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Childhood Extranodal Marginal Zone Lymphoma of Mucosa-Associated Lymphoid Tissue

MedGen UID:
884669
Concept ID:
C4055247
Neoplastic Process
Synonym: Childhood MALT Lymphoma

Definition

An extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue that occurs during childhood. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChildhood Extranodal Marginal Zone Lymphoma of Mucosa-Associated Lymphoid Tissue

Professional guidelines

PubMed

Xavier AC, Suzuki R, Attarbaschi A
Best Pract Res Clin Haematol 2023 Mar;36(1):101440. Epub 2023 Jan 15 doi: 10.1016/j.beha.2023.101440. PMID: 36907633

Recent clinical studies

Etiology

Xavier AC, Suzuki R, Attarbaschi A
Best Pract Res Clin Haematol 2023 Mar;36(1):101440. Epub 2023 Jan 15 doi: 10.1016/j.beha.2023.101440. PMID: 36907633
Kleinstern G, Camp NJ, Berndt SI, Birmann BM, Nieters A, Bracci PM, McKay JD, Ghesquières H, Lan Q, Hjalgrim H, Benavente Y, Monnereau A, Wang SS, Zhang Y, Purdue MP, Zeleniuch-Jacquotte A, Giles GG, Vermeulen R, Cocco P, Albanes D, Teras LR, Brooks-Wilson AR, Vajdic CM, Kane E, Caporaso NE, Smedby KE, Salles G, Vijai J, Chanock SJ, Skibola CF, Rothman N, Slager SL, Cerhan JR
Cancer Epidemiol Biomarkers Prev 2020 May;29(5):1074-1078. Epub 2020 Feb 27 doi: 10.1158/1055-9965.EPI-19-0803. PMID: 32108027Free PMC Article
Din L, Sheikh M, Kosaraju N, Smedby KE, Bernatsky S, Berndt SI, Skibola CF, Nieters A, Wang S, McKay JD, Cocco P, Maynadié M, Foretová L, Staines A, Mack TM, de Sanjosé S, Vyse TJ, Padyukov L, Monnereau A, Arslan AA, Moore A, Brooks-Wilson AR, Novak AJ, Glimelius B, Birmann BM, Link BK, Stewart C, Vajdic CM, Haioun C, Magnani C, Conti DV, Cox DG, Casabonne D, Albanes D, Kane E, Roman E, Muzi G, Salles G, Giles GG, Adami HO, Ghesquières H, De Vivo I, Clavel J, Cerhan JR, Spinelli JJ, Hofmann J, Vijai J, Curtin K, Costenbader KH, Onel K, Offit K, Teras LR, Morton L, Conde L, Miligi L, Melbye M, Ennas MG, Liebow M, Purdue MP, Glenn M, Southey MC, Din M, Rothman N, Camp NJ, Wong Doo N, Becker N, Pradhan N, Bracci PM, Boffetta P, Vineis P, Brennan P, Kraft P, Lan Q, Severson RK, Vermeulen RCH, Milne RL, Kaaks R, Travis RC, Weinstein SJ, Chanock SJ, Ansell SM, Slager SL, Zheng T, Zhang Y, Benavente Y, Taub Z, Madireddy L, Gourraud PA, Oksenberg JR, Cozen W, Hjalgrim H, Khankhanian P
Genet Epidemiol 2019 Oct;43(7):844-863. Epub 2019 Aug 13 doi: 10.1002/gepi.22242. PMID: 31407831Free PMC Article
Ju JY, Stelow EB, Mahadevan MS, Fan J, Aguilera NS
Am J Surg Pathol 2019 Oct;43(10):1361-1367. doi: 10.1097/PAS.0000000000001317. PMID: 31261290
Papagiannakis P, Michalopoulos C, Papalexi F, Dalampoura D, Diamantidis MD
Eur J Intern Med 2013 Dec;24(8):685-90. Epub 2013 Mar 21 doi: 10.1016/j.ejim.2013.02.011. PMID: 23523153

