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Cellular schwannoma

MedGen UID:
98124
Concept ID:
C0431124
Neoplastic Process
Synonyms: Cellular neurilemmoma; Cellular Neurilemmoma; cellular neurilemmoma; Cellular Neurinoma; cellular neurinoma; Cellular Schwannoma; cellular schwannoma; CSCHW
SNOMED CT: Cellular neurilemmoma (404026003); Cellular schwannoma (404026003); Cellular neurilemmoma (253086004); Cellular schwannoma (253086004)
 
Monarch Initiative: MONDO:0002548

Definition

A morphologic variant of schwannoma characterized by hypercellularity, Antoni A pattern, and the absence of well-formed Verocay bodies. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCellular schwannoma

Professional guidelines

PubMed

Magro G
Surg Pathol Clin 2018 Mar;11(1):91-121. Epub 2017 Dec 9 doi: 10.1016/j.path.2017.09.005. PMID: 29413661
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Expert Rev Neurother 2018 Jan;18(1):29-39. Epub 2017 Nov 7 doi: 10.1080/14737175.2018.1399795. PMID: 29088993
Karsy M, Guan J, Sivakumar W, Neil JA, Schmidt MH, Mahan MA
Neurosurg Focus 2015 Aug;39(2):E3. doi: 10.3171/2015.5.FOCUS15143. PMID: 26235020

Recent clinical studies

Etiology

Shapira Y, Juniat V, Dave T, Hussain A, McNeely D, Watanabe A, Yoneda A, Saeed P, Woo KI, Hardy TG, Price B, Drummond K, Selva D
Eye (Lond) 2023 Jan;37(1):48-53. Epub 2022 Jan 9 doi: 10.1038/s41433-021-01850-1. PMID: 34999720Free PMC Article
Zhang Z, Zheng X, Zhang D, Zhang J, Li F, Li C, Wang X, Li J, Han D, Zhang J
World Neurosurg 2022 Feb;158:e166-e178. Epub 2021 Oct 26 doi: 10.1016/j.wneu.2021.10.145. PMID: 34710579
Zhu J, Yang Z, Tang R, Tang G
Eur J Radiol 2021 Aug;141:109783. Epub 2021 May 21 doi: 10.1016/j.ejrad.2021.109783. PMID: 34049057
D'Almeida Costa F, Dias TM, Lombardo KA, Raghunathan A, Giannini C, Kenyon L, Saad AG, Gokden M, Burger PC, Montgomery EA, Rodriguez FJ
Histopathology 2020 Jan;76(2):275-282. Epub 2019 Nov 13 doi: 10.1111/his.13967. PMID: 31379028Free PMC Article
Zhang E, Zhang J, Lang N, Yuan H
Eur J Radiol 2018 Aug;105:81-86. Epub 2018 May 30 doi: 10.1016/j.ejrad.2018.05.025. PMID: 30017303

Diagnosis

Shapira Y, Juniat V, Dave T, Hussain A, McNeely D, Watanabe A, Yoneda A, Saeed P, Woo KI, Hardy TG, Price B, Drummond K, Selva D
Eye (Lond) 2023 Jan;37(1):48-53. Epub 2022 Jan 9 doi: 10.1038/s41433-021-01850-1. PMID: 34999720Free PMC Article
Coy S, Rashid R, Stemmer-Rachamimov A, Santagata S
Acta Neuropathol 2020 Apr;139(4):643-665. Epub 2019 Jun 4 doi: 10.1007/s00401-019-02029-5. PMID: 31161239Free PMC Article
Zhang E, Zhang J, Lang N, Yuan H
Eur J Radiol 2018 Aug;105:81-86. Epub 2018 May 30 doi: 10.1016/j.ejrad.2018.05.025. PMID: 30017303
Domen H, Iwashiro N, Kimura N, Jinushi E, Komuro K, Ohara M, Ishizaka M
Ann Thorac Surg 2010 Oct;90(4):1352-5. doi: 10.1016/j.athoracsur.2010.04.023. PMID: 20868846
Megahed M, Ruzicka T
Am J Dermatopathol 1994 Aug;16(4):418-21. doi: 10.1097/00000372-199408000-00012. PMID: 7978072

Therapy

J Neurosurg Spine 2017 Apr;26(4):494-500. Epub 2017 Jan 13 doi: 10.3171/2016.9.SPINE16778. PMID: 28084933
Ayberk G, Ozveren MF, Yildirim T, Ercan K, Cay EK, Koçak A
Turk Neurosurg 2008 Oct;18(4):366-73. PMID: 19107682
Koyye RT, Mahadevan A, Santosh V, Chickabasaviah YT, Govindappa SS, Hegde T, Shankar SK
Brain Tumor Pathol 2003;20(2):79-83. doi: 10.1007/BF02483451. PMID: 14756445

Prognosis

Zhang Z, Zheng X, Zhang D, Zhang J, Li F, Li C, Wang X, Li J, Han D, Zhang J
World Neurosurg 2022 Feb;158:e166-e178. Epub 2021 Oct 26 doi: 10.1016/j.wneu.2021.10.145. PMID: 34710579
Zhu J, Yang Z, Tang R, Tang G
Eur J Radiol 2021 Aug;141:109783. Epub 2021 May 21 doi: 10.1016/j.ejrad.2021.109783. PMID: 34049057
Coy S, Rashid R, Stemmer-Rachamimov A, Santagata S
Acta Neuropathol 2020 Apr;139(4):643-665. Epub 2019 Jun 4 doi: 10.1007/s00401-019-02029-5. PMID: 31161239Free PMC Article
Zhang E, Zhang J, Lang N, Yuan H
Eur J Radiol 2018 Aug;105:81-86. Epub 2018 May 30 doi: 10.1016/j.ejrad.2018.05.025. PMID: 30017303
Kurtkaya-Yapicier O, Scheithauer B, Woodruff JM
Histol Histopathol 2003 Jul;18(3):925-34. doi: 10.14670/HH-18.925. PMID: 12792904

Clinical prediction guides

Shapira Y, Juniat V, Dave T, Hussain A, McNeely D, Watanabe A, Yoneda A, Saeed P, Woo KI, Hardy TG, Price B, Drummond K, Selva D
Eye (Lond) 2023 Jan;37(1):48-53. Epub 2022 Jan 9 doi: 10.1038/s41433-021-01850-1. PMID: 34999720Free PMC Article
Thompson LDR, Koh SS, Lau SK
Head Neck Pathol 2020 Sep;14(3):571-576. Epub 2019 Sep 4 doi: 10.1007/s12105-019-01071-9. PMID: 31485983Free PMC Article
Jo VY, Mariño-Enríquez A, Fletcher CDM, Hornick JL
Am J Surg Pathol 2018 Oct;42(10):1275-1285. doi: 10.1097/PAS.0000000000001092. PMID: 29863547
Pekmezci M, Reuss DE, Hirbe AC, Dahiya S, Gutmann DH, von Deimling A, Horvai AE, Perry A
Mod Pathol 2015 Feb;28(2):187-200. Epub 2014 Sep 5 doi: 10.1038/modpathol.2014.109. PMID: 25189642Free PMC Article
Casadei GP, Scheithauer BW, Hirose T, Manfrini M, Van Houton C, Wood MB
Cancer 1995 Mar 1;75(5):1109-19. doi: 10.1002/1097-0142(19950301)75:5<1109::aid-cncr2820750510>3.0.co;2-m. PMID: 7850709

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