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Medulloepithelioma

MedGen UID:
87272
Concept ID:
C0334596
Neoplastic Process
Synonym: Medulloepitheliomas
SNOMED CT: Diktyoma, malignant (39005004); Medulloepithelioma (715903004); Medulloepithelioma (39005004); Diktyoma (39005004)
 
HPO: HP:0030071
Monarch Initiative: MONDO:0003144
Orphanet: ORPHA251883

Definition

A primitive neuroectodermal tumor that originates from the cells of the embryonic medullary canal. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • Medulloepithelioma
Follow this link to review classifications for Medulloepithelioma in Orphanet.

Recent clinical studies

Etiology

Tadepalli SH, Shields CL, Shields JA, Honavar SG
Indian J Ophthalmol 2019 Jun;67(6):755-762. doi: 10.4103/ijo.IJO_845_19. PMID: 31124483Free PMC Article
Ang SM, Dalvin LA, Emrich J, Komarnicky L, Shields JA, Shields CL
Asia Pac J Ophthalmol (Phila) 2019 Jan-Feb;8(1):30-35. Epub 2018 Oct 30 doi: 10.22608/APO.2018257. PMID: 30375203
Galluzzi P, Casseri T, Cerase A, Guglielmucci D, Toti P, Hadjistilianou T
Neuroradiology 2018 Nov;60(11):1213-1222. Epub 2018 Sep 19 doi: 10.1007/s00234-018-2094-1. PMID: 30232518
Kaliki S, Shields CL, Eagle RC Jr, Vemuganti GK, Almeida A, Manjandavida FP, Mulay K, Honavar SG, Shields JA
Ophthalmology 2013 Dec;120(12):2552-2559. Epub 2013 Jun 21 doi: 10.1016/j.ophtha.2013.05.015. PMID: 23796765
Lindegaard J, Heegaard S, Toft PB, Nysom K, Prause JU
Orbit 2010 Jun;29(3):161-4. doi: 10.3109/01676830903421200. PMID: 20497085

Diagnosis

Sarangi J, Kakkar A, Roy D, Thakur R, Singh CA, Sharma MC
Eur J Ophthalmol 2021 Mar;31(2):NP126-NP130. Epub 2019 Aug 14 doi: 10.1177/1120672119870079. PMID: 31411051
Stathopoulos C, Gaillard MC, Schneider J, Munier FL
BMC Ophthalmol 2020 Jun 18;20(1):239. doi: 10.1186/s12886-020-01512-y. PMID: 32552699Free PMC Article
Ang SM, Dalvin LA, Emrich J, Komarnicky L, Shields JA, Shields CL
Asia Pac J Ophthalmol (Phila) 2019 Jan-Feb;8(1):30-35. Epub 2018 Oct 30 doi: 10.22608/APO.2018257. PMID: 30375203
Galluzzi P, Casseri T, Cerase A, Guglielmucci D, Toti P, Hadjistilianou T
Neuroradiology 2018 Nov;60(11):1213-1222. Epub 2018 Sep 19 doi: 10.1007/s00234-018-2094-1. PMID: 30232518
Kusakabe K, Kohno S, Inoue A, Seno T, Yonezawa S, Moritani K, Mizuno Y, Kurata M, Kitazawa R, Tauchi H, Watanabe H, Iwata S, Hirato J, Kunieda T
Neuropathology 2018 Apr;38(2):179-184. Epub 2017 Oct 3 doi: 10.1111/neup.12431. PMID: 28971535

Therapy

Stathopoulos C, Gaillard MC, Schneider J, Munier FL
BMC Ophthalmol 2020 Jun 18;20(1):239. doi: 10.1186/s12886-020-01512-y. PMID: 32552699Free PMC Article
Thottian AG, Benson R, Kashyap S, Haresh KP, Gupta S, Sharma D, Rath GK
Orbit 2016 Dec;35(6):313-316. Epub 2016 Aug 12 doi: 10.1080/01676830.2016.1193536. PMID: 27715363
Hayase T, Morimoto A, Kawahara Y, Yagi M, Kanai N, Nobusawa S, Hirato J, Gomi A
J Pediatr Hematol Oncol 2015 Aug;37(6):e394-8. doi: 10.1097/MPH.0000000000000381. PMID: 26181425
Poon DS, Reich E, Smith VM, Kingston J, Reddy MA, Hungerford JL, Sagoo MS
Ophthalmology 2015 Sep;122(9):1949-51. Epub 2015 Apr 8 doi: 10.1016/j.ophtha.2015.03.002. PMID: 25863421
Müller K, Zwiener I, Welker H, Maass E, Bongartz R, Berthold F, Pietsch T, Warmuth-Metz M, von Bueren A, Rutkowski S
Strahlenther Onkol 2011 Nov;187(11):757-62. Epub 2011 Oct 28 doi: 10.1007/s00066-011-2256-0. PMID: 22037651

Prognosis

Chaudhary S, Regmi V, Shah S, Adhikari P
JNMA J Nepal Med Assoc 2021 Jan 31;59(233):77-80. doi: 10.31729/jnma.5269. PMID: 34508461Free PMC Article
Tadepalli SH, Shields CL, Shields JA, Honavar SG
Indian J Ophthalmol 2019 Jun;67(6):755-762. doi: 10.4103/ijo.IJO_845_19. PMID: 31124483Free PMC Article
Thottian AG, Benson R, Kashyap S, Haresh KP, Gupta S, Sharma D, Rath GK
Orbit 2016 Dec;35(6):313-316. Epub 2016 Aug 12 doi: 10.1080/01676830.2016.1193536. PMID: 27715363
Ozolek JA, Cohen DE, Kool M, Pfister SM, Korshunov A, Bukowinski AJ, Davis AW
CNS Oncol 2015;4(4):203-12. Epub 2015 Jun 29 doi: 10.2217/cns.15.9. PMID: 26118758Free PMC Article
Lindegaard J, Heegaard S, Toft PB, Nysom K, Prause JU
Orbit 2010 Jun;29(3):161-4. doi: 10.3109/01676830903421200. PMID: 20497085

Clinical prediction guides

Jakobiec FA, Borkar DS, Stagner AM, Lee NG
JAMA Ophthalmol 2016 Aug 1;134(8):919-23. doi: 10.1001/jamaophthalmol.2016.1515. PMID: 27254319
Tauziède-Espariat A, Roche O, Dufier JL, Putterman M
Eur J Ophthalmol 2016 Nov 4;26(6):e145-e148. doi: 10.5301/ejo.5000798. PMID: 27173894
Priest JR, Williams GM, Manera R, Jenkinson H, Bründler MA, Davis S, Murray TG, Galliani CA, Dehner LP
Br J Ophthalmol 2011 Jul;95(7):1001-5. Epub 2010 Dec 13 doi: 10.1136/bjo.2010.189779. PMID: 21156700
Lindegaard J, Heegaard S, Toft PB, Nysom K, Prause JU
Orbit 2010 Jun;29(3):161-4. doi: 10.3109/01676830903421200. PMID: 20497085
Zhou M, Xu G, Bojanowski CM, Song Y, Chen R, Sun X, Wang W, Chan CC
Acta Ophthalmol Scand 2006 Feb;84(1):137-9. doi: 10.1111/j.1600-0420.2005.00542.x. PMID: 16445454Free PMC Article

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