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Abnormal auditory canal morphology

MedGen UID:
867433
•Concept ID:
C4021807
•
Anatomical Abnormality
Synonym: Abnormality of the auditory canal
 
HPO: HP:0000372

Definition

Any structural abnormality of the external acoustic tube (also known as the auditory canal). [from HPO]

Professional guidelines

PubMed

The role of MRI in the prenatal diagnosis and classification of fetal microtia.
Zhang X, Zheng W, Feng Y, Yu N, Qin J, Li K, Yan G, Zou Y, Li B
Eur Radiol 2023 Nov;33(11):7707-7715. Epub 2023 Jun 14 doi: 10.1007/s00330-023-09816-5. PMID: 37311804Free PMC Article
The diagnosis and treatment of a variant type of auricular sinus: postauricular sinus.
Pang J, Xiong H, Liao Q, Xu Y, Huang Q, Ou Y
Eur Arch Otorhinolaryngol 2019 Jul;276(7):1961-1967. Epub 2019 May 15 doi: 10.1007/s00405-019-05431-7. PMID: 31093733
Management of Cochlear Nerve Hypoplasia and Aplasia.
Freeman SR, Sennaroglu L
Adv Otorhinolaryngol 2018;81:81-92. Epub 2018 Apr 6 doi: 10.1159/000485542. PMID: 29794457

Recent clinical studies

Etiology

Internal auditory canal volume in normal and malformed inner ears.
Bächinger D, Breitsprecher TM, Pscheidl A, Dhanasingh A, Mlynski R, Dazert S, Langner S, Weiss NM
Eur Arch Otorhinolaryngol 2023 May;280(5):2149-2154. Epub 2022 Oct 9 doi: 10.1007/s00405-022-07676-1. PMID: 36210370Free PMC Article
Congenital Aural Stenosis With Cholesteatoma.
Casazza GC, Jonas RH, Kesser BW
Otol Neurotol 2022 Mar 1;43(3):320-327. doi: 10.1097/MAO.0000000000003440. PMID: 34889827
Management of Cochlear Nerve Hypoplasia and Aplasia.
Freeman SR, Sennaroglu L
Adv Otorhinolaryngol 2018;81:81-92. Epub 2018 Apr 6 doi: 10.1159/000485542. PMID: 29794457
The auditory characteristics of children with inner auditory canal stenosis.
Ai Y, Xu L, Li L, Li J, Luo J, Wang M, Fan Z, Wang H
Acta Otolaryngol 2016 Jul;136(7):687-91. Epub 2016 Mar 16 doi: 10.3109/00016489.2016.1152505. PMID: 26981851
Etiology and genes.
Matsunaga T
Adv Otorhinolaryngol 2014;75:2-8. Epub 2013 Oct 11 doi: 10.1159/000350491. PMID: 24135340

