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Childhood Central Nervous System Ganglioneuroblastoma

MedGen UID:
903020
Concept ID:
C4086154
Neoplastic Process
Synonym: Childhood Cerebral Ganglioneuroblastoma

Definition

A central nervous system ganglioneuroblastoma that occurs during childhood. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChildhood Central Nervous System Ganglioneuroblastoma

Recent clinical studies

Etiology

Kamenova M, Kaneva R, Genova K, Gabrovsky N
Adv Exp Med Biol 2023;1405:225-252. doi: 10.1007/978-3-031-23705-8_8. PMID: 37452940
Okonta VN, Majlessipour F, Baca NM
J Pediatr Hematol Oncol 2023 Jan 1;45(1):e131-e134. Epub 2022 Apr 6 doi: 10.1097/MPH.0000000000002461. PMID: 35398860
Blanc T, Meignan P, Vinit N, Ballouhey Q, Pio L, Capito C, Harte C, Vatta F, Galmiche-Rolland L, Minard V, Orbach D, Berteloot L, Muller C, Kohaut J, Broch A, Braik K, Binet A, Heloury Y, Fourcade L, Lardy H, Sarnacki S
Ann Surg Oncol 2022 Feb;29(2):1315-1326. Epub 2021 Sep 14 doi: 10.1245/s10434-021-10777-6. PMID: 34523002
Tulla M, Berthold F, Graf N, Rutkowski S, von Schweinitz D, Spix C, Kaatsch P
Pediatrics 2015 Sep;136(3):e623-32. doi: 10.1542/peds.2015-0224. PMID: 26304823

Diagnosis

Sarnat HB, Chan ES, Ng D, Yu W
J Neuropathol Exp Neurol 2023 Sep 20;82(10):853-864. doi: 10.1093/jnen/nlad068. PMID: 37682248
Kamenova M, Kaneva R, Genova K, Gabrovsky N
Adv Exp Med Biol 2023;1405:225-252. doi: 10.1007/978-3-031-23705-8_8. PMID: 37452940
Tulla M, Berthold F, Graf N, Rutkowski S, von Schweinitz D, Spix C, Kaatsch P
Pediatrics 2015 Sep;136(3):e623-32. doi: 10.1542/peds.2015-0224. PMID: 26304823
Dama E, Pastore G, Mosso ML, Maule MM, Zuccolo L, Magnani C, Merletti F
Eur J Pediatr 2006 Apr;165(4):240-9. Epub 2006 Jan 13 doi: 10.1007/s00431-005-0034-7. PMID: 16411094
Taşdemiroğlu E, Patchell RA, Kryscio R
Acta Neurochir (Wien) 1999;141(12):1313-21. doi: 10.1007/s007010050436. PMID: 10672303

Therapy

Packer RJ, Sutton LN, Rosenstock JG, Rorke LB, Bilaniuk LT, Zimmerman RA, Littman PA, Bruce DA, Schut L
Pediatrics 1984 Jul;74(1):97-102. PMID: 6739222

Prognosis

Kamenova M, Kaneva R, Genova K, Gabrovsky N
Adv Exp Med Biol 2023;1405:225-252. doi: 10.1007/978-3-031-23705-8_8. PMID: 37452940
Tulla M, Berthold F, Graf N, Rutkowski S, von Schweinitz D, Spix C, Kaatsch P
Pediatrics 2015 Sep;136(3):e623-32. doi: 10.1542/peds.2015-0224. PMID: 26304823
Dama E, Pastore G, Mosso ML, Maule MM, Zuccolo L, Magnani C, Merletti F
Eur J Pediatr 2006 Apr;165(4):240-9. Epub 2006 Jan 13 doi: 10.1007/s00431-005-0034-7. PMID: 16411094
Taşdemiroğlu E, Patchell RA, Kryscio R
Acta Neurochir (Wien) 1999;141(12):1313-21. doi: 10.1007/s007010050436. PMID: 10672303

Clinical prediction guides

Okonta VN, Majlessipour F, Baca NM
J Pediatr Hematol Oncol 2023 Jan 1;45(1):e131-e134. Epub 2022 Apr 6 doi: 10.1097/MPH.0000000000002461. PMID: 35398860

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