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Orbit rhabdomyosarcoma

MedGen UID:
83419
Concept ID:
C0346347
Neoplastic Process
Synonym: Rhabdomyosarcoma of the orbit
SNOMED CT: Rhabdomyosarcoma of orbit (254994000)
 
Monarch Initiative: MONDO:0002580

Definition

A malignant mesenchymal neoplasm with skeletal muscle differentiation that arises from the orbit. [from NCI]

Term Hierarchy

Professional guidelines

PubMed

Kuan EC, Wang EW, Adappa ND, Beswick DM, London NR Jr, Su SY, Wang MB, Abuzeid WM, Alexiev B, Alt JA, Antognoni P, Alonso-Basanta M, Batra PS, Bhayani M, Bell D, Bernal-Sprekelsen M, Betz CS, Blay JY, Bleier BS, Bonilla-Velez J, Callejas C, Carrau RL, Casiano RR, Castelnuovo P, Chandra RK, Chatzinakis V, Chen SB, Chiu AG, Choby G, Chowdhury NI, Citardi MJ, Cohen MA, Dagan R, Dalfino G, Dallan I, Dassi CS, de Almeida J, Dei Tos AP, DelGaudio JM, Ebert CS, El-Sayed IH, Eloy JA, Evans JJ, Fang CH, Farrell NF, Ferrari M, Fischbein N, Folbe A, Fokkens WJ, Fox MG, Lund VJ, Gallia GL, Gardner PA, Geltzeiler M, Georgalas C, Getz AE, Govindaraj S, Gray ST, Grayson JW, Gross BA, Grube JG, Guo R, Ha PK, Halderman AA, Hanna EY, Harvey RJ, Hernandez SC, Holtzman AL, Hopkins C, Huang Z, Huang Z, Humphreys IM, Hwang PH, Iloreta AM, Ishii M, Ivan ME, Jafari A, Kennedy DW, Khan M, Kimple AJ, Kingdom TT, Knisely A, Kuo YJ, Lal D, Lamarre ED, Lan MY, Le H, Lechner M, Lee NY, Lee JK, Lee VH, Levine CG, Lin JC, Lin DT, Lobo BC, Locke T, Luong AU, Magliocca KR, Markovic SN, Matnjani G, McKean EL, Meço C, Mendenhall WM, Michel L, Na'ara S, Nicolai P, Nuss DW, Nyquist GG, Oakley GM, Omura K, Orlandi RR, Otori N, Papagiannopoulos P, Patel ZM, Pfister DG, Phan J, Psaltis AJ, Rabinowitz MR, Ramanathan M Jr, Rimmer R, Rosen MR, Sanusi O, Sargi ZB, Schafhausen P, Schlosser RJ, Sedaghat AR, Senior BA, Shrivastava R, Sindwani R, Smith TL, Smith KA, Snyderman CH, Solares CA, Sreenath SB, Stamm A, Stölzel K, Sumer B, Surda P, Tajudeen BA, Thompson LDR, Thorp BD, Tong CCL, Tsang RK, Turner JH, Turri-Zanoni M, Udager AM, van Zele T, VanKoevering K, Welch KC, Wise SK, Witterick IJ, Won TB, Wong SN, Woodworth BA, Wormald PJ, Yao WC, Yeh CF, Zhou B, Palmer JN
Int Forum Allergy Rhinol 2024 Feb;14(2):149-608. Epub 2024 Jan 2 doi: 10.1002/alr.23262. PMID: 37658764
Sobel RK, Ford JR, Dong W, Shriver E, Griepentrog GJ, Debnam JM, Esmaeli B
Am J Ophthalmol 2022 Feb;234:28-36. Epub 2021 Jul 17 doi: 10.1016/j.ajo.2021.06.035. PMID: 34280364
Shields JA, Shields CL
Surv Ophthalmol 2004 May-Jun;49(3):281-99. doi: 10.1016/j.survophthal.2004.02.001. PMID: 15110666

Recent clinical studies

Etiology

Chen SC, Bee YS, Lin MC, Sheu SJ
J Chin Med Assoc 2011 Mar;74(3):140-3. Epub 2011 Feb 19 doi: 10.1016/j.jcma.2011.01.031. PMID: 21421211

Diagnosis

Vaquera-Aparicio DN, Mascareñas-De Los Santos AH, Casillas-Vega N, Riojas-Hernández P, Llaca-Díaz J, Herrera-Benavente I, Castillo-Bejarano JI
Bol Med Hosp Infant Mex 2020;77(3):149-152. doi: 10.24875/BMHIM.19000205. PMID: 32496471
Chen SC, Bee YS, Lin MC, Sheu SJ
J Chin Med Assoc 2011 Mar;74(3):140-3. Epub 2011 Feb 19 doi: 10.1016/j.jcma.2011.01.031. PMID: 21421211

Therapy

Acquaviva A, Barberi L, Bernardini C, D'Ambrosio A, Lasorella G
J Neurosurg Sci 1982 Jan-Mar;26(1):45-8. PMID: 7143084

Prognosis

Chen SC, Bee YS, Lin MC, Sheu SJ
J Chin Med Assoc 2011 Mar;74(3):140-3. Epub 2011 Feb 19 doi: 10.1016/j.jcma.2011.01.031. PMID: 21421211
Acquaviva A, Barberi L, Bernardini C, D'Ambrosio A, Lasorella G
J Neurosurg Sci 1982 Jan-Mar;26(1):45-8. PMID: 7143084

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