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Idiopathic multicentric Castleman disease

MedGen UID:
1680858
Concept ID:
C5197665
Disease or Syndrome
Synonyms: HHV-8-negative idiopathic multicentric Castleman disease; HHV-8-negative MCD; Idiopathic multicentric Castleman's disease
 
Monarch Initiative: MONDO:0035838
Orphanet: ORPHA570431

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVIdiopathic multicentric Castleman disease

Professional guidelines

PubMed

van Rhee F, Voorhees P, Dispenzieri A, Fosså A, Srkalovic G, Ide M, Munshi N, Schey S, Streetly M, Pierson SK, Partridge HL, Mukherjee S, Shilling D, Stone K, Greenway A, Ruth J, Lechowicz MJ, Chandrakasan S, Jayanthan R, Jaffe ES, Leitch H, Pemmaraju N, Chadburn A, Lim MS, Elenitoba-Johnson KS, Krymskaya V, Goodman A, Hoffmann C, Zinzani PL, Ferrero S, Terriou L, Sato Y, Simpson D, Wong R, Rossi JF, Nasta S, Yoshizaki K, Kurzrock R, Uldrick TS, Casper C, Oksenhendler E, Fajgenbaum DC
Blood 2018 Nov 15;132(20):2115-2124. Epub 2018 Sep 4 doi: 10.1182/blood-2018-07-862334. PMID: 30181172Free PMC Article
van Rhee F, Greenway A, Stone K
Hematol Oncol Clin North Am 2018 Feb;32(1):89-106. doi: 10.1016/j.hoc.2017.09.008. PMID: 29157622
Fajgenbaum DC, Uldrick TS, Bagg A, Frank D, Wu D, Srkalovic G, Simpson D, Liu AY, Menke D, Chandrakasan S, Lechowicz MJ, Wong RS, Pierson S, Paessler M, Rossi JF, Ide M, Ruth J, Croglio M, Suarez A, Krymskaya V, Chadburn A, Colleoni G, Nasta S, Jayanthan R, Nabel CS, Casper C, Dispenzieri A, Fosså A, Kelleher D, Kurzrock R, Voorhees P, Dogan A, Yoshizaki K, van Rhee F, Oksenhendler E, Jaffe ES, Elenitoba-Johnson KS, Lim MS
Blood 2017 Mar 23;129(12):1646-1657. Epub 2017 Jan 13 doi: 10.1182/blood-2016-10-746933. PMID: 28087540Free PMC Article

Curated

NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Castleman Disease, 2024

Recent clinical studies

Etiology

Adam Z, Řehák Z, Adamová Z, Koukalová R, Pour L, Krejčí M, Boichuk I, Sandecká V, Krejčí M, Štork M, Ševčíková S, Král Z
Vnitr Lek 2022 Winter;68(1):41-53. PMID: 35459346
Fajgenbaum DC
Hematology Am Soc Hematol Educ Program 2018 Nov 30;2018(1):318-325. doi: 10.1182/asheducation-2018.1.318. PMID: 30504327Free PMC Article
Fajgenbaum DC
Blood 2018 Nov 29;132(22):2323-2330. doi: 10.1182/blood-2018-05-848671. PMID: 30487129Free PMC Article
van Rhee F, Voorhees P, Dispenzieri A, Fosså A, Srkalovic G, Ide M, Munshi N, Schey S, Streetly M, Pierson SK, Partridge HL, Mukherjee S, Shilling D, Stone K, Greenway A, Ruth J, Lechowicz MJ, Chandrakasan S, Jayanthan R, Jaffe ES, Leitch H, Pemmaraju N, Chadburn A, Lim MS, Elenitoba-Johnson KS, Krymskaya V, Goodman A, Hoffmann C, Zinzani PL, Ferrero S, Terriou L, Sato Y, Simpson D, Wong R, Rossi JF, Nasta S, Yoshizaki K, Kurzrock R, Uldrick TS, Casper C, Oksenhendler E, Fajgenbaum DC
Blood 2018 Nov 15;132(20):2115-2124. Epub 2018 Sep 4 doi: 10.1182/blood-2018-07-862334. PMID: 30181172Free PMC Article
Fajgenbaum DC, Uldrick TS, Bagg A, Frank D, Wu D, Srkalovic G, Simpson D, Liu AY, Menke D, Chandrakasan S, Lechowicz MJ, Wong RS, Pierson S, Paessler M, Rossi JF, Ide M, Ruth J, Croglio M, Suarez A, Krymskaya V, Chadburn A, Colleoni G, Nasta S, Jayanthan R, Nabel CS, Casper C, Dispenzieri A, Fosså A, Kelleher D, Kurzrock R, Voorhees P, Dogan A, Yoshizaki K, van Rhee F, Oksenhendler E, Jaffe ES, Elenitoba-Johnson KS, Lim MS
Blood 2017 Mar 23;129(12):1646-1657. Epub 2017 Jan 13 doi: 10.1182/blood-2016-10-746933. PMID: 28087540Free PMC Article

