β-catenin stabilization enhances SS18-SSX2-driven synovial sarcomagenesis and blocks the mesenchymal to epithelial transition

Oncotarget. 2015 Sep 8;6(26):22758-66. doi: 10.18632/oncotarget.4283.

Abstract

β-catenin is a master regulator in the cellular biology of development and neoplasia. Its dysregulation is implicated as a driver of colorectal carcinogenesis and the epithelial-mesenchymal transition in other cancers. Nuclear β-catenin staining is a poor prognostic sign in synovial sarcoma, the most common soft-tissue sarcoma in adolescents and young adults. We show through genetic experiments in a mouse model that expression of a stabilized form of β-catenin greatly enhances synovial sarcomagenesis. Stabilization of β-catenin enables a stem-cell phenotype in synovial sarcoma cells, specifically blocking epithelial differentiation and driving invasion. β-catenin achieves its reprogramming in part by upregulating transcription of TCF/LEF target genes. Even though synovial sarcoma is primarily a mesenchymal neoplasm, its progression towards a more aggressive and invasive phenotype parallels the epithelial-mesenchymal transition observed in epithelial cancers, where β-catenin's transcriptional contribution includes blocking epithelial differentiation.

Keywords: Wnt-signaling; epithelial-mesenchymal transition; mouse genetic model; translocation.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Disease Models, Animal
  • Epithelial-Mesenchymal Transition
  • Humans
  • Mice
  • Mice, Inbred C57BL
  • Oncogene Proteins, Fusion / genetics*
  • Sarcoma, Synovial / genetics
  • Sarcoma, Synovial / metabolism*
  • Sarcoma, Synovial / pathology*
  • Transcriptional Activation
  • Transfection
  • Wnt Signaling Pathway
  • beta Catenin / metabolism*

Substances

  • CTNNB1 protein, human
  • CTNNB1 protein, mouse
  • Oncogene Proteins, Fusion
  • SYT-SSX fusion protein
  • beta Catenin