Diagnosis

Ohlsen TJD, Morse RJ, Ahmad H, Pacheco MC, Debiec KE, Bohling SD
Pediatr Dev Pathol 2024 Jan-Feb;27(1):96-101. Epub 2023 Oct 30 doi: 10.1177/10935266231205511. PMID: 37903152
Xavier AC, Suzuki R, Attarbaschi A
Best Pract Res Clin Haematol 2023 Mar;36(1):101440. Epub 2023 Jan 15 doi: 10.1016/j.beha.2023.101440. PMID: 36907633
Attarbaschi A, Abla O, Arias Padilla L, Beishuizen A, Burke GAA, Brugières L, Bruneau J, Burkhardt B, d'Amore ESG, Klapper W, Kontny U, Pillon M, Taj M, Turner SD, Uyttebroeck A, Woessmann W, Mellgren K
Pediatr Blood Cancer 2020 Aug;67(8):e28416. Epub 2020 May 26 doi: 10.1002/pbc.28416. PMID: 32452165
Ju JY, Stelow EB, Mahadevan MS, Fan J, Aguilera NS
Am J Surg Pathol 2019 Oct;43(10):1361-1367. doi: 10.1097/PAS.0000000000001317. PMID: 31261290
Collado P, Kelada A, Cámara M, Zeft A, Flagg A
Reumatol Clin (Engl Ed) 2018 Jul-Aug;14(4):227-229. Epub 2017 Mar 8 doi: 10.1016/j.reuma.2017.01.015. PMID: 28284773

Therapy

Kleinstern G, Camp NJ, Berndt SI, Birmann BM, Nieters A, Bracci PM, McKay JD, Ghesquières H, Lan Q, Hjalgrim H, Benavente Y, Monnereau A, Wang SS, Zhang Y, Purdue MP, Zeleniuch-Jacquotte A, Giles GG, Vermeulen R, Cocco P, Albanes D, Teras LR, Brooks-Wilson AR, Vajdic CM, Kane E, Caporaso NE, Smedby KE, Salles G, Vijai J, Chanock SJ, Skibola CF, Rothman N, Slager SL, Cerhan JR
Cancer Epidemiol Biomarkers Prev 2020 May;29(5):1074-1078. Epub 2020 Feb 27 doi: 10.1158/1055-9965.EPI-19-0803. PMID: 32108027Free PMC Article
Ronceray L, Abla O, Barzilai-Birenboim S, Bomken S, Chiang AK, Jazbec J, Kabickova E, Lazic J, Beishuizen A, Mellgren K, Tanaka F, Pillon M, Devalck C, Gouttenoire M, Makarova O, Burkhardt B, Attarbaschi A; European Intergroup for Childhood Non-Hodgkin Lymphoma (EICNHL) and the International Berlin-Frankfurt-Münster (i-BFM) Study Group
Pediatr Blood Cancer 2018 Apr;65(4) Epub 2017 Dec 29 doi: 10.1002/pbc.26932. PMID: 29286565
Kempf W, Kazakov DV, Buechner SA, Graf M, Zettl A, Zimmermann DR, Tinguely M
Am J Dermatopathol 2014 Aug;36(8):661-6. doi: 10.1097/DAD.0000000000000062. PMID: 24698939
Chen PH, Chiang BL, Lu MY, Yang YH
J Microbiol Immunol Infect 2014 Oct;47(5):438-40. Epub 2012 Sep 21 doi: 10.1016/j.jmii.2012.06.011. PMID: 23006506
Laurie KL, Blundell MP, Baxendale HE, Howe SJ, Sinclair J, Qasim W, Brunsberg U, Thrasher AJ, Holmdahl R, Gustafsson K
Gene Ther 2007 Dec;14(23):1623-31. Epub 2007 Sep 13 doi: 10.1038/sj.gt.3303021. PMID: 17851547

Prognosis

Kurucu N, Akyüz C, Yalçın B, Bajin İY, Varan A, Orhan D, Karnak İ, Aydın B, Kutluk T
Pediatr Hematol Oncol 2020 Nov;37(8):656-664. Epub 2020 Jul 24 doi: 10.1080/08880018.2020.1779884. PMID: 32705927
Kleinstern G, Camp NJ, Berndt SI, Birmann BM, Nieters A, Bracci PM, McKay JD, Ghesquières H, Lan Q, Hjalgrim H, Benavente Y, Monnereau A, Wang SS, Zhang Y, Purdue MP, Zeleniuch-Jacquotte A, Giles GG, Vermeulen R, Cocco P, Albanes D, Teras LR, Brooks-Wilson AR, Vajdic CM, Kane E, Caporaso NE, Smedby KE, Salles G, Vijai J, Chanock SJ, Skibola CF, Rothman N, Slager SL, Cerhan JR
Cancer Epidemiol Biomarkers Prev 2020 May;29(5):1074-1078. Epub 2020 Feb 27 doi: 10.1158/1055-9965.EPI-19-0803. PMID: 32108027Free PMC Article
Ju JY, Stelow EB, Mahadevan MS, Fan J, Aguilera NS
Am J Surg Pathol 2019 Oct;43(10):1361-1367. doi: 10.1097/PAS.0000000000001317. PMID: 31261290
Ronceray L, Abla O, Barzilai-Birenboim S, Bomken S, Chiang AK, Jazbec J, Kabickova E, Lazic J, Beishuizen A, Mellgren K, Tanaka F, Pillon M, Devalck C, Gouttenoire M, Makarova O, Burkhardt B, Attarbaschi A; European Intergroup for Childhood Non-Hodgkin Lymphoma (EICNHL) and the International Berlin-Frankfurt-Münster (i-BFM) Study Group
Pediatr Blood Cancer 2018 Apr;65(4) Epub 2017 Dec 29 doi: 10.1002/pbc.26932. PMID: 29286565
Kempf W, Kazakov DV, Buechner SA, Graf M, Zettl A, Zimmermann DR, Tinguely M
Am J Dermatopathol 2014 Aug;36(8):661-6. doi: 10.1097/DAD.0000000000000062. PMID: 24698939