Diagnosis

González García A, Fernández-Martín J, Robles Marhuenda Á
Rheumatology (Oxford) 2023 Apr 3;62(4):1426-1435. doi: 10.1093/rheumatology/keac481. PMID: 35997567Free PMC Article
Masaki Y, Arita K, Sakai T, Takai K, Aoki S, Kawabata H
Ann Hematol 2022 Mar;101(3):485-490. Epub 2022 Jan 19 doi: 10.1007/s00277-022-04762-6. PMID: 35044513Free PMC Article
Nishimura Y, Fajgenbaum DC, Pierson SK, Iwaki N, Nishikori A, Kawano M, Nakamura N, Izutsu K, Takeuchi K, Nishimura MF, Maeda Y, Otsuka F, Yoshizaki K, Oksenhendler E, van Rhee F, Sato Y
Am J Hematol 2021 Oct 1;96(10):1241-1252. Epub 2021 Jul 28 doi: 10.1002/ajh.26292. PMID: 34265103Free PMC Article
Igawa T, Sato Y
Hematol Oncol Clin North Am 2018 Feb;32(1):107-118. doi: 10.1016/j.hoc.2017.09.009. PMID: 29157612
Fajgenbaum DC, Uldrick TS, Bagg A, Frank D, Wu D, Srkalovic G, Simpson D, Liu AY, Menke D, Chandrakasan S, Lechowicz MJ, Wong RS, Pierson S, Paessler M, Rossi JF, Ide M, Ruth J, Croglio M, Suarez A, Krymskaya V, Chadburn A, Colleoni G, Nasta S, Jayanthan R, Nabel CS, Casper C, Dispenzieri A, Fosså A, Kelleher D, Kurzrock R, Voorhees P, Dogan A, Yoshizaki K, van Rhee F, Oksenhendler E, Jaffe ES, Elenitoba-Johnson KS, Lim MS
Blood 2017 Mar 23;129(12):1646-1657. Epub 2017 Jan 13 doi: 10.1182/blood-2016-10-746933. PMID: 28087540Free PMC Article

