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Cystic Fibrosis Pulmonary Exacerbation

MedGen UID:
888330
Concept ID:
C1135342
Disease or Syndrome

Definition

An acute episode of worsening pulmonary symptoms related to cystic fibrosis. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCystic Fibrosis Pulmonary Exacerbation

Professional guidelines

PubMed

Gavioli EM, Guardado N, Haniff F, Deiab N, Vider E
Microb Drug Resist 2021 Dec;27(12):1726-1732. Epub 2021 Jun 1 doi: 10.1089/mdr.2020.0602. PMID: 34077286
Cogen JD, Faino AV, Onchiri F, Gibson RL, Hoffman LR, Kronman MP, Rosenfeld M, Nichols DP
Ann Am Thorac Soc 2021 Feb;18(2):266-272. doi: 10.1513/AnnalsATS.202002-176OC. PMID: 32810412Free PMC Article
Parkins MD, Elborn JS
J Antimicrob Chemother 2010 Sep;65(9):1853-61. Epub 2010 Jul 6 doi: 10.1093/jac/dkq245. PMID: 20605846

Recent clinical studies

Etiology

List R, Solomon G, Bichl S, Horton BJ, Shen S, Corcoran B, Sadeghi H, Britto MT, Ren C, Albon D; CFLN Collaboration Group FIES/SIES Innovation Lab
BMJ Open Qual 2023 Dec 28;12(4) doi: 10.1136/bmjoq-2023-002466. PMID: 38154821Free PMC Article
Wojsyk-Banaszak I, Więckowska B, Stachowiak Z, Kycler M, Szczepankiewicz A
Pediatr Pulmonol 2022 Jun;57(6):1466-1474. Epub 2022 Apr 8 doi: 10.1002/ppul.25891. PMID: 35293155
Cogen JD, Faino AV, Onchiri F, Gibson RL, Hoffman LR, Kronman MP, Rosenfeld M, Nichols DP
Ann Am Thorac Soc 2021 Feb;18(2):266-272. doi: 10.1513/AnnalsATS.202002-176OC. PMID: 32810412Free PMC Article
Laguna TA, Reilly CS, Williams CB, Welchlin C, Wendt CH
Pediatr Pulmonol 2015 Sep;50(9):869-77. Epub 2015 Jun 26 doi: 10.1002/ppul.23225. PMID: 26115542Free PMC Article
Antos NJ, Quintero DR, Walsh-Kelly CM, Noe JE, Schechter MS
BMJ Qual Saf 2014 Apr;23 Suppl 1:i33-i41. doi: 10.1136/bmjqs-2013-002367. PMID: 24608549

Diagnosis

Wojsyk-Banaszak I, Więckowska B, Stachowiak Z, Kycler M, Szczepankiewicz A
Pediatr Pulmonol 2022 Jun;57(6):1466-1474. Epub 2022 Apr 8 doi: 10.1002/ppul.25891. PMID: 35293155
Hassanzad M, Kiani A, Abedini A, Ghaffaripour H, Emami H, Alizadeh N, Zoghi G, Hashemi S, Velayati AA
BMC Pulm Med 2021 Nov 8;21(1):353. doi: 10.1186/s12890-021-01728-8. PMID: 34743707Free PMC Article
Goss CH, Heltshe SL, West NE, Skalland M, Sanders DB, Jain R, Barto TL, Fogarty B, Marshall BC, VanDevanter DR, Flume PA; STOP2 Investigators
Am J Respir Crit Care Med 2021 Dec 1;204(11):1295-1305. doi: 10.1164/rccm.202102-0461OC. PMID: 34469706Free PMC Article
Scott LK, Toner R
Lung 2017 Aug;195(4):397-401. Epub 2017 Jun 16 doi: 10.1007/s00408-017-0024-3. PMID: 28623538
Rogers GB, Hoffman LR, Johnson MW, Mayer-Hamblett N, Schwarze J, Carroll MP, Bruce KD
Expert Rev Mol Diagn 2011 Mar;11(2):197-206. doi: 10.1586/erm.10.117. PMID: 21405970Free PMC Article

