Accumulation of tissue glucosylsphingosine in Gaucher-like mouse induced by the glucosylceramidase inhibitor cyclophellitol

Arch Biochem Biophys. 1993 Jul;304(1):302-4. doi: 10.1006/abbi.1993.1353.
No abstract available

MeSH terms

  • Animals
  • Brain / metabolism
  • Cells, Cultured
  • Cyclohexanols / pharmacology*
  • Disease Models, Animal
  • Gaucher Disease / metabolism*
  • Glucosylceramidase / antagonists & inhibitors
  • In Vitro Techniques
  • Liver / metabolism
  • Mice
  • Psychosine / analogs & derivatives*
  • Psychosine / metabolism
  • Spleen / metabolism

Substances

  • Cyclohexanols
  • cyclophellitol
  • Psychosine
  • sphingosyl beta-glucoside
  • Glucosylceramidase