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Vestibulocochlear nerve neoplasm

MedGen UID:
91099
•Concept ID:
C0346330
•
Neoplastic Process
Synonyms: Acoustic Nerve Neoplasm; acoustic nerve neoplasm; Acoustic Nerve Tumor; acoustic nerve tumor; acoustic nerve tumour; Cranial Nerve Eight Neoplasms; cranial nerve eight neoplasms; Eighth Cranial Nerve Neoplasm; eighth cranial nerve neoplasm; Eighth Cranial Nerve Neoplasms; eighth cranial nerve neoplasms; Eighth Cranial Nerve Tumor; eighth cranial nerve tumor; eighth cranial nerve tumour; Neoplasm of acoustic nerve; Neoplasm of Acoustic Nerve; neoplasm of acoustic nerve; Neoplasm of Eighth Cranial Nerve; neoplasm of eighth cranial nerve; Neoplasm of the Acoustic Nerve; neoplasm of the acoustic nerve; Neoplasm of the Eighth Cranial Nerve; neoplasm of the eighth cranial nerve; Neoplasm of the Vestibulocochlear Nerve; neoplasm of the vestibulocochlear nerve; Neoplasm of Vestibulocochlear Nerve; neoplasm of vestibulocochlear nerve; Tumor of Acoustic Nerve; tumor of acoustic nerve; Tumor of eighth cranial nerve; Tumor of Eighth Cranial Nerve; tumor of eighth cranial nerve; Tumor of the Acoustic Nerve; tumor of the acoustic nerve; Tumor of the Eighth Cranial Nerve; tumor of the eighth cranial nerve; Tumor of the Vestibulocochlear Nerve; tumor of the vestibulocochlear nerve; Tumor of Vestibulocochlear Nerve; tumor of vestibulocochlear nerve; Tumor of VIII cranial nerve; tumour of acoustic nerve; tumour of eighth cranial nerve; tumour of the acoustic nerve; tumour of the eighth cranial nerve; tumour of the vestibulocochlear nerve; tumour of vestibulocochlear nerve; Vestibuloacoustic Nerve Neoplasms; Vestibuloacoustic nerve neoplasms; Vestibulocochlear Nerve Neoplasm; vestibulocochlear nerve neoplasm; vestibulocochlear nerve neoplasm (disease); Vestibulocochlear Nerve Neoplasms; vestibulocochlear nerve neoplasms; Vestibulocochlear Nerve Tumor; vestibulocochlear nerve tumor; vestibulocochlear nerve tumour
SNOMED CT: Neoplasm of acoustic nerve (387891008); Tumor of VIII cranial nerve (387891008); Tumor of eighth cranial nerve (387891008)
 
Monarch Initiative: MONDO:0021221

Definition

A benign or malignant neoplasm affecting the eighth cranial nerve, also referred to as the vestibulocochlear nerve. Clinical features may include hearing loss, vertigo, tinnitus, headache and involvement of the trigeminal or facial nerves. [from NCI]

Professional guidelines

PubMed

ERN GENTURIS clinical practice guidelines for the diagnosis, treatment, management and surveillance of people with schwannomatosis.
Evans DG, Mostaccioli S, Pang D, Fadzil O Connor M, Pittara M, Champollion N, Wolkenstein P, Thomas N, Ferner RE, Kalamarides M, Peyre M, Papi L, Legius E, Becerra JL, King A, Duff C, Stivaros S, Blanco I
Eur J Hum Genet 2022 Jul;30(7):812-817. Epub 2022 Apr 1 doi: 10.1038/s41431-022-01086-x. PMID: 35361920Free PMC Article
A review of treatment modalities for vestibular schwannoma.
Arthurs BJ, Fairbanks RK, Demakas JJ, Lamoreaux WT, Giddings NA, Mackay AR, Cooke BS, Elaimy AL, Lee CM
Neurosurg Rev 2011 Jul;34(3):265-77; discussion 277-9. Epub 2011 Feb 9 doi: 10.1007/s10143-011-0307-8. PMID: 21305333
Controversies in building a management algorithm for vestibular schwannomas.
Doherty JK, Friedman RA
Curr Opin Otolaryngol Head Neck Surg 2006 Oct;14(5):305-13. doi: 10.1097/01.moo.0000244186.72645.d4. PMID: 16974142