Clinical prediction guides

Kleinstern G, Camp NJ, Berndt SI, Birmann BM, Nieters A, Bracci PM, McKay JD, Ghesquières H, Lan Q, Hjalgrim H, Benavente Y, Monnereau A, Wang SS, Zhang Y, Purdue MP, Zeleniuch-Jacquotte A, Giles GG, Vermeulen R, Cocco P, Albanes D, Teras LR, Brooks-Wilson AR, Vajdic CM, Kane E, Caporaso NE, Smedby KE, Salles G, Vijai J, Chanock SJ, Skibola CF, Rothman N, Slager SL, Cerhan JR
Cancer Epidemiol Biomarkers Prev 2020 May;29(5):1074-1078. Epub 2020 Feb 27 doi: 10.1158/1055-9965.EPI-19-0803. PMID: 32108027Free PMC Article
Din L, Sheikh M, Kosaraju N, Smedby KE, Bernatsky S, Berndt SI, Skibola CF, Nieters A, Wang S, McKay JD, Cocco P, Maynadié M, Foretová L, Staines A, Mack TM, de Sanjosé S, Vyse TJ, Padyukov L, Monnereau A, Arslan AA, Moore A, Brooks-Wilson AR, Novak AJ, Glimelius B, Birmann BM, Link BK, Stewart C, Vajdic CM, Haioun C, Magnani C, Conti DV, Cox DG, Casabonne D, Albanes D, Kane E, Roman E, Muzi G, Salles G, Giles GG, Adami HO, Ghesquières H, De Vivo I, Clavel J, Cerhan JR, Spinelli JJ, Hofmann J, Vijai J, Curtin K, Costenbader KH, Onel K, Offit K, Teras LR, Morton L, Conde L, Miligi L, Melbye M, Ennas MG, Liebow M, Purdue MP, Glenn M, Southey MC, Din M, Rothman N, Camp NJ, Wong Doo N, Becker N, Pradhan N, Bracci PM, Boffetta P, Vineis P, Brennan P, Kraft P, Lan Q, Severson RK, Vermeulen RCH, Milne RL, Kaaks R, Travis RC, Weinstein SJ, Chanock SJ, Ansell SM, Slager SL, Zheng T, Zhang Y, Benavente Y, Taub Z, Madireddy L, Gourraud PA, Oksenberg JR, Cozen W, Hjalgrim H, Khankhanian P
Genet Epidemiol 2019 Oct;43(7):844-863. Epub 2019 Aug 13 doi: 10.1002/gepi.22242. PMID: 31407831Free PMC Article
Ju JY, Stelow EB, Mahadevan MS, Fan J, Aguilera NS
Am J Surg Pathol 2019 Oct;43(10):1361-1367. doi: 10.1097/PAS.0000000000001317. PMID: 31261290
Ronceray L, Abla O, Barzilai-Birenboim S, Bomken S, Chiang AK, Jazbec J, Kabickova E, Lazic J, Beishuizen A, Mellgren K, Tanaka F, Pillon M, Devalck C, Gouttenoire M, Makarova O, Burkhardt B, Attarbaschi A; European Intergroup for Childhood Non-Hodgkin Lymphoma (EICNHL) and the International Berlin-Frankfurt-Münster (i-BFM) Study Group
Pediatr Blood Cancer 2018 Apr;65(4) Epub 2017 Dec 29 doi: 10.1002/pbc.26932. PMID: 29286565
Yang HR, Choi HS, Paik JH, Lee HS
J Pediatr Gastroenterol Nutr 2013 Sep;57(3):298-304. doi: 10.1097/MPG.0b013e318298020a. PMID: 23974061

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