Diagnosis

Deep phenotyping of the neuroimaging and skeletal features in KBG syndrome: a study of 53 patients and review of the literature.
Peluso F, Caraffi SG, Contrò G, Valeri L, Napoli M, Carboni G, Seth A, Zuntini R, Coccia E, Astrea G, Bisgaard AM, Ivanovski I, Maitz S, Brischoux-Boucher E, Carter MT, Dentici ML, Devriendt K, Bellini M, Digilio MC, Doja A, Dyment DA, Farholt S, Ferreira CR, Wolfe LA, Gahl WA, Gnazzo M, Goel H, Grønborg SW, Hammer T, Iughetti L, Kleefstra T, Koolen DA, Lepri FR, Lemire G, Louro P, McCullagh G, Madeo SF, Milone A, Milone R, Nielsen JEK, Novelli A, Ockeloen CW, Pascarella R, Pippucci T, Ricca I, Robertson SP, Sawyer S, Falkenberg Smeland M, Stegmann S, Stumpel CT, Goel A, Taylor JM, Barbuti D, Soresina A, Bedeschi MF, Battini R, Cavalli A, Fusco C, Iascone M, Van Maldergem L, Venkateswaran S, Zuffardi O, Vergano S, Garavelli L, Bayat A
J Med Genet 2023 Nov 27;60(12):1224-1234. doi: 10.1136/jmg-2023-109141. PMID: 37586838Free PMC Article
Internal auditory canal volume in normal and malformed inner ears.
Bächinger D, Breitsprecher TM, Pscheidl A, Dhanasingh A, Mlynski R, Dazert S, Langner S, Weiss NM
Eur Arch Otorhinolaryngol 2023 May;280(5):2149-2154. Epub 2022 Oct 9 doi: 10.1007/s00405-022-07676-1. PMID: 36210370Free PMC Article
Cholesteatoma in Congenital Aural Atresia and External Auditory Canal Stenosis: A Systematic Review.
Chan CY, Karmali SA, Arulanandam B, Nguyen LHP, Duval M
Otolaryngol Head Neck Surg 2023 Sep;169(3):449-453. Epub 2022 Apr 18 doi: 10.1177/01945998221094230. PMID: 35439089
Audiometry.
Kaga K
Adv Otorhinolaryngol 2014;75:20-3. Epub 2013 Oct 11 doi: 10.1159/000350596. PMID: 24135344
Tympanometry.
Shanks JE
Ear Hear 1984 Sep-Oct;5(5):268-80. doi: 10.1097/00003446-198409000-00003. PMID: 6542036

Therapy

Vestibular hydrops in patients with semicircular canal malformation.
Niu Y, Chen W, Lin M, Sha Y
Auris Nasus Larynx 2023 Oct;50(5):727-732. Epub 2023 Feb 4 doi: 10.1016/j.anl.2023.01.009. PMID: 36740469
Isolated Internal Auditory Canal Diverticula: A Normal Anatomic Variant Not Associated with Sensorineural Hearing Loss.
Mihal DC, Feng Y, Kodet ML, Lohse CM, Carlson ML, Lane JI
AJNR Am J Neuroradiol 2018 Dec;39(12):2340-2344. Epub 2018 Nov 15 doi: 10.3174/ajnr.A5862. PMID: 30442698Free PMC Article
Blowout fractures - clinic, imaging and applied anatomy of the orbit.
Felding UNA
Dan Med J 2018 Mar;65(3) PMID: 29510812
Management of surgical difficulties during cochlear implant with inner ear anomalies.
Aldhafeeri AM, Alsanosi AA
Int J Pediatr Otorhinolaryngol 2017 Jan;92:45-49. Epub 2016 Nov 3 doi: 10.1016/j.ijporl.2016.11.001. PMID: 28012532
X-linked Malformation and Cochlear Implantation.
Smeds H, Wales J, Asp F, Löfkvist U, Falahat B, Anderlid BM, Anmyr L, Karltorp E
Otol Neurotol 2017 Jan;38(1):38-46. doi: 10.1097/MAO.0000000000001253. PMID: 27779564

Prognosis

Otopathologic Abnormalities in CHARGE Syndrome.
da Costa Monsanto R, Knoll RM, de Oliveira Penido N, Song G, Santos F, Paparella MM, Cureoglu S
Otolaryngol Head Neck Surg 2022 Feb;166(2):363-372. Epub 2021 Apr 20 doi: 10.1177/01945998211008911. PMID: 33874787
Sex-specific enlarged vestibular aqueduct morphology and audiometry.
Ruthberg J, Ascha MS, Kocharyan A, Gupta A, Murray GS, Megerian CA, Otteson TD
Am J Otolaryngol 2019 Jul-Aug;40(4):473-477. Epub 2019 Mar 29 doi: 10.1016/j.amjoto.2019.03.008. PMID: 31060752
Inner ear manifestations in CHARGE: Abnormalities, treatments, animal models, and progress toward treatments in auditory and vestibular structures.
Choo DI, Tawfik KO, Martin DM, Raphael Y
Am J Med Genet C Semin Med Genet 2017 Dec;175(4):439-449. Epub 2017 Oct 30 doi: 10.1002/ajmg.c.31587. PMID: 29082607Free PMC Article
Bony cochlear nerve canal and internal auditory canal measures predict cochlear nerve status.
Tahir E, Bajin MD, Atay G, Mocan BÖ, Sennaroğlu L
J Laryngol Otol 2017 Aug;131(8):676-683. Epub 2017 Jun 1 doi: 10.1017/S0022215117001141. PMID: 28566097
Acoustic neuroma. Assessment and management.
Ho SY, Kveton JF
Otolaryngol Clin North Am 2002 Apr;35(2):393-404, viii. doi: 10.1016/s0030-6665(02)00004-x. PMID: 12391625

