U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Congenital defect of the pericardium

MedGen UID:
868851
Concept ID:
C4023261
Congenital Abnormality
HPO: HP:0011628

Definition

A developmental defect of the pericardium with congenital onset. [from HPO]

Professional guidelines

PubMed

Kubala M, Tschabrunn C, Marchlinski DF, Marchlinski FE
Kardiol Pol 2020 May 25;78(5):386-395. Epub 2020 May 19 doi: 10.33963/KP.15374. PMID: 32431133
Xu B, Betancor J, Asher C, Rosario A, Klein A
Cardiology 2017;136(4):270-278. Epub 2016 Dec 7 doi: 10.1159/000452441. PMID: 27923231
Itkin M
Tech Vasc Interv Radiol 2016 Dec;19(4):299-304. Epub 2016 Oct 8 doi: 10.1053/j.tvir.2016.10.005. PMID: 27993326

Recent clinical studies

Etiology

Patukale AA, Suna J, Anand A, Betts KS, Karl TR, Venugopal P, Marathe SP, Alphonso N
World J Pediatr Congenit Heart Surg 2023 Mar;14(2):211-219. Epub 2023 Feb 23 doi: 10.1177/21501351221149416. PMID: 36823973
Stephens EH, Dearani JA, Jaroszewski DE
Ann Thorac Surg 2023 May;115(5):1312-1321. Epub 2023 Feb 11 doi: 10.1016/j.athoracsur.2023.01.040. PMID: 36781097
Marchetto C, Sgrò A, Gamba P, Trojan D, Pagliara C, Midrio P
Cell Tissue Bank 2022 Sep;23(3):607-614. Epub 2022 Apr 6 doi: 10.1007/s10561-022-10003-x. PMID: 35381893Free PMC Article
Parmar YJ, Shah AB, Poon M, Kronzon I
Cardiol Clin 2017 Nov;35(4):601-614. doi: 10.1016/j.ccl.2017.07.012. PMID: 29025550
Di Lorenzo M, Collin PP, Vaillancourt R, Duranceau A
J Pediatr Surg 1989 Oct;24(10):988-91. doi: 10.1016/s0022-3468(89)80199-x. PMID: 2809973

Diagnosis

Sheridan JA, Noga M, Mackie AS
Can J Cardiol 2023 Aug;39(8):1140-1143. Epub 2023 Mar 15 doi: 10.1016/j.cjca.2023.03.012. PMID: 36931623
Williams AP, Marayati R, Beierle EA
Semin Pediatr Surg 2019 Apr;28(2):106-110. Epub 2019 Apr 9 doi: 10.1053/j.sempedsurg.2019.04.006. PMID: 31072457Free PMC Article
Kligerman S
Radiol Clin North Am 2019 Jan;57(1):179-199. doi: 10.1016/j.rcl.2018.09.001. PMID: 30454812
Parmar YJ, Shah AB, Poon M, Kronzon I
Cardiol Clin 2017 Nov;35(4):601-614. doi: 10.1016/j.ccl.2017.07.012. PMID: 29025550
Lopez D, Asher CR
Prog Cardiovasc Dis 2017 Jan-Feb;59(4):398-406. Epub 2016 Dec 9 doi: 10.1016/j.pcad.2016.12.002. PMID: 27956198

Therapy

Stephens EH, Dearani JA, Jaroszewski DE
Ann Thorac Surg 2023 May;115(5):1312-1321. Epub 2023 Feb 11 doi: 10.1016/j.athoracsur.2023.01.040. PMID: 36781097
Jbarah OF, Aburayya BI, Shatnawi AR, Alkhasoneh MA, Toubasi AA, Alharahsheh SM, Nukho SK, Nassar AS, Jamous MA
Neurosurg Rev 2022 Dec;45(6):3537-3550. Epub 2022 Oct 1 doi: 10.1007/s10143-022-01873-6. PMID: 36180807
Wiggins LM, Mimic B, Issitt R, Ilic S, Bonello B, Marek J, Kostolny M
J Thorac Cardiovasc Surg 2020 Jun;159(6):2369-2378. Epub 2019 Oct 26 doi: 10.1016/j.jtcvs.2019.09.176. PMID: 31864692
Bogush N, Espinosa RE, Cannon BC, Wackel PL, Okamura H, Friedman PA, McLeod CJ
Int J Cardiol 2018 Jan 1;250:133-138. Epub 2017 Oct 13 doi: 10.1016/j.ijcard.2017.09.213. PMID: 29169751
Itkin M
Tech Vasc Interv Radiol 2016 Dec;19(4):299-304. Epub 2016 Oct 8 doi: 10.1053/j.tvir.2016.10.005. PMID: 27993326