Recent clinical studies

Etiology

Vestibular Schwannoma: What We Know and Where We are Heading.
Gupta VK, Thakker A, Gupta KK
Head Neck Pathol 2020 Dec;14(4):1058-1066. Epub 2020 Mar 30 doi: 10.1007/s12105-020-01155-x. PMID: 32232723Free PMC Article
Diagnosis and therapy of vestibular schwannoma.
Mann W, Gouveris HT
Expert Rev Neurother 2009 Aug;9(8):1219-32. doi: 10.1586/ern.09.66. PMID: 19673609
Meningiomas of the internal auditory canal.
Nakamura M, Roser F, Mirzai S, Matthies C, Vorkapic P, Samii M
Neurosurgery 2004 Jul;55(1):119-27; discussion 127-8. doi: 10.1227/01.neu.0000126887.55995.e7. PMID: 15214980
Neurofibromatosis.
Roos KL, Muckway M
Dermatol Clin 1995 Jan;13(1):105-11. PMID: 7712636
Bilateral acoustic neuromas.
Anand VT, Byrnes DP, Walby AP, Kerr AG
Clin Otolaryngol Allied Sci 1993 Oct;18(5):365-71. doi: 10.1111/j.1365-2273.1993.tb00594.x. PMID: 8877201

Diagnosis

The Vestibulocochlear Nerve: Anatomy and Pathology.
Corrêa DG, Hygino da Cruz LC Jr, Freddi TAL
Semin Ultrasound CT MR 2023 Apr;44(2):81-94. Epub 2023 Mar 22 doi: 10.1053/j.sult.2023.03.007. PMID: 37055143
The vestibulocochlear nerve (VIII).
Benoudiba F, Toulgoat F, Sarrazin JL
Diagn Interv Imaging 2013 Oct;94(10):1043-50. Epub 2013 Oct 1 doi: 10.1016/j.diii.2013.08.015. PMID: 24095603
The vestibulocochlear nerve.
Spickler EM, Govila L
Semin Ultrasound CT MR 2002 Jun;23(3):218-37. doi: 10.1016/s0887-2171(02)90048-x. PMID: 12168998
Bilateral acoustic neuromas.
Anand VT, Byrnes DP, Walby AP, Kerr AG
Clin Otolaryngol Allied Sci 1993 Oct;18(5):365-71. doi: 10.1111/j.1365-2273.1993.tb00594.x. PMID: 8877201
Electro-nystagmography.
Hood JD
J Laryngol Otol 1968 Mar;82(3):167-83. doi: 10.1017/s0022215100068651. PMID: 5640988

Therapy

Postoperative headache following treatment of vestibular schwannoma: A literature review.
Sabab A, Sandhu J, Bacchi S, Jukes A, Zacest A
J Clin Neurosci 2018 Jun;52:26-31. Epub 2018 Apr 12 doi: 10.1016/j.jocn.2018.04.003. PMID: 29656878
Complications in translabyrinthine surgery of vestibular schwannoma.
Ölander C, Gudjonsson O, Kinnefors A, Laurell G, Edfeldt L
Acta Otolaryngol 2018 Jul;138(7):639-645. Epub 2018 Jan 23 doi: 10.1080/00016489.2018.1427887. PMID: 29361875
Systematic review of quality of life in the management of vestibular schwannoma.
Gauden A, Weir P, Hawthorne G, Kaye A
J Clin Neurosci 2011 Dec;18(12):1573-84. Epub 2011 Oct 19 doi: 10.1016/j.jocn.2011.05.009. PMID: 22014598
Retrosigmoid approach for small and medium-sized acoustic neuromas.
Magnan J, Barbieri M, Mora R, Murphy S, Meller R, Bruzzo M, Chays A
Otol Neurotol 2002 Mar;23(2):141-5. doi: 10.1097/00129492-200203000-00006. PMID: 11875340
Otoneurology.
Perlman HB, Lindsay JR
Prog Neurol Psychiatry 1968;23:198-202. PMID: 4976880