Clinical prediction guides

Internal Auditory Canal Diverticula in Children: A Congenital Variant.
Muelleman TJ, Kavookjian H, Asmar J, Patel K, Nielsen D, Summers K, Tracy M, Noel-MacDonnell J, Staecker H, Ledbetter L, Weatherly R
Laryngoscope 2021 May;131(5):E1683-E1687. Epub 2020 Nov 17 doi: 10.1002/lary.29278. PMID: 33200834
Management of Cochlear Nerve Hypoplasia and Aplasia.
Freeman SR, Sennaroglu L
Adv Otorhinolaryngol 2018;81:81-92. Epub 2018 Apr 6 doi: 10.1159/000485542. PMID: 29794457
Blowout fractures - clinic, imaging and applied anatomy of the orbit.
Felding UNA
Dan Med J 2018 Mar;65(3) PMID: 29510812
Bony cochlear nerve canal and internal auditory canal measures predict cochlear nerve status.
Tahir E, Bajin MD, Atay G, Mocan BÖ, Sennaroğlu L
J Laryngol Otol 2017 Aug;131(8):676-683. Epub 2017 Jun 1 doi: 10.1017/S0022215117001141. PMID: 28566097
The auditory characteristics of children with inner auditory canal stenosis.
Ai Y, Xu L, Li L, Li J, Luo J, Wang M, Fan Z, Wang H
Acta Otolaryngol 2016 Jul;136(7):687-91. Epub 2016 Mar 16 doi: 10.3109/00016489.2016.1152505. PMID: 26981851

Recent systematic reviews

Cholesteatoma in Congenital Aural Atresia and External Auditory Canal Stenosis: A Systematic Review.
Chan CY, Karmali SA, Arulanandam B, Nguyen LHP, Duval M
Otolaryngol Head Neck Surg 2023 Sep;169(3):449-453. Epub 2022 Apr 18 doi: 10.1177/01945998221094230. PMID: 35439089
Spontaneous Congenital Perilabyrinthine Cerebrospinal Fluid Fistulas.
Lovin BD, Appelbaum EN, Makoshi L, Whitehead WE, Sweeney AD
Ann Otol Rhinol Laryngol 2021 Dec;130(12):1360-1368. Epub 2021 Apr 9 doi: 10.1177/00034894211007242. PMID: 33834882
Sudden hearing loss as an early detector of multiple sclerosis: a systematic review.
Di Stadio A, Dipietro L, Ralli M, Meneghello F, Minni A, Greco A, Stabile MR, Bernitsas E
Eur Rev Med Pharmacol Sci 2018 Jul;22(14):4611-4624. doi: 10.26355/eurrev_201807_15520. PMID: 30058696
Accessory Auricles: Systematic Review of Definition, Associated Conditions, and Recommendations for Clinical Practice.
Amirhassankhani S, Lloyd MS
J Craniofac Surg 2018 Mar;29(2):372-375. doi: 10.1097/SCS.0000000000004201. PMID: 29239919
Pediatric superior semicircular canal dehiscence: illustrative case and systematic review.
Lagman C, Ong V, Chung LK, Elhajjmoussa L, Fong C, Wang AC, Gopen Q, Yang I
J Neurosurg Pediatr 2017 Aug;20(2):196-203. Epub 2017 May 26 doi: 10.3171/2017.3.PEDS1734. PMID: 28548616

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