Prognosis

Khayata M, Haouzi AA, Asher CR, Xu B
Curr Cardiol Rep 2023 Dec;25(12):1715-1724. Epub 2023 Dec 7 doi: 10.1007/s11886-023-02004-3. PMID: 38060098
Chetrit M, Xu B, Verma BR, Klein AL
Curr Cardiol Rep 2019 Apr 16;21(5):41. doi: 10.1007/s11886-019-1115-y. PMID: 30993456
Friedberg MK
JACC Cardiovasc Imaging 2018 May;11(5):755-771. doi: 10.1016/j.jcmg.2018.01.028. PMID: 29747850
Puvabanditsin S, Di Stefano V, Garrow E, Wong R, Eng J, Balbin J
Hong Kong Med J 2013 Oct;19(5):447-50. doi: 10.12809/hkmj133737. PMID: 24088589
Di Lorenzo M, Collin PP, Vaillancourt R, Duranceau A
J Pediatr Surg 1989 Oct;24(10):988-91. doi: 10.1016/s0022-3468(89)80199-x. PMID: 2809973

Clinical prediction guides

Piron S, Tridetti J, Marchetta S, Lancellotti P
Acta Cardiol 2023 Jun;78(4):459-462. Epub 2021 Oct 21 doi: 10.1080/00015385.2021.1991666. PMID: 34670482
Vatzia K, Fanariotis M, Makridis KG, Vlychou M, Fezoulidis IV, Vassiou K
Eur J Radiol 2021 Sep;142:109828. Epub 2021 Jun 24 doi: 10.1016/j.ejrad.2021.109828. PMID: 34280594
Fadl SA, Nasrullah A, Harris A, Edwards R, Kicska G
Int J Cardiovasc Imaging 2020 May;36(5):947-969. Epub 2020 Feb 11 doi: 10.1007/s10554-020-01784-x. PMID: 32048125
Wittig JG, Münsterberg A
Cold Spring Harb Perspect Biol 2020 Aug 3;12(8) doi: 10.1101/cshperspect.a037218. PMID: 31767650Free PMC Article
Friedberg MK
JACC Cardiovasc Imaging 2018 May;11(5):755-771. doi: 10.1016/j.jcmg.2018.01.028. PMID: 29747850

Recent systematic reviews

Patukale AA, Suna J, Anand A, Betts KS, Karl TR, Venugopal P, Marathe SP, Alphonso N
World J Pediatr Congenit Heart Surg 2023 Mar;14(2):211-219. Epub 2023 Feb 23 doi: 10.1177/21501351221149416. PMID: 36823973
Jbarah OF, Aburayya BI, Shatnawi AR, Alkhasoneh MA, Toubasi AA, Alharahsheh SM, Nukho SK, Nassar AS, Jamous MA
Neurosurg Rev 2022 Dec;45(6):3537-3550. Epub 2022 Oct 1 doi: 10.1007/s10143-022-01873-6. PMID: 36180807
Collins RT 2nd, O'Connor MJ
Pediatr Cardiol 2021 Apr;42(4):875-882. Epub 2021 Apr 15 doi: 10.1007/s00246-021-02555-8. PMID: 33856497
Romero J, Patel K, Briceno D, Alviz I, Gabr M, Diaz JC, Trivedi C, Mohanty S, Della Rocca D, Al-Ahmad A, Yang R, Rios S, Cerna L, Du X, Tarantino N, Zhang XD, Lakkireddy D, Natale A, Di Biase L
J Cardiovasc Electrophysiol 2020 Aug;31(8):2022-2031. Epub 2020 Jun 18 doi: 10.1111/jce.14593. PMID: 32478430
Centola M, Longo M, De Marco F, Cremonesi G, Marconi M, Danzi GB
J Cardiovasc Med (Hagerstown) 2009 Sep;10(9):687-92. doi: 10.2459/JCM.0b013e32832b3d4a. PMID: 19448561

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...