Autophosphorylation of CaMKK2 generates autonomous activity that is disrupted by a T85S mutation linked to anxiety and bipolar disorder

Sci Rep. 2015 Sep 23:5:14436. doi: 10.1038/srep14436.

Abstract

Mutations that reduce expression or give rise to a Thr85Ser (T85S) mutation of Ca(2+)-CaM-dependent protein kinase kinase-2 (CaMKK2) have been implicated in behavioural disorders such as anxiety, bipolar and schizophrenia in humans. Here we report that Thr85 is an autophosphorylation site that endows CaMKK2 with a molecular memory that enables sustained autonomous activation following an initial, transient Ca(2+) signal. Conversely, autophosphorylation of Ser85 in the T85S mutant fails to generate autonomous activity but instead causes a partial loss of CaMKK2 activity. The loss of autonomous activity in the mutant can be rescued by blocking glycogen synthase kinase-3 (GSK3) phosphorylation of CaMKK2 with the anti-mania drug lithium. Furthermore, CaMKK2 null mice representing a loss of function model the human behavioural phenotypes, displaying anxiety and manic-like behavioural disturbances. Our data provide a novel insight into CaMKK2 regulation and its perturbation by a mutation associated with behavioural disorders.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Animals
  • Anxiety / genetics*
  • Bipolar Disorder / genetics*
  • COS Cells
  • Calcium / metabolism
  • Calcium-Calmodulin-Dependent Protein Kinase Kinase / genetics*
  • Calcium-Calmodulin-Dependent Protein Kinase Kinase / metabolism*
  • Cell Line
  • Chlorocebus aethiops
  • Glycogen Synthase Kinase 3 / antagonists & inhibitors
  • Humans
  • Ionomycin / pharmacology
  • Lithium Chloride / pharmacology
  • Maze Learning / physiology
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Mutation / genetics
  • Phosphorylation
  • Reflex, Startle / physiology
  • Sequence Alignment

Substances

  • Ionomycin
  • Calcium-Calmodulin-Dependent Protein Kinase Kinase
  • Camkk2 protein, mouse
  • Glycogen Synthase Kinase 3
  • Lithium Chloride
  • Calcium