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Refractory Chordoma

MedGen UID:
1689454
Concept ID:
C5206769
Neoplastic Process

Definition

A chordoma that does not respond to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRefractory Chordoma

Professional guidelines

PubMed

Wang L, Tian K, Ma J, Wang K, Jia G, Wu Z, Zhang L, Zhang J
Acta Neurochir (Wien) 2017 Oct;159(10):1803-1813. Epub 2017 Jul 11 doi: 10.1007/s00701-017-3261-6. PMID: 28699066
Ailon T, Torabi R, Fisher CG, Rhines LD, Clarke MJ, Bettegowda C, Boriani S, Yamada YJ, Kawahara N, Varga PP, Shin JH, Saghal A, Gokaslan ZL
Spine (Phila Pa 1976) 2016 Oct 15;41 Suppl 20(Suppl 20):S193-S198. doi: 10.1097/BRS.0000000000001812. PMID: 27753782Free PMC Article
Patel SS, Schwab JH
Curr Oncol Rep 2016 Sep;18(9):55. doi: 10.1007/s11912-016-0543-8. PMID: 27475804

Recent clinical studies

Etiology

Jalessi M, Gholami MS, Razmara E, Hassanzadeh S, Sadeghipour A, Jahanbakhshi A, Tabibkhooei A, Bahrami E, Falah M
J Clin Lab Anal 2022 Jan;36(1):e24150. Epub 2021 Nov 27 doi: 10.1002/jcla.24150. PMID: 34837714Free PMC Article
Chanplakorn P, Lertudomphonwanit T, Homcharoen W, Suwanpramote P, Laohacharoensombat W
World J Surg Oncol 2020 Aug 27;18(1):228. doi: 10.1186/s12957-020-02005-4. PMID: 32854731Free PMC Article
Morimoto Y, Tamura R, Ohara K, Kosugi K, Oishi Y, Kuranari Y, Yoshida K, Toda M
J Neurooncol 2019 Aug;144(1):65-77. Epub 2019 Jun 25 doi: 10.1007/s11060-019-03221-z. PMID: 31240525
Ailon T, Torabi R, Fisher CG, Rhines LD, Clarke MJ, Bettegowda C, Boriani S, Yamada YJ, Kawahara N, Varga PP, Shin JH, Saghal A, Gokaslan ZL
Spine (Phila Pa 1976) 2016 Oct 15;41 Suppl 20(Suppl 20):S193-S198. doi: 10.1097/BRS.0000000000001812. PMID: 27753782Free PMC Article
Patel SS, Schwab JH
Curr Oncol Rep 2016 Sep;18(9):55. doi: 10.1007/s11912-016-0543-8. PMID: 27475804

Diagnosis

Chanplakorn P, Lertudomphonwanit T, Homcharoen W, Suwanpramote P, Laohacharoensombat W
World J Surg Oncol 2020 Aug 27;18(1):228. doi: 10.1186/s12957-020-02005-4. PMID: 32854731Free PMC Article
Asklund T, Danfors T, Henriksson R
Clin Neuropathol 2011 Sep-Oct;30(5):242-6. doi: 10.5414/np300371. PMID: 21955928
Singhal N, Kotasek D, Parnis FX
Anticancer Drugs 2009 Nov;20(10):953-5. doi: 10.1097/CAD.0b013e328330c7f0. PMID: 19730087
Geoerger B, Morland B, Ndiaye A, Doz F, Kalifa G, Geoffray A, Pichon F, Frappaz D, Chatelut E, Opolon P, Hain S, Boderet F, Bosq J, Emile JF, Le Deley MC, Capdeville R, Vassal G; Innovative Therapies for Children with Cancer European Consortium
Eur J Cancer 2009 Sep;45(13):2342-51. Epub 2009 Apr 9 doi: 10.1016/j.ejca.2009.03.007. PMID: 19362466

Therapy

Stacchiotti S, Baldi GG, Frezza AM, Morosi C, Greco FG, Collini P, Barisella M, Dagrada GP, Zaffaroni N, Pasquali S, Gronchi A, Huang P, Ingrosso M, Tinè G, Miceli R, Casali PG
Eur J Cancer 2023 Dec;195:113391. Epub 2023 Oct 18 doi: 10.1016/j.ejca.2023.113391. PMID: 37918286
D'Angelo SP, Richards AL, Conley AP, Woo HJ, Dickson MA, Gounder M, Kelly C, Keohan ML, Movva S, Thornton K, Rosenbaum E, Chi P, Nacev B, Chan JE, Slotkin EK, Kiesler H, Adamson T, Ling L, Rao P, Patel S, Livingston JA, Singer S, Agaram NP, Antonescu CR, Koff A, Erinjeri JP, Hwang S, Qin LX, Donoghue MTA, Tap WD
Nat Commun 2022 Jun 16;13(1):3477. doi: 10.1038/s41467-022-30874-8. PMID: 35710741Free PMC Article
Gröschel S, Hübschmann D, Raimondi F, Horak P, Warsow G, Fröhlich M, Klink B, Gieldon L, Hutter B, Kleinheinz K, Bonekamp D, Marschal O, Chudasama P, Mika J, Groth M, Uhrig S, Krämer S, Heining C, Heilig CE, Richter D, Reisinger E, Pfütze K, Eils R, Wolf S, von Kalle C, Brandts C, Scholl C, Weichert W, Richter S, Bauer S, Penzel R, Schröck E, Stenzinger A, Schlenk RF, Brors B, Russell RB, Glimm H, Schlesner M, Fröhling S
Nat Commun 2019 Apr 9;10(1):1635. doi: 10.1038/s41467-019-09633-9. PMID: 30967556Free PMC Article
Adenis A, Ray-Coquard I, Italiano A, Chauzit E, Bui-Nguyen B, Blay JY, Tresch-Bruneel E, Fournier C, Clisant S, Amela EY, Cassier PA, Molimard M, Penel N
Br J Cancer 2013 Nov 12;109(10):2574-8. Epub 2013 Oct 22 doi: 10.1038/bjc.2013.648. PMID: 24149182Free PMC Article
Asklund T, Danfors T, Henriksson R
Clin Neuropathol 2011 Sep-Oct;30(5):242-6. doi: 10.5414/np300371. PMID: 21955928

