LRRK1 is critical in the regulation of B-cell responses and CARMA1-dependent NF-κB activation

Sci Rep. 2016 May 11:6:25738. doi: 10.1038/srep25738.

Abstract

B-cell receptor (BCR) signaling plays a critical role in B-cell activation and humoral immunity. In this study, we discovered a critical function of leucine-rich repeat kinase 1 (LRRK1) in BCR-mediated immune responses. Lrrk1(-/-) mice exhibited altered B1a-cell development and basal immunoglobulin production. In addition, these mice failed to produce IgG3 antibody in response to T cell-independent type 2 antigen due to defects in IgG3 class-switch recombination. Concomitantly, B cells lacking LRRK1 exhibited a profound defect in proliferation and survival upon BCR stimulation, which correlated with impaired BCR-mediated NF-κB activation and reduced expression of NF-κB target genes including Bcl-xL, cyclin D2, and NFATc1/αA. Furthermore, LRRK1 physically interacted and potently synergized with CARMA1 to enhance NF-κB activation. Our results reveal a critical role of LRRK1 in NF-κB signaling in B cells and the humoral immune response.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Antibody Formation
  • B-Lymphocytes / cytology
  • B-Lymphocytes / metabolism*
  • CARD Signaling Adaptor Proteins / metabolism*
  • Cell Proliferation
  • Cell Survival
  • Endocytosis
  • HEK293 Cells
  • Humans
  • Immunoglobulin Class Switching
  • Immunoglobulin G / metabolism
  • Lymphocyte Activation
  • NF-kappa B / metabolism*
  • Peritoneal Cavity / cytology
  • Protein Serine-Threonine Kinases / deficiency
  • Protein Serine-Threonine Kinases / metabolism*
  • Receptors, Antigen, B-Cell / metabolism
  • Recombination, Genetic / genetics
  • Spleen / cytology
  • T-Lymphocytes / metabolism

Substances

  • CARD Signaling Adaptor Proteins
  • Card11 protein, mouse
  • Immunoglobulin G
  • NF-kappa B
  • Receptors, Antigen, B-Cell
  • Lrrk1 protein, mouse
  • Protein Serine-Threonine Kinases