Therapy

Goss CH, Heltshe SL, West NE, Skalland M, Sanders DB, Jain R, Barto TL, Fogarty B, Marshall BC, VanDevanter DR, Flume PA; STOP2 Investigators
Am J Respir Crit Care Med 2021 Dec 1;204(11):1295-1305. doi: 10.1164/rccm.202102-0461OC. PMID: 34469706Free PMC Article
Gavioli EM, Guardado N, Haniff F, Deiab N, Vider E
Microb Drug Resist 2021 Dec;27(12):1726-1732. Epub 2021 Jun 1 doi: 10.1089/mdr.2020.0602. PMID: 34077286
Scott LK, Toner R
Lung 2017 Aug;195(4):397-401. Epub 2017 Jun 16 doi: 10.1007/s00408-017-0024-3. PMID: 28623538
Gifford AH, Moulton LA, Dorman DB, Olbina G, Westerman M, Parker HW, Stanton BA, O'Toole GA
Clin Transl Sci 2012 Aug;5(4):368-73. Epub 2012 Jun 1 doi: 10.1111/j.1752-8062.2012.00417.x. PMID: 22883617Free PMC Article
Parkins MD, Elborn JS
J Antimicrob Chemother 2010 Sep;65(9):1853-61. Epub 2010 Jul 6 doi: 10.1093/jac/dkq245. PMID: 20605846

Prognosis

Hassanzad M, Kiani A, Abedini A, Ghaffaripour H, Emami H, Alizadeh N, Zoghi G, Hashemi S, Velayati AA
BMC Pulm Med 2021 Nov 8;21(1):353. doi: 10.1186/s12890-021-01728-8. PMID: 34743707Free PMC Article
Goss CH, Heltshe SL, West NE, Skalland M, Sanders DB, Jain R, Barto TL, Fogarty B, Marshall BC, VanDevanter DR, Flume PA; STOP2 Investigators
Am J Respir Crit Care Med 2021 Dec 1;204(11):1295-1305. doi: 10.1164/rccm.202102-0461OC. PMID: 34469706Free PMC Article
Scott LK, Toner R
Lung 2017 Aug;195(4):397-401. Epub 2017 Jun 16 doi: 10.1007/s00408-017-0024-3. PMID: 28623538
Rogers GB, Hoffman LR, Johnson MW, Mayer-Hamblett N, Schwarze J, Carroll MP, Bruce KD
Expert Rev Mol Diagn 2011 Mar;11(2):197-206. doi: 10.1586/erm.10.117. PMID: 21405970Free PMC Article
Parkins MD, Elborn JS
J Antimicrob Chemother 2010 Sep;65(9):1853-61. Epub 2010 Jul 6 doi: 10.1093/jac/dkq245. PMID: 20605846

Clinical prediction guides

Hassanzad M, Kiani A, Abedini A, Ghaffaripour H, Emami H, Alizadeh N, Zoghi G, Hashemi S, Velayati AA
BMC Pulm Med 2021 Nov 8;21(1):353. doi: 10.1186/s12890-021-01728-8. PMID: 34743707Free PMC Article
Goss CH, Heltshe SL, West NE, Skalland M, Sanders DB, Jain R, Barto TL, Fogarty B, Marshall BC, VanDevanter DR, Flume PA; STOP2 Investigators
Am J Respir Crit Care Med 2021 Dec 1;204(11):1295-1305. doi: 10.1164/rccm.202102-0461OC. PMID: 34469706Free PMC Article
Scott LK, Toner R
Lung 2017 Aug;195(4):397-401. Epub 2017 Jun 16 doi: 10.1007/s00408-017-0024-3. PMID: 28623538
Rogers GB, Hoffman LR, Johnson MW, Mayer-Hamblett N, Schwarze J, Carroll MP, Bruce KD
Expert Rev Mol Diagn 2011 Mar;11(2):197-206. doi: 10.1586/erm.10.117. PMID: 21405970Free PMC Article
Parkins MD, Elborn JS
J Antimicrob Chemother 2010 Sep;65(9):1853-61. Epub 2010 Jul 6 doi: 10.1093/jac/dkq245. PMID: 20605846

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