Prognosis

D'Angelo SP, Richards AL, Conley AP, Woo HJ, Dickson MA, Gounder M, Kelly C, Keohan ML, Movva S, Thornton K, Rosenbaum E, Chi P, Nacev B, Chan JE, Slotkin EK, Kiesler H, Adamson T, Ling L, Rao P, Patel S, Livingston JA, Singer S, Agaram NP, Antonescu CR, Koff A, Erinjeri JP, Hwang S, Qin LX, Donoghue MTA, Tap WD
Nat Commun 2022 Jun 16;13(1):3477. doi: 10.1038/s41467-022-30874-8. PMID: 35710741Free PMC Article
Chanplakorn P, Lertudomphonwanit T, Homcharoen W, Suwanpramote P, Laohacharoensombat W
World J Surg Oncol 2020 Aug 27;18(1):228. doi: 10.1186/s12957-020-02005-4. PMID: 32854731Free PMC Article
Tamura R, Sato M, Morimoto Y, Ohara K, Kosugi K, Oishi Y, Kuranari Y, Murase M, Yoshida K, Toda M
Exp Mol Pathol 2020 Jun;114:104408. Epub 2020 Feb 21 doi: 10.1016/j.yexmp.2020.104408. PMID: 32088190
Gröschel S, Hübschmann D, Raimondi F, Horak P, Warsow G, Fröhlich M, Klink B, Gieldon L, Hutter B, Kleinheinz K, Bonekamp D, Marschal O, Chudasama P, Mika J, Groth M, Uhrig S, Krämer S, Heining C, Heilig CE, Richter D, Reisinger E, Pfütze K, Eils R, Wolf S, von Kalle C, Brandts C, Scholl C, Weichert W, Richter S, Bauer S, Penzel R, Schröck E, Stenzinger A, Schlenk RF, Brors B, Russell RB, Glimm H, Schlesner M, Fröhling S
Nat Commun 2019 Apr 9;10(1):1635. doi: 10.1038/s41467-019-09633-9. PMID: 30967556Free PMC Article
Sa JK, Lee IH, Hong SD, Kong DS, Nam DH
Oncotarget 2017 Jan 3;8(1):1321-1328. doi: 10.18632/oncotarget.13616. PMID: 27901492Free PMC Article

Clinical prediction guides

Stacchiotti S, Baldi GG, Frezza AM, Morosi C, Greco FG, Collini P, Barisella M, Dagrada GP, Zaffaroni N, Pasquali S, Gronchi A, Huang P, Ingrosso M, Tinè G, Miceli R, Casali PG
Eur J Cancer 2023 Dec;195:113391. Epub 2023 Oct 18 doi: 10.1016/j.ejca.2023.113391. PMID: 37918286
D'Angelo SP, Richards AL, Conley AP, Woo HJ, Dickson MA, Gounder M, Kelly C, Keohan ML, Movva S, Thornton K, Rosenbaum E, Chi P, Nacev B, Chan JE, Slotkin EK, Kiesler H, Adamson T, Ling L, Rao P, Patel S, Livingston JA, Singer S, Agaram NP, Antonescu CR, Koff A, Erinjeri JP, Hwang S, Qin LX, Donoghue MTA, Tap WD
Nat Commun 2022 Jun 16;13(1):3477. doi: 10.1038/s41467-022-30874-8. PMID: 35710741Free PMC Article
Gröschel S, Hübschmann D, Raimondi F, Horak P, Warsow G, Fröhlich M, Klink B, Gieldon L, Hutter B, Kleinheinz K, Bonekamp D, Marschal O, Chudasama P, Mika J, Groth M, Uhrig S, Krämer S, Heining C, Heilig CE, Richter D, Reisinger E, Pfütze K, Eils R, Wolf S, von Kalle C, Brandts C, Scholl C, Weichert W, Richter S, Bauer S, Penzel R, Schröck E, Stenzinger A, Schlenk RF, Brors B, Russell RB, Glimm H, Schlesner M, Fröhling S
Nat Commun 2019 Apr 9;10(1):1635. doi: 10.1038/s41467-019-09633-9. PMID: 30967556Free PMC Article
Sa JK, Lee IH, Hong SD, Kong DS, Nam DH
Oncotarget 2017 Jan 3;8(1):1321-1328. doi: 10.18632/oncotarget.13616. PMID: 27901492Free PMC Article
Ji Z, Long H, Hu Y, Qiu X, Chen X, Li Z, Fan D, Ma B, Fan Q
J Exp Clin Cancer Res 2010 Dec 8;29(1):158. doi: 10.1186/1756-9966-29-158. PMID: 21143841Free PMC Article

Recent systematic reviews

Ailon T, Torabi R, Fisher CG, Rhines LD, Clarke MJ, Bettegowda C, Boriani S, Yamada YJ, Kawahara N, Varga PP, Shin JH, Saghal A, Gokaslan ZL
Spine (Phila Pa 1976) 2016 Oct 15;41 Suppl 20(Suppl 20):S193-S198. doi: 10.1097/BRS.0000000000001812. PMID: 27753782Free PMC Article

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