Therapy

Pierson SK, Lim MS, Srkalovic G, Brandstadter JD, Sarmiento Bustamante M, Shyamsundar S, Mango N, Lavery C, Austin B, Alapat D, Lechowicz MJ, Bagg A, Li H, Casper C, van Rhee F, Fajgenbaum DC
Blood Adv 2023 Nov 14;7(21):6652-6664. doi: 10.1182/bloodadvances.2023010745. PMID: 37656441Free PMC Article
Fajgenbaum DC
Blood 2018 Nov 29;132(22):2323-2330. doi: 10.1182/blood-2018-05-848671. PMID: 30487129Free PMC Article
van Rhee F, Voorhees P, Dispenzieri A, Fosså A, Srkalovic G, Ide M, Munshi N, Schey S, Streetly M, Pierson SK, Partridge HL, Mukherjee S, Shilling D, Stone K, Greenway A, Ruth J, Lechowicz MJ, Chandrakasan S, Jayanthan R, Jaffe ES, Leitch H, Pemmaraju N, Chadburn A, Lim MS, Elenitoba-Johnson KS, Krymskaya V, Goodman A, Hoffmann C, Zinzani PL, Ferrero S, Terriou L, Sato Y, Simpson D, Wong R, Rossi JF, Nasta S, Yoshizaki K, Kurzrock R, Uldrick TS, Casper C, Oksenhendler E, Fajgenbaum DC
Blood 2018 Nov 15;132(20):2115-2124. Epub 2018 Sep 4 doi: 10.1182/blood-2018-07-862334. PMID: 30181172Free PMC Article
van Rhee F, Greenway A, Stone K
Hematol Oncol Clin North Am 2018 Feb;32(1):89-106. doi: 10.1016/j.hoc.2017.09.008. PMID: 29157622
Fajgenbaum DC, Kurzrock R
Immunotherapy 2016;8(1):17-26. Epub 2015 Dec 4 doi: 10.2217/imt.15.95. PMID: 26634298

Prognosis

Pierson SK, Katz L, Williams R, Mumau M, Gonzalez M, Guzman S, Rubenstein A, Oromendia AB, Beineke P, Fosså A, van Rhee F, Fajgenbaum DC
Nat Commun 2022 Nov 24;13(1):7236. doi: 10.1038/s41467-022-34873-7. PMID: 36433996Free PMC Article
Igawa T, Sato Y
Hematol Oncol Clin North Am 2018 Feb;32(1):107-118. doi: 10.1016/j.hoc.2017.09.009. PMID: 29157612
Simpson D
Hematol Oncol Clin North Am 2018 Feb;32(1):1-10. doi: 10.1016/j.hoc.2017.09.001. PMID: 29157611
Srkalovic G, Marijanovic I, Srkalovic MB, Fajgenbaum DC
Bosn J Basic Med Sci 2017 May 20;17(2):81-84. doi: 10.17305/bjbms.2017.1930. PMID: 28135567Free PMC Article
Fajgenbaum DC, Kurzrock R
Immunotherapy 2016;8(1):17-26. Epub 2015 Dec 4 doi: 10.2217/imt.15.95. PMID: 26634298

Clinical prediction guides

Pierson SK, Lim MS, Srkalovic G, Brandstadter JD, Sarmiento Bustamante M, Shyamsundar S, Mango N, Lavery C, Austin B, Alapat D, Lechowicz MJ, Bagg A, Li H, Casper C, van Rhee F, Fajgenbaum DC
Blood Adv 2023 Nov 14;7(21):6652-6664. doi: 10.1182/bloodadvances.2023010745. PMID: 37656441Free PMC Article
Pierson SK, Katz L, Williams R, Mumau M, Gonzalez M, Guzman S, Rubenstein A, Oromendia AB, Beineke P, Fosså A, van Rhee F, Fajgenbaum DC
Nat Commun 2022 Nov 24;13(1):7236. doi: 10.1038/s41467-022-34873-7. PMID: 36433996Free PMC Article
Fajgenbaum DC
Hematology Am Soc Hematol Educ Program 2018 Nov 30;2018(1):318-325. doi: 10.1182/asheducation-2018.1.318. PMID: 30504327Free PMC Article
Fajgenbaum DC
Blood 2018 Nov 29;132(22):2323-2330. doi: 10.1182/blood-2018-05-848671. PMID: 30487129Free PMC Article
Fajgenbaum DC, Kurzrock R
Immunotherapy 2016;8(1):17-26. Epub 2015 Dec 4 doi: 10.2217/imt.15.95. PMID: 26634298

Recent systematic reviews

Belyaeva E, Rubenstein A, Pierson SK, Dalldorf D, Frank D, Lim MS, Fajgenbaum DC
Hematol Oncol 2022 Apr;40(2):191-201. Epub 2022 Feb 18 doi: 10.1002/hon.2969. PMID: 35104370Free PMC Article

Supplemental Content

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    Clinical resources

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      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Curated

    • NCCN, 2024
      NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Castleman Disease, 2024

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