Zawlik I
Genes (Basel) 2023 Mar 14;14(3) doi: 10.3390/genes14030712. PMID: 36980984Free PMC Article
Ma H, Niu Y, Yang Z, Zheng M
J Ultrasound Med 2022 May;41(5):1101-1108. Epub 2021 Aug 11 doi: 10.1002/jum.15799. PMID: 34382236
Ordulu Z, Chai H, Peng G, McDonald AG, De Nictolis M, Garcia-Fernandez E, Hardisson D, Prat J, Li P, Hui P, Oliva E, Buza N
Mod Pathol 2020 Sep;33(9):1844-1860. Epub 2020 Apr 27 doi: 10.1038/s41379-020-0546-8. PMID: 32341498Free PMC Article
Liu N, Long Y, Liu Y
J Int Med Res 2020 Jan;48(1):300060519896887. doi: 10.1177/0300060519896887. PMID: 31937178Free PMC Article

Recent systematic reviews

Lim WH, Lamaro VP, Sivagnanam V
Surg Oncol 2022 Dec;45:101879. Epub 2022 Oct 17 doi: 10.1016/j.suronc.2022.101879. PMID: 36332557
Liang J, Lei R, Xie M, Lin S, Xu J, Ling X, Xie Q
Orphanet J Rare Dis 2021 Oct 29;16(1):453. doi: 10.1186/s13023-021-02087-7. PMID: 34715881Free PMC Article
Karpathiou G, Papoudou-Bai A, Clemenson A, Chauleur C, Peoc'h M
Am J Clin Pathol 2020 Jul 7;154(2):178-189. doi: 10.1093/ajcp/aqaa054. PMID: 32459343
Matsuo K, Fleischman F, Ghattas CS, Gabrielyan AS, Ballard CA, Roman LD, Morrow CP
Fertil Steril 2012 Nov;98(5):1341-5.e1. Epub 2012 Aug 15 doi: 10.1016/j.fertnstert.2012.07.1121. PMID: 22902061

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