Abstract
We report a 2-month-old boy with severe congenital neutropenia (SCN), who developed acute necrotizing otitis media and coalescent mastoiditis due to methicillin-sensitive Staphylococcus aureus. The infection fulminantly progressed within a day to a subtotal perforation of the tympanic membrane, destructive bony changes of ossicles, lateral subperiosteal abscess, and suppurative labyrinthitis. Despite the combined treatment with intravenous antibiotics and granulocyte colony-stimulating factor, the infection resulted in mixed hearing impairment. Much attention should be given to prompt diagnosis of otomastoiditis in SCN, a rare congenital disorder, since resultant acoustic sequelae may affect subsequent speech development and intellectual ability.
MeSH terms
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Acute Disease
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Anti-Bacterial Agents
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Audiometry
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Drug Therapy, Combination / administration & dosage
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Follow-Up Studies
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Granulocyte Colony-Stimulating Factor / administration & dosage
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Hearing Disorders / diagnosis
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Hearing Disorders / etiology*
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Humans
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Infant
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Male
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Mastoiditis / complications
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Mastoiditis / diagnosis*
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Mastoiditis / drug therapy
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Neutropenia / complications
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Neutropenia / congenital*
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Neutropenia / drug therapy
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Otitis Media with Effusion / complications
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Otitis Media with Effusion / drug therapy
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Otitis Media with Effusion / microbiology*
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Risk Assessment
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Severity of Illness Index
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Staphylococcal Infections / complications
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Staphylococcal Infections / diagnosis*
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Staphylococcal Infections / drug therapy
Substances
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Anti-Bacterial Agents
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Granulocyte Colony-Stimulating Factor