Prognosis

Optimized preoperative determination of nerve of origin in patients with vestibular schwannoma.
Rahne T, Plontke SK, Fröhlich L, Strauss C
Sci Rep 2021 Apr 21;11(1):8608. doi: 10.1038/s41598-021-87515-1. PMID: 33883565Free PMC Article
Postoperative headache following treatment of vestibular schwannoma: A literature review.
Sabab A, Sandhu J, Bacchi S, Jukes A, Zacest A
J Clin Neurosci 2018 Jun;52:26-31. Epub 2018 Apr 12 doi: 10.1016/j.jocn.2018.04.003. PMID: 29656878
Meningiomas of the internal auditory canal.
Nakamura M, Roser F, Mirzai S, Matthies C, Vorkapic P, Samii M
Neurosurgery 2004 Jul;55(1):119-27; discussion 127-8. doi: 10.1227/01.neu.0000126887.55995.e7. PMID: 15214980
Retrosigmoid approach for small and medium-sized acoustic neuromas.
Magnan J, Barbieri M, Mora R, Murphy S, Meller R, Bruzzo M, Chays A
Otol Neurotol 2002 Mar;23(2):141-5. doi: 10.1097/00129492-200203000-00006. PMID: 11875340
Management of seventh and eighth nerve involvement by cerebellopontine angle tumors.
Samii M, Turel KE, Penkert G
Clin Neurosurg 1985;32:242-72. PMID: 3933876

Clinical prediction guides

Management of Vestibular Schwannomas for the Radiologist.
Ramaswamy AT, Golub JS
Neuroimaging Clin N Am 2019 Feb;29(1):173-182. Epub 2018 Oct 31 doi: 10.1016/j.nic.2018.09.003. PMID: 30466639
Systematic review of quality of life in the management of vestibular schwannoma.
Gauden A, Weir P, Hawthorne G, Kaye A
J Clin Neurosci 2011 Dec;18(12):1573-84. Epub 2011 Oct 19 doi: 10.1016/j.jocn.2011.05.009. PMID: 22014598
Vestibular neurectomy.
Thomsen J, Berner B, Tos M
Auris Nasus Larynx 2000 Oct;27(4):297-301. doi: 10.1016/s0385-8146(00)00076-6. PMID: 10996487
Bilateral acoustic neuromas.
Anand VT, Byrnes DP, Walby AP, Kerr AG
Clin Otolaryngol Allied Sci 1993 Oct;18(5):365-71. doi: 10.1111/j.1365-2273.1993.tb00594.x. PMID: 8877201
Management of seventh and eighth nerve involvement by cerebellopontine angle tumors.
Samii M, Turel KE, Penkert G
Clin Neurosurg 1985;32:242-72. PMID: 3933876

Recent systematic reviews

Cranial Nerve Disorders Associated With Immune Checkpoint Inhibitors.
Vogrig A, Muñiz-Castrillo S, Joubert B, Picard G, Rogemond V, Skowron F, Egri M, Desestret V, Tilikete C, Psimaras D, Ducray F, Honnorat J
Neurology 2021 Feb 9;96(6):e866-e875. Epub 2020 Dec 14 doi: 10.1212/WNL.0000000000011340. PMID: 33318162
Indications and contraindications of auditory brainstem implants: systematic review and illustrative cases.
Merkus P, Di Lella F, Di Trapani G, Pasanisi E, Beltrame MA, Zanetti D, Negri M, Sanna M
Eur Arch Otorhinolaryngol 2014 Jan;271(1):3-13. Epub 2013 Feb 13 doi: 10.1007/s00405-013-2378-3. PMID: 23404468
Systematic review of quality of life in the management of vestibular schwannoma.
Gauden A, Weir P, Hawthorne G, Kaye A
J Clin Neurosci 2011 Dec;18(12):1573-84. Epub 2011 Oct 19 doi: 10.1016/j.jocn.2011.05.009. PMID: 22014598
Risk factors associated with vestibulocochlear nerve schwannoma: systematic review.
Corona AP, Oliveira JC, Souza FP, Santana LV, Rêgo MA
Braz J Otorhinolaryngol 2009 Jul-Aug;75(4):593-615. doi: 10.1016/s1808-8694(15)30501-2. PMID: 19784431Free PMC Article
Hearing preservation after stereotactic radiosurgery for vestibular schwannoma: a systematic review.
Yang I, Aranda D, Han SJ, Chennupati S, Sughrue ME, Cheung SW, Pitts LH, Parsa AT
J Clin Neurosci 2009 Jun;16(6):742-7. Epub 2009 Mar 20 doi: 10.1016/j.jocn.2008.09.023. PMID